C5H11NO2
L-Valine
117.07898
CHEBI:16015
ChEBI
1005
ChemSpider
6022
PubChem-compound
C23H38N7O17P3S
Acetyl-CoA
809.1258
439161
PubChem-compound
937
ChemSpider
Acyl-CoA synthetase short-chain family member 3, mitochondrial
388353
ChemSpider
Reaction1011
false
(S)-Methylmalonic acid semialdehyde + Coenzyme A + NAD + Water → Hydrogen carbonate + NADH + Propionyl-CoA
LEFT_TO_RIGHT
Reaction1254
false
Malonyl-CoA semialdehyde ↔ 3-Hydroxypropionyl-CoA
REVERSIBLE
439153
PubChem-compound
57
ChemSpider
D-METHYL-MALONYL-COA
BioCyc
ReactionCatalysis703
ACTIVATION
Enoyl-CoA hydratase, mitochondrial
HMDB0000094
HMDB
50
ChemSpider
4.2.1.17
false
4.2.1.17
3-Hydroxypropionyl-CoA ↔ Acrylyl-CoA + Water
REVERSIBLE
3.1.2.4
false
3.1.2.4
3-Hydroxypropionyl-CoA + Water ↔ Coenzyme A + Hydroxypropionic acid
REVERSIBLE
Propinol adenylate
CHEBI:16027
ChEBI
PW000054
PathWhiz
C00683
KEGG Compound
ATP
BioCyc
Acyl-CoA synthetase short-chain family member 3, mitochondrial
PW000051
PathWhiz
6.4.1.3
false
6.4.1.3
Adenosine triphosphate + Hydrogen carbonate + Propionyl-CoA → Adenosine diphosphate + Hydrogen + S-Methylmalonyl-CoA
LEFT_TO_RIGHT
Medium-chain specific acyl-CoA dehydrogenase, mitochondrial
Acetoacetyl-CoA
2.3.1.168
false
2.3.1.168
2-Ketobutyric acid + Coenzyme A + NAD → NADH + Propionyl-CoA
LEFT_TO_RIGHT
559142
ChemSpider
4.1.1.9
false
4.1.1.9
Malonyl-CoA → Acetyl-CoA + Carbon dioxide
LEFT_TO_RIGHT
6287
PubChem-compound
1.0
ReactionCatalysis972
ACTIVATION
PANTETHEINE-P
BioCyc
ReactionCatalysis970
ACTIVATION
HMDB0002170
HMDB
P09622
UniProt
HCO3
BioCyc
CHEBI:15380
ChEBI
ReactionCatalysis62989
ACTIVATION
5742
ChemSpider
NADH
Methylmalonyl-CoA mutase, mitochondrial
C25H40N7O19P3S
Succinyl-CoA
867.1312
1.0
Acetyl-CoA
C00332
KEGG Compound
6.2.1.1
false
6.2.1.1
Propinol adenylate ↔ Adenosine monophosphate + Propionic acid
REVERSIBLE
ALPHA-GLUCOSE-16-BISPHOSPHATE
BioCyc
1.0
ReactionCatalysis969
ACTIVATION
388468
ChemSpider
5858
ChemSpider
ReactionCatalysis961
ACTIVATION
11266
PubChem-compound
PW000032
PathWhiz
C00109
KEGG Compound
C00100
KEGG Compound
Acetyl-CoA
SubPathwayInput
5776-58-9
CAS
1010
ChemSpider
C00222
KEGG Compound
5.4.99.2
false
5.4.99.2
R-Methylmalonyl-CoA ↔ Succinyl-CoA
REVERSIBLE
SMILES
CC(C)(COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N)[C@@H](O)C(=O)NCCC(=O)NCCS
6.2.1.1
false
6.2.1.1
Adenosine monophosphate + Propionyl-CoA + Pyrophosphate ↔ Adenosine triphosphate + Pantetheine + Propinol adenylate
REVERSIBLE
5.1.99.1
false
5.1.99.1
S-Methylmalonyl-CoA → R-Methylmalonyl-CoA
LEFT_TO_RIGHT
Propionyl-CoA carboxylase alpha chain, mitochondrial
1.3.8.7
false
1.3.8.7
Acrylyl-CoA + electron-transfer flavoprotein ↔ Propionyl-CoA + Reduced electron-transfer flavoprotein
