Carnitine O-
palmitoyltransferase
2, mitochondrial
Enoyl-CoA
hydratase,
mitochondrial
Trifunctional
enzyme subunit
alpha,
mitochondrial
Trifunctional
enzyme subunit
beta,
mitochondrial
3-ketoacyl-CoA
thiolase,
mitochondrial
Carnitine O-
palmitoyltransferase
1, liver isoform
Long-chain-
fatty-acid--CoA
ligase 1
Enoyl-CoA
hydratase,
mitochondrial
Trifunctional
enzyme subunit
alpha,
mitochondrial
Trifunctional
enzyme subunit
beta,
mitochondrial
3-ketoacyl-CoA
thiolase,
mitochondrial
Trifunctional
enzyme subunit
alpha,
mitochondrial
Trifunctional
enzyme subunit
beta,
mitochondrial
3-ketoacyl-CoA
thiolase,
mitochondrial
Enoyl-CoA
hydratase,
mitochondrial
Trifunctional
enzyme subunit
alpha,
mitochondrial
Trifunctional
enzyme subunit
beta,
mitochondrial
3-ketoacyl-CoA
thiolase,
mitochondrial
Enoyl-CoA
hydratase,
mitochondrial
Trifunctional
enzyme subunit
alpha,
mitochondrial
Trifunctional
enzyme subunit
beta,
mitochondrial
3-ketoacyl-CoA
thiolase,
mitochondrial
Long-chain
specific acyl-CoA
dehydrogenase,
mitochondrial
Medium-chain
specific acyl-CoA
dehydrogenase,
mitochondrial
Short/branched
chain specific
acyl-CoA
dehydrogenase,
mitochondrial
Short-chain
specific acyl-CoA
dehydrogenase,
mitochondrial
Enoyl-CoA
hydratase,
mitochondrial
Trifunctional
enzyme subunit
alpha,
mitochondrial
Trifunctional
enzyme subunit
beta,
mitochondrial
3-ketoacyl-CoA
thiolase,
mitochondrial
Long-chain
specific acyl-CoA
dehydrogenase,
mitochondrial
Medium-chain
specific acyl-CoA
dehydrogenase,
mitochondrial
Short/branched
chain specific
acyl-CoA
dehydrogenase,
mitochondrial
Enoyl-CoA
hydratase,
mitochondrial
Acetyl-CoA
acetyltransferase,
mitochondrial
Glutaryl-CoA
dehydrogenase,
mitochondrial
Very long-chain
specific acyl-CoA
dehydrogenase,
mitochondrial
Long-chain
specific acyl-CoA
dehydrogenase,
mitochondrial
Medium-chain
specific acyl-CoA
dehydrogenase,
mitochondrial
Long-chain
specific acyl-CoA
dehydrogenase,
mitochondrial
Medium-chain
specific acyl-CoA
dehydrogenase,
mitochondrial
Long-chain
specific acyl-CoA
dehydrogenase,
mitochondrial
Medium-chain
specific acyl-CoA
dehydrogenase,
mitochondrial
Enoyl-CoA
hydratase,
mitochondrial
Long-chain
specific acyl-CoA
dehydrogenase,
mitochondrial
Medium-chain
specific acyl-CoA
dehydrogenase,
mitochondrial
Long-chain
specific acyl-CoA
dehydrogenase,
mitochondrial
Medium-chain
specific acyl-CoA
dehydrogenase,
mitochondrial
Trifunctional
enzyme subunit
alpha,
mitochondrial
Trifunctional
enzyme subunit
beta,
mitochondrial
Palmitic acid
L-
Palmitoylcarnitine
L-
Palmitoylcarnitine
Palmitoyl-CoA
L-Carnitine
CoA
3-
Hydroxyhexadecanoyl-
CoA
(2E)-
Hexadecenoyl- CoA
H2O
NAD
3-
oxohexadecanoyl-
CoA
NADH
H+
Tetradecanoyl-CoA
Acetyl-CoA
CoA
Palmitoyl-CoA
L-Carnitine
CoA
ATP
CoA
AMP
PPi
3-
Hydroxytetradecanoyl-
CoA
(2E)-
Tetradecenoyl-
CoA
H2O
NAD
3-
oxotetradecanoyl-
CoA
NADH
H+
Lauroyl-CoA
Acetyl-CoA
CoA
3-
Hydroxydodecanoyl-
CoA
NAD
3- oxododecanoyl-
CoA
NADH
H+
Decanoyl-CoA
Acetyl-CoA
CoA
3-
Hydroxydecanoyl-
CoA
(2E)-Decenoyl-CoA
H2O
NAD
3-oxodecanoyl-CoA
H+
NADH
Octanoyl-CoA
Acetyl-CoA
CoA
3-
hydroxyoctanoyl-
CoA
(2E)-Octenoyl-CoA
H2O
NAD
3-oxooctanoyl-CoA
H+
NADH
Acetyl-CoA
Hexanoyl-CoA
CoA
(2E)-Hexenoyl-CoA
3-
Hydroxyhexanoyl-
CoA
H2O
NAD
3-oxohexanoyl-CoA
NADH
H+
Acetyl-CoA
Butyryl-CoA
CoA
Crotonoyl-CoA
3-
Hydroxybutyryl-
CoA
H2O
Acetyl-CoA
Acetoacetyl-CoA
CoA
Glutaryl-CoA
CO2
NAD
NADH
H+
(2E)-
Tetradecenoyl-
CoA
H2O
Magnesium
FAD
FAD
FAD
FAD
FAD
electron-
transfer
flavoprotein
Reduced
electron-
transfer
flavoprotein
electron-
transfer
flavoprotein
Reduced
electron-
transfer
flavoprotein
electron-
transfer
flavoprotein
Reduced
electron-
transfer
flavoprotein
electron-
transfer
flavoprotein
Reduced
electron-
transfer
flavoprotein
electron-
transfer
flavoprotein
Reduced
electron-
transfer
flavoprotein
electron-
transfer
flavoprotein
Reduced
electron-
transfer
flavoprotein
Fatty Acid
Elongation in
Mitochondria
Glycerolipid
Metabolism
Phospholipid
Biosynthesis
FAD
FAD
FAD
FAD
FAD
FAD
FAD
FAD
FAD
FAD
FAD
FAD
FAD
FAD
Mitochondrial Matrix
Inner Mitochondria Membrane
Mitochondrial Intermembrane
Space
Outer Mitochondria Membrane
Cytosol
Extracellular Space