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Aldose reductase Sorbitol dehydrogenase 14 kDa phosphohistidine phosphatase Hexokinase-1 Mannose-6- phosphate isomerase Hexokinase-1 Phosphomannomutase 1 6- phosphofructokinase, liver type Fructose-1,6- bisphosphatase 1 Mannose-1- phosphate guanyltransferase beta Fructose- bisphosphate aldolase B GDP-mannose 4,6 dehydratase GDP-L-fucose synthase Fucose-1- phosphate guanylyltransferase L-fucose kinase Ketohexokinase Triosephosphate isomerase Fructose- bisphosphate aldolase A 6- phosphofructo- 2- kinase/fructose- 2,6- bisphosphatase 1 α-D-Glucose Fructose 6-phosphate Dihydroxyacetone phosphate NADP Sorbitol NADPH NAD Accumulation D-Fructose NADH β-D-Fructose 2-phosphate H2O Pi ATP ADP Mannose 6-phosphate D-Mannose ATP ADP D-Mannose 1-phosphate ATP Fructose 1,6-bisphosphate ADP H2O Pi GTP Guanosine diphosphate mannose PPi D-Glyceraldehyde 3-phosphate GDP-4-Dehydro-6-deoxy-D- mannose H2O GDP-L-fucose NADP NADPH Fucose 1-phosphate GTP PPi L-Fucose ATP ADP ATP Fructose 1-phosphate ADP Glyceraldehyde D-Fructose 2,6-bisphosphate H2O Pi Zinc (II) ion NADP Galactose Metabolism Glycolysis Glycolysis Amino Sugar Metabolism Magnesium Zinc (II) ion Magnesium Magnesium Mitochondrial Membrane Mitochondria Intracellular Space Liver Hepatic Liver Cell
Mitochondria AKR1B1 SORD PHPT1 HK1 MPI HK1 PMM1 PFKL FBP1 GMPPB ALDOB GMDS TSTA3 FPGT FUK KHK TPI1 ALDOA PFKFB1 α-D-Glucose Fructose 6-phosphate Dihydroxyacetone phosphate NADP Sorbitol NADPH NAD Accumulation D-Fructose NADH β-D-Fructose 2-phosphate Water Phosphoric acid Adenosine triphosphate Adenosine diphosphate Mannose 6-phosphate D-Mannose Adenosine triphosphate Adenosine diphosphate D-Mannose 1-phosphate Adenosine triphosphate Fructose 1,6- bisphosphate Adenosine diphosphate Water Phosphate Guanosine triphosphate Guanosine diphosphate mannose Pyrophosphate D- Glyceraldehyde 3-phosphate GDP-4- Dehydro-6- deoxy-D- mannose Water GDP-L-fucose NADP NADPH Fucose 1-phosphate Guanosine triphosphate Pyrophosphate L-Fucose Adenosine triphosphate Adenosine diphosphate Adenosine triphosphate Fructose 1-phosphate Adenosine diphosphate Glyceraldehyde D-Fructose 2,6- bisphosphate Water Phosphate Galactose Metabolism Glycolysis Glycolysis Amino Sugar Metabolism
AKR1B1 SORD PHPT1 HK1 MPI HK1 PMM1 PFKL FBP1 GMPPB ALDOB GMDS TSTA3 FPGT FUK KHK TPI1 ALDOA PFKFB1 a-D-Glc Fru6P Dhapp NADP Srbitol NADPH NAD Accumulation Fru NADH βDF2P H2O Pi ATP ADP Man-6P Man ATP ADP M1P ATP Fru1,6P ADP H2O Pi GTP GDPMan PPi Glyc3P G4D6DMn H2O GDP-Fuc NADP NADPH Fuc-1P GTP PPi Fucose ATP ADP ATP Fru-1P ADP Glycald Fru2,6P H2O Pi Zinc NADP PW000159 PW000146 PW000146 PW000008 Mg2+ Zinc Mg2+ Mg2+ Mitochondrial Membrane Mitochondria Intracellular Space Liver Hepatic Liver Cell
Mitochondria AKR1B1 SORD PHPT1 HK1 MPI HK1 PMM1 PFKL FBP1 GMPPB ALDOB GMDS TSTA3 FPGT FUK KHK TPI1 ALDOA PFKFB1 a-D-Glc Fru6P Dhapp NADP Srbitol NADPH NAD Accumulation Fru NADH βDF2P H2O PhosfrA ATP ADP Man-6P Man ATP ADP M1P ATP Fru1,6P ADP H2O Pi GTP GDPMan Ppi Glyc3P G4D6DMn H2O GDP-Fuc NADP NADPH Fuc-1P GTP Ppi Fucose ATP ADP ATP Fru-1P ADP Glycald Fru2,6P H2O Pi PW000159 PW000146 PW000146 PW000008