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C23H38N7O17P3S Acetyl-CoA 809.1258 17220838 ChemSpider C00318 KEGG Compound 937 ChemSpider 388353 ChemSpider (2E)-Decenoyl-CoA 439153 PubChem-compound L-Carnitine 1.0 Trifunctional enzyme subunit alpha, mitochondrial Enoyl-CoA hydratase, mitochondrial 1.0 Trifunctional enzyme subunit beta, mitochondrial C33H58N7O17P3S Lauroyl-CoA 949.2823 CHEBI:16027 ChEBI 38795-33-4 CAS Hexanoyl-CoA HMDB0001070 HMDB ATP BioCyc 1.0 Reduced electron-transfer flavoprotein HMDB0006404 HMDB P45954 UniProt 559142 ChemSpider 1.0 HMDB0006402 HMDB 1.0 Tetradecanoyl-CoA PW000048 PathWhiz 5742 ChemSpider CPD-196 BioCyc C02990 KEGG Compound C00332 KEGG Compound 11966197 PubChem-compound Trifunctional enzyme, mitochondrial 440045 PubChem-compound 1.0 SMP0000541 SMPDB HMDB0001088 HMDB 5858 ChemSpider 2364-67-2 CAS Carbon dioxide 7-METHYL-3-OXOOCTANOYL-COA BioCyc 4.0 Reduced electron-transfer flavoprotein 1010 ChemSpider Enoyl-CoA hydratase, mitochondrial SMILES CC(C)(COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N)[C@@H](O)C(=O)NCCC(=O)NCCS PPI BioCyc (2E)-Octenoyl-CoA Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial C27H46N7O17P3S Hexanoyl-CoA 865.18835 P16219 UniProt CHEBI:5086 ChEBI Medium-chain specific acyl-CoA dehydrogenase, mitochondrial LAUROYLCOA-CPD BioCyc Short-chain specific acyl-CoA dehydrogenase, mitochondrial Lauroyl-CoA Long-chain-fatty-acid--CoA ligase 1 53477508 PubChem-compound C00249 KEGG Compound 3-ketoacyl-CoA thiolase, mitochondrial C00001 KEGG Compound 1.0 SubPathwayInteraction80 SubPathway80Reaction SubPathwayReaction CHEBI:18361 ChEBI NADH C00004 KEGG Compound C00003 KEGG Compound C00002 KEGG Compound Acetyl-CoA acetyltransferase, mitochondrial 103192-48-9 CAS L-Palmitoylcarnitine P42765 UniProt Coenzyme A Mitochondrial Inner Membrane SubPathwayInteraction79 SubPathwayReaction SubPathway79Reaction L-Carnitine CHEBI:28276 ChEBI 3130-72-1 CAS 389502 ChemSpider 389501 ChemSpider C29H50N7O17P3S Octanoyl-CoA 893.21967 389500 ChemSpider SMILES C[C@@H](O)CC(=O)SCCNC(=O)CCNC(=O)C(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N C21H28N7O14P2 NAD 664.11694 389506 ChemSpider 1.0 389504 ChemSpider C00011 KEGG Compound C00010 KEGG Compound HMDB0000902 HMDB 11966160 PubChem-compound C00136 KEGG Compound C00013 KEGG Compound CHEBI:10723 ChEBI 389508 ChemSpider CHEBI:28264 ChEBI P28330 UniProt H Hydrogen Ion 1.007825 CARNITINE BioCyc C25H42N7O17P3S Butyryl-CoA 837.15704 56-65-5 CAS C00020 KEGG Compound 53-84-9 CAS 389510 ChemSpider Carnitine O-palmitoyltransferase 1 1.0 C00024 KEGG Compound (S)-Hydroxydecanoyl-CoA 1.3.8.7 false 1.3.8.7 Lauroyl-CoA + electron-transfer flavoprotein → (2E)-Tetradecenoyl-CoA + Reduced electron-transfer flavoprotein LEFT_TO_RIGHT 1264-57-9 CAS CHEBI:17490 ChEBI CHEBI:28493 ChEBI Adenosine monophosphate 4460-95-1 CAS 4.2.1.17 false 4.2.1.17 (S)-3-Hydroxydodecanoyl-CoA → (2E)-Tetradecenoyl-CoA + Water LEFT_TO_RIGHT 72059-49-5 CAS L-Palmitoylcarnitine 3-Oxohexadecanoyl-CoA C00154 KEGG Compound C37H66N7O18P3S (S)-3-Hydroxyhexadecanoyl-CoA 1021.3398 C35H62N7O18P3S (S)-3-Hydroxytetradecanoyl-CoA 993.3085 Carnitine O-palmitoyltransferase 1, liver isoform C35H60N7O18P3S 3-Oxotetradecanoyl-CoA 991.29285 4.0 Carnitine O-palmitoyltransferase 2, mitochondrial Long-chain-fatty-acid--CoA ligase 1 SMILES