REVERSIBLE
CHEBI:30769
ChEBI
439164
PubChem-compound
CHEBI:30768
ChEBI
2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
PPI
BioCyc
Enoyl-CoA hydratase, mitochondrial
2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
Malonyl-CoA semialdehyde
SMILES
CC(C)(COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N)C(O)C(=O)NCCC(=O)NCCSC(=O)CCC(O)=O
L-Valine
C24H40N7O17P3S
Propionyl-CoA
823.1414
1.0
C01213
KEGG Compound
Cytosol
388310
ChemSpider
503-66-2
CAS
CHEBI:5086
ChEBI
1.0
1.0
Medium-chain specific acyl-CoA dehydrogenase, mitochondrial
2-Hydroxybutyric acid
Reaction2266
false
Malonyl-CoA ↔ Malonyl-CoA semialdehyde
REVERSIBLE
7664-38-2
CAS
73173-92-9
CAS
1.0
ReactionCatalysis627
ACTIVATION
ReactionCatalysis989
ACTIVATION
C00009
KEGG Compound
C00008
KEGG Compound
Q9H6R3
UniProt
Methylmalonyl-CoA epimerase, mitochondrial
C00001
KEGG Compound
1.0
PROPIONYL-COA
BioCyc
CHEBI:18361
ChEBI
NADH
SubPathwayInteraction118631
SubPathway118631Reaction
SubPathwayReaction
C00004
KEGG Compound
SubPathwayInteraction118632
SubPathwayReaction
SubPathway118632Reaction
C00003
KEGG Compound
2-OXOBUTANOATE
BioCyc
C00002
KEGG Compound
Acetyl-CoA acetyltransferase, mitochondrial
SubPathwayInteraction118630
SubPathwayReaction
SubPathway118630Reaction
SubPathwayInteraction118625
SubPathwayReaction
SubPathway118625Reaction
Reaction1282
false
(S)-Methylmalonic acid semialdehyde + NAD + Water → Methylmalonic acid + NADH
LEFT_TO_RIGHT
SubPathwayInteraction118628
SubPathwayReaction
SubPathway118628Reaction
SubPathwayInteraction118629
SubPathwayReaction
SubPathway118629Reaction
Coenzyme A
SubPathwayInteraction118626
SubPathway118626Reaction
SubPathwayReaction
Reaction1281
false
L-Valine → (S)-Methylmalonic acid semialdehyde
LEFT_TO_RIGHT
Malonic semialdehyde
SubPathwayInteraction118627
SubPathwayReaction
SubPathway118627Reaction
ReactionCatalysis977
ACTIVATION
ReactionCatalysis978
ACTIVATION
Reaction1048
false
Acetyl-CoA + Adenosine triphosphate + Hydrogen carbonate → Adenosine diphosphate + Malonyl-CoA + Phosphoric acid
LEFT_TO_RIGHT
ReactionCatalysis976
ACTIVATION
389623
ChemSpider
Coenzyme A
C21H27N7O14P2
NAD
663.10913
73173-91-8
CAS
C00011
KEGG Compound
C00010
KEGG Compound
HMDB0000902
HMDB
C00013
KEGG Compound
P21953
UniProt
Succinyl-CoA
4-aminobutyrate aminotransferase, mitochondrial
H
Hydrogen Ion
1.007825
388307
ChemSpider
22833590
PubChem-compound
56-65-5
CAS
53-84-9
CAS
C00020
KEGG Compound
Malonyl-CoA decarboxylase, mitochondrial
C00026
KEGG Compound
C00025
KEGG Compound
SMILES
CC(C)(COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N)C(O)C(=O)NCCC(=O)NCCSC(=O)CC(O)=O
C00024
KEGG Compound
CHEBI:26078
ChEBI
317-66-8
CAS
