branched-chain
amino-acid
aminotransferase
2-
isopropylmalate
synthase
isopropylmalate
isomerase
isopropylmalate
isomerase
isopropylmalate
isomerase
isopropylmalate
isomerase
D-malate / 3-
isopropylmalate
dehydrogenase
(decarboxylating)
tyrosine
aminotransferase
3-Methyl-2-
oxovaleric acid
H2O
Acetyl-CoA
CoA
H+
2-
Isopropylmalic
acid
H2O
Isopropylmaleate
H2O
3-
Isopropylmalate
NAD
NADH
H+
2-Isopropyl- 3-
oxosuccinate
H+
CO2
Ketoleucine
L-Glutamic acid
Oxoglutaric
acid
L-Leucine
Isoleucine
Biosynthesis
3-
isopropylmalate
dehydrogenase
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