Glycine cleavage
system H protein,
mitochondrial
Aquaporin-8
L-serine
dehydratase/L-
threonine
deaminase
Isoaspartyl
peptidase/L-
asparaginase
Asparagine
synthetase
[glutamine-
hydrolyzing]
Histidine
ammonia-lyase
Carbamoyl-
phosphate
synthase
[ammonia],
mitochondrial
Glutamine
synthetase
Glutamate
dehydrogenase 1,
mitochondrial
Glutaminase liver
isoform,
mitochondrial
Aminomethyltransferase,
mitochondrial
Dihydrolipoyl
dehydrogenase,
mitochondrial
Glycine
dehydrogenase
[decarboxylating],
mitochondrial
L-Serine
L-Histidine
Pyruvic acid
Carbamoyl
phosphate
Glycine
L-Glutamic acid
L-Glutamic acid
L-Aspartic acid
NH3
NH3
L-Asparagine
H2O
ATP
L-Glutamine
H2O
AMP
PPi
Urocanic acid
ATP
CO2
H2O
ADP
Pi
ATP
ADP
Pi
L-Glutamine
H2O
NAD
Oxoglutaric acid
NADH
H2O
L-Glutamic acid
Tetrahydrofolic
acid
8-
[(Aminomethyl)sulfanyl]-
6-
sulfanyloctanoic
acid
Dihydrolipoate
5,10-Methylene-
THF
NAD
(R)-lipoic acid
NADH
CO2
Pyridoxal
5'-phosphate
Biotin
Magnesium
FAD
Glycine and
Serine
Metabolism
Histidine
Metabolism
Citric Acid
Cycle
Urea Cycle
Glycine and
Serine
Metabolism
Glutamate
Metabolism
Glutamate
Metabolism
Aspartate
Metabolism
Pyridoxal
5'-phosphate
Glycine cleavage system
Mitochondrial Matrix
Extracellular Space
Cytoplasm
Mitochondria
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