1.0
Methylmalonyl-CoA mutase, mitochondrial
Methylmalonyl-CoA epimerase, mitochondrial
Propionyl-CoA carboxylase alpha chain, mitochondrial
Propionyl-CoA carboxylase beta chain, mitochondrial
Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial
L-Glutamic acid
Acrylyl-CoA
5462303
PubChem-compound
769
PubChem-compound
C00158
KEGG Compound
CHEBI:18276
ChEBI
SMILES
NC(=O)C1=CN(C=CC1)[C@@H]1O[C@H](CO[P@](O)(=O)O[P@](O)(=O)OC[C@H]2O[C@H]([C@H](O)[C@@H]2O)N2C=NC3=C(N)N=CN=C23)[C@@H](O)[C@H]1O
328-50-7
CAS
SMILES
CC(=O)CC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
AMP
BioCyc
1.0
1.0
C00282
KEGG Compound
C3H6O3
Hydroxypropionic acid
90.03169
HMDB0002310
HMDB
HMDB0000250
HMDB
3-Hydroxypropionyl-CoA
SMILES
OP(O)(=O)OP(O)(O)=O
HMDB0001341
HMDB
1.0
Hydroxypropionic acid
Acetyl-CoA acetyltransferase, mitochondrial
C01013
KEGG Compound
C25H40N7O19P3S
R-Methylmalonyl-CoA
867.1312
C11H22N2O4S
Pantetheine
278.13004
C00163
KEGG Compound
Propionyl-CoA carboxylase beta chain, mitochondrial
C00288
KEGG Compound
SMILES
NC1=NC=NC2=C1N=CN2[C@@H]1O[C@H](COP(O)(=O)OP(O)(O)=O)[C@@H](O)[C@H]1O
(S)-Methylmalonic acid semialdehyde
604-98-8
CAS
HMDB0006806
HMDB
762
ChemSpider
SMILES
OC(=O)CC(O)(CC(O)=O)C(O)=O
HMDB0000148
HMDB
389700
ChemSpider
Succinyl-CoA
SubPathwayOutput
389702
ChemSpider
C13H18N5O8P
Propinol adenylate
403.0893
C24H40N7O18P3S
3-Hydroxypropionyl-CoA
839.13635
4-aminobutyrate aminotransferase, mitochondrial
C05989
KEGG Compound
2.0
HMDB0006807
HMDB
7732-18-5
CAS
C05983
KEGG Compound
C05984
KEGG Compound
72-18-4
CAS
HMDB0001487
HMDB
NAD
61-19-8
CAS
SMILES
NC1=C2N=CN([C@@H]3O[C@H](COP(O)(O)=O)[C@@H](O)[C@H]3O)C2=NC=N1
1.0
1.0
C00183
KEGG Compound
926-61-4
CAS
CHEBI:33404
ChEBI
HMDB0003426
HMDB
HMDB0002217
HMDB
56-86-0
CAS
1.0
HMDB0001362
HMDB
HMDB0001484
HMDB
NAD
C10H16N5O13P3
Adenosine triphosphate
506.99576
Phosphoric acid
C4H6O3
(S)-Methylmalonic acid semialdehyde
102.03169
SMILES
CCC(O)=O
Enoyl-CoA hydratase, mitochondrial
NAD
305
ChemSpider
HMDB0000045
HMDB
S-Methylmalonyl-CoA
Reaction5
false
Oxoglutaric acid + β-Alanine → L-Glutamic acid + Malonic semialdehyde
LEFT_TO_RIGHT
SMILES
NCCC(O)=O
2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
962
PubChem-compound
5800
ChemSpider
CO2
Carbon dioxide
43.98983
979
ChemSpider
C24H38N7O17P3S
Acrylyl-CoA
821.1258
HMDB0000056
HMDB
C00080
KEGG Compound
C25H40N7O19P3S
S-Methylmalonyl-CoA
867.1312
Water
2.0
ACRYLYL-COA
BioCyc
H3O4P
Phosphoric acid
97.9769
1.0
C00083
KEGG Compound
SMILES
OC(=O)CC=O
3-HYDROXY-PROPIONYL-COA
BioCyc
HMDB0002111
HMDB
SMILES
N[C@@H](CCC(O)=O)C(O)=O
6.0
1.0
HMDB0001022
HMDB
58-64-0
CAS
Pantetheine
1.0
99043-16-0
CAS
1.0
2-Ketobutyric acid
2-Ketobutyric acid
