Peroxisome
Mitochondria
Unknown
Unknown
Unknown
Unknown
Unknown
Unknown
Unknown
Unknown
Unknown
Unknown
SLC25A20
SLC25A20
SLC25A20
ACSL1
ALDH2
HACL1
PHYH
CRAT
CROT
CRAT
ACSL1
CRAT
CRAT
CPT2
Pristanoyl-CoA
Propionyl-CoA
Acetyl-CoA
4,8-
Dimethylnonanoyl-
CoA
4,8-
Dimethylnonanoyl-
CoA
Acetyl-CoA
Pristanoyl-CoA
Propionylcarnitine
Propionylcarnitine
L-Acetylcarnitine
L-Acetylcarnitine
4,8
Dimethylnonanoyl
carnitine
4,8
Dimethylnonanoyl
carnitine
Phytanoyl-CoA
Phytanoyl-CoA
Propionylcarnitine
L-Acetylcarnitine
4,8
Dimethylnonanoyl
carnitine
Adenosine
triphosphate
Pristanic acid
Coenzyme A
Adenosine
diphosphate
Pyrophosphate
Pristanal
Coenzyme A
2-
Hydroxyphytanoyl-
CoA
Formyl-CoA
Oxoglutaric acid
Oxygen
Succinic acid
Carbon dioxide
L-Carnitine
Coenzyme A
L-Carnitine
Coenzyme A
Coenzyme A
Phytanic acid
Adenosine
triphosphate
Coenzyme A
Adenosine
diphosphate
Pyrophosphate
Propionyl-CoA
L-Carnitine
Coenzyme A
Acetyl-CoA
Coenzyme A
L-Carnitine
Coenzyme A
Beta Oxidation
Beta Oxidation
Beta Oxidation
Beta Oxidation