SubPathwayOutput
845
ChemSpider
C00091
KEGG Compound
Methylmalonyl-CoA mutase, mitochondrial
METHYL-MALONYL-COA
BioCyc
C4H6O3
2-Ketobutyric acid
102.03169
Malonic semialdehyde
1.0
HMDB0001275
HMDB
PROPIONATE
BioCyc
644102
PubChem-compound
1.0
444493
PubChem-compound
868
PubChem-compound
6083
PubChem-compound
4575365
ChemSpider
C05668
KEGG Compound
C00099
KEGG Compound
10663
PubChem-compound
1.0
1.0
ACETYL-COA
BioCyc
H2O
Water
18.010565
1.0
(S)-Methylmalonic acid semialdehyde
NADH
BioCyc
HMDB0002255
HMDB
P11182
UniProt
NAD
BioCyc
CPD-3564
BioCyc
Malonyl-CoA semialdehyde
1.0
HMDB0059597
HMDB
1.0
Propionic acid
749
ChemSpider
71-52-3
CAS
1.0
Acetyl-CoA
SubPathwayOutput
61460
ChemSpider
C02170
KEGG Compound
CH2O3
Hydrogen carbonate
62.000393
HMDB0001175
HMDB
SMILES
[H][H]
HMDB0002142
HMDB
487
PubChem-compound
30572
ChemSpider
S-Methylmalonyl-CoA
ReactionCatalysis1205
ACTIVATION
Valine, Leucine, and Isoleucine Degradation
SubPathway
Adenosine monophosphate
ReactionCatalysis1204
ACTIVATION
Q02252
UniProt
SMILES
O
CIT
BioCyc
P12694
UniProt
Propionyl-CoA
SubPathwayInput
Acetyl-CoA
C10H14N5O7P
Adenosine monophosphate
347.06308
58838673
PubChem-compound
Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial
479
PubChem-compound
1.0
C3H6O2
Propionic acid
74.03678
239
PubChem-compound
HMDB0000538
HMDB
1004
PubChem-compound
L-lactate dehydrogenase A-like 6B
Propionic acid
SubPathwayOutput
1.0
1.0
Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial
CHEBI:27821
ChEBI
6816
PubChem-compound
51
PubChem-compound
1.0
SMILES
OC(O)=O
CHEBI:15846
ChEBI
1.0
ADP
BioCyc
58
PubChem-compound
C3H7NO2
β-Alanine
89.047676
Q9BYZ2
UniProt
ReactionCatalysis178
ACTIVATION
Malonyl-CoA
3-hydroxyisobutyryl-CoA hydrolase, mitochondrial
C4H8O3
2-Hydroxybutyric acid
104.04734
C24H38N7O18P3S
Malonyl-CoA semialdehyde
837.12067
1038
PubChem-compound
1032
PubChem-compound
GO:0005829
GENE ONTOLOGY
1.0
SMILES
OCCC(O)=O
274
ChemSpider
1.0
C5H6O5
Oxoglutaric acid
146.02153
C4H6O4
Methylmalonic acid
118.02661
CHEBI:16908
ChEBI
Citric Acid Cycle
SubPathway
1.0
Pyrophosphate
ReactionCatalysis161
ACTIVATION
SMILES
CC(C)(CO)C(O)C(=O)NCCC(=O)NCCS
SMILES
C[C@H](C(O)=O)C(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OCC1OC(C(O)C1OP(O)(O)=O)N1C=NC2=C(N)N=CN=C12
P22033
UniProt
77-92-9
CAS
HMDB0000202
HMDB
600-18-0
CAS
Pyruvate Metabolism
SubPathway
Reaction666
false
Coenzyme A + Malonic semialdehyde + NAD → Acetyl-CoA + Carbon dioxide + NADH
LEFT_TO_RIGHT
Mitochondrion
4.0
HMDB0000208
HMDB
SMILES
CC(C)(COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N)C(O)C(=O)NCCC(=O)NCCSC(=O)CC=O
Carbon dioxide
1.0
440865
PubChem-compound
440863
PubChem-compound
58-68-4
CAS
SMILES
CC(C(O)=O)C(O)=O
HMDB0001423
HMDB
4.0
SMILES
OC(=O)CCC(=O)C(O)=O
124-38-9
CAS
CHEBI:30915
ChEBI
1.0
1.0
ReactionCatalysis6
ACTIVATION
P30084
UniProt
CHEBI:15531
ChEBI
1.0
Q13085
UniProt
1.0
HMDB0011111
HMDB
6050
ChemSpider
GO:0005759
GENE ONTOLOGY
P24752
UniProt
Hydrogen
GLT
BioCyc
107-95-9
CAS
SMP0000057
SMPDB
Hydrogen carbonate
H2
Hydrogen
2.01565
SMILES
O=C=O
SMILES
CC(C)(COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C(N)N=CN=C12)C(O)C(=O)NCCC(=O)NCCSC(=O)C=C
Hydrogen Ion
C06002
KEGG Compound
1.0
SMILES
OP(O)(O)=O
HMDB0000595
HMDB
H4O7P2
Pyrophosphate
177.94322
SMILES
C[C@@H](C(O)=O)C(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OCC1OC([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C(N)N=CN=C12
C25H40N7O18P3S
Acetoacetyl-CoA
851.13635
234
ChemSpider
496-65-1
CAS
SMP0000060
SMPDB
C21H29N7O14P2
NADH
665.12476
HMDB0000237
HMDB
473
ChemSpider
HMDB0001206
HMDB
5957
PubChem-compound
CHEBI:1148
ChEBI
Propanoate Metabolism
1.0
3-Hydroxypropionyl-CoA
CHEBI:15513
ChEBI
L-lactate dehydrogenase A-like 6B
1.0
Lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial
1.0
O95822
UniProt
440753
PubChem-compound
1.0
Citric acid
SubPathwayOutput
466
ChemSpider
GO:0005739
GENE ONTOLOGY
1.0
Adenosine triphosphate
C10H15N5O10P2
Adenosine diphosphate
427.02942
SMILES
CC[C@H](O)C(O)=O
HMDB0002307
HMDB
HMDB0000005
HMDB
SMILES
CCC(=O)C(O)=O
HMDB0000008
HMDB
CHEBI:16958
ChEBI
79-09-4
CAS
Pantothenate and CoA Biosynthesis
SubPathway
C6H8O7
Citric acid
192.02701
Acetyl-CoA carboxylase 1
C00831
KEGG Compound
CHEBI:16414
ChEBI
SMILES
NC(=O)C1=C[N+](=CC=C1)[C@@H]1O[C@H](COP([O-])(=O)OP(O)(=O)OC[C@H]2O[C@H]([C@H](O)[C@@H]2O)N2C=NC3=C2N=CN=C3N)[C@@H](O)[C@H]1O
R-Methylmalonyl-CoA
electron-transfer flavoprotein
19782904
PubChem-compound
5682
ChemSpider
Reduced electron-transfer flavoprotein
CHEBI:30831
ChEBI
CHEBI:1146900
ChEBI
17216177
ChemSpider
1.0
Glycine, Serine, and Threonine Metabolism
SubPathway
Tricarboxylate Transport System
SubPathway
Mitochondrial Matrix
2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
21252287
PubChem-compound
14000-31-8
CAS
Cysteine and Methionine Metabolism
SubPathway
Hydroxypropionic acid
SubPathwayOutput
SMP0000016
SMPDB
CO-A
BioCyc
B-ALANINE
BioCyc
72-89-9
CAS
Carbon dioxide
600-15-7
CAS
C21H36N7O16P3S
Coenzyme A
767.11523
Adenosine diphosphate
HMDB0000700
HMDB
electron-transfer flavoprotein
1.0
Reduced electron-transfer flavoprotein
ReactionCatalysis1058
ACTIVATION
10213
ChemSpider
ReactionCatalysis1057
ACTIVATION
Acetyl-CoA carboxylase 1
ACETOACETYL-COA
BioCyc
1.0
Propionyl-CoA carboxylase
CHEBI:15422
ChEBI
CHEBI:16753
ChEBI
Malonyl-CoA decarboxylase, mitochondrial
Coenzyme A
6557
ChemSpider
Acetyl-coenzyme A synthetase 2-like, mitochondrial
SMP0000027
SMPDB
1.0
P80404
UniProt
Homo sapiens
1.0
524-14-1
CAS
SMILES
CC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
388299
ChemSpider
SMILES
CC(C)[C@H](N)C(O)=O
Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial
CHEBI:17960
ChEBI
1.0
C3H4O3
Malonic semialdehyde
88.016045
1.0
439214
PubChem-compound
1.0
CHEBI:15539
ChEBI
C5H9NO4
L-Glutamic acid
147.05316
Water
33032
PubChem-compound
1.0
Dihydrolipoyl dehydrogenase, mitochondrial
CHEBI:16526
ChEBI
P11310
UniProt
CHEBI:16761
ChEBI
CHEBI:27762
ChEBI
Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial
10792
ChemSpider
Methylmalonic acid
1.0
SMP0000032
SMPDB
Q96PE7
UniProt
NADH
157786-88-4
CAS
9606
TAXONOMY
P05166
UniProt
1333-74-0
CAS
P05165
UniProt
CHEBI:17544
ChEBI
PW000149
PathWhiz
2-KETOGLUTARATE
BioCyc
392413
ChemSpider
6244-93-5
CAS
SMILES
CC(C)(COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C(N)N=CN=C12)C(O)C(=O)NCCC(=O)NCCSC(=O)CCO
Oxoglutaric acid
5893
PubChem-compound
SMILES
C[C@@H](C=O)C(O)=O
4-aminobutyrate aminotransferase, mitochondrial
1.1.1.27
false
1.1.1.27
2-Hydroxybutyric acid + NAD ↔ 2-Ketobutyric acid + Hydrogen Ion + NADH
REVERSIBLE
13628334
ChemSpider
1420-36-6
CAS
branched-chain alpha-keto dehydrogenase complex
CHEBI:15377
ChEBI
Lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial
C24H38N7O19P3S
Malonyl-CoA
853.1156
CHEBI:15378
ChEBI
SMILES
[H+]
516-05-2
CAS
4.0
4.0
SMILES
NC1=NC=NC2=C1N=CN2[C@@H]1O[C@H](COP(O)(=O)OP(O)(=O)OP(O)(O)=O)[C@@H](O)[C@H]1O
R-Methylmalonyl-CoA
VAL
BioCyc
2.0
Q6NVY1
UniProt
Acetyl-coenzyme A synthetase 2-like, mitochondrial
280
PubChem-compound
439340
PubChem-compound
Acetyl-CoA acetyltransferase, mitochondrial
Medium-chain specific acyl-CoA dehydrogenase, mitochondrial
Dihydrolipoyl dehydrogenase, mitochondrial
2.3.1.9
false
2.3.1.9
2 Acetyl-CoA ↔ Acetoacetyl-CoA + Coenzyme A
REVERSIBLE
CHEBI:15345
ChEBI
Propionyl-CoA
PW000005
PathWhiz
Q9NUB1
UniProt
β-Alanine
SubPathwayInput
CHEBI:30860
ChEBI
C00894
KEGG Compound
SMILES
CCC(=O)SCCNC(=O)CCNC(=O)C(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
1.0
1.0
3-METHYLBENZYLSUCCINYL-COA
BioCyc
HMDB0001967
HMDB
CHEBI:15351
ChEBI
3-hydroxyisobutyryl-CoA hydrolase, mitochondrial
68152
PubChem-compound
6.2.1.1
false
6.2.1.1
Adenosine triphosphate + Pantetheine + Propinol adenylate ↔ Adenosine monophosphate + Propionyl-CoA + Pyrophosphate
REVERSIBLE
HMDB0000883
HMDB
SMILES
CCC(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1O)N1C=NC2=C1N=CN=C2N
1.0
Intestinal Microflora
SubPathway
CHEBI:62415
ChEBI
85-61-0
CAS
1.0
MALONYL-COA
BioCyc
6.2.1.1
false
6.2.1.1
Propinol adenylate ↔ Adenosine monophosphate + Propionic acid
REVERSIBLE