NC(=O)C1=CN(C=CC1)[C@@H]1O[C@H](CO[P@](O)(=O)O[P@](O)(=O)OC[C@H]2O[C@H]([C@H](O)[C@@H]2O)N2C=NC3=C(N)N=CN=C23)[C@@H](O)[C@H]1O AMP BioCyc 2871-66-1 CAS SMILES CC(=O)CC(=O)SCCNC(=O)CCNC(=O)C(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N 35106-50-4 CAS Palmitic acid HMDB0000250 HMDB SMILES [O-]P([O-])(=O)OP([O-])([O-])=O 16061159 PubChem-compound 1.0 CPD-12174 BioCyc SMILES CCCCCCCC(=O)CC(=O)SCCNC(=O)CCNC(=O)C(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C(N)N=CN=C12 SMILES [H][C@](O)(CCCCC)CC(=O)SCCNC(=O)CCNC(=O)[C@]([H])(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H](C(O)[C@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N SMILES CCCCCC(=O)CC(=O)SCCNC(=O)CCNC(=O)C(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C(N)N=CN=C12 SMILES CC(C)(COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N)C(O)C(=O)NCCC(=O)NCCSC(=O)CCCC(O)=O SMILES CCCCCCCCCCCCCCCC(=O)SCCNC(=O)CCNC(=O)C(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N C02593 KEGG Compound SMILES CCC[C@H](O)CC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N C03561 KEGG Compound C37H64N7O18P3S 3-Oxohexadecanoyl-CoA 1019.32416 SMILES CCCCCCCCC[C@H](O)CC(=O)SCCNC(=O)CCNC(=O)C(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C(N)N=CN=C12 SMILES CCCCCCCCCC(=O)CC(=O)SCCNC(=O)CCNC(=O)C(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C(N)N=CN=C12 1.0 (S)-Hydroxyoctanoyl-CoA C31H54N7O17P3S Decanoyl-CoA 921.251 SMILES CCCCCCC[C@H](O)CC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H](C(O)[C@H]1OP(O)(O)=O)N1C=NC2=C(N)N=CN=C12 1.0 7732-18-5 CAS 54684-64-9 CAS 3-OXOPALMITOYL-COA BioCyc 61-19-8 CAS HMDB0001487 HMDB 2140-48-9 CAS SMILES NC1=C2N=CN([C@@H]3O[C@H](COP(O)(O)=O)[C@@H](O)[C@H]3O)C2=NC=N1 1.0 1.0 Acetoacetyl-CoA 1.0 57-10-3 CAS 3-Oxooctanoyl-CoA Q92947 UniProt 2.0 HMDB0001484 HMDB C10H16N5O13P3 Adenosine triphosphate 506.99576 165436 PubChem-compound NAD SMILES C[N+](C)(C)C[C@H](O)CC([O-])=O HMDB0000045 HMDB 1.0 Adenosine triphosphate 962 PubChem-compound GLUTARYL-COA BioCyc Long-chain specific acyl-CoA dehydrogenase, mitochondrial trans-2-Hexenoyl-CoA CO2 Carbon dioxide 43.98983 C00080 KEGG Compound P50416 UniProt Water Long-chain specific acyl-CoA dehydrogenase, mitochondrial Enoyl-CoA hydratase, mitochondrial 1.0 HMDB0002111 HMDB 4.0 6245-70-1 CAS 6.0 1.0 1.0 1.0 Medium-chain specific acyl-CoA dehydrogenase, mitochondrial 1.0 1.0 1.0 6.0 960 ChemSpider HMDB0002009 HMDB 1.0 HMDB0003571 HMDB HMDB0000062 HMDB 1.0 1.0 1264-52-4 CAS 985 PubChem-compound 644102 PubChem-compound 444493 PubChem-compound 6083 PubChem-compound Glutaryl-CoA dehydrogenase, mitochondrial 3-Oxododecanoyl-CoA SMILES CCCC(=O)CC(=O)SCCNC(=O)CCNC(=O)C(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C(N)N=CN=C12 SMILES CCC\C=C\C(=O)SCCNC(=O)CCNC(=O)C(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N SMILES CCCCCCCCCCCCC\C=C\C(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(=O)([O-])OP([O-])(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(=O)([O-])[O-])N1C=NC2=C1N=CN=C2N ACETYL-COA BioCyc SMILES CCCCCCCCCCC\C=C\C(=O)SCCNC(=O)CCNC(=O)C(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N H2O Water 18.010565 SMILES CCCCCCC\C=C\C(=O)SCCNC(=O)CCNC(=O)C(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C(N)N=CN=C12 4.0 Carnitine O-palmitoyltransferase 2, mitochondrial SMILES CCCCC\C=C\C(=O)SCCNC(=O)CCNC(=O)C(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N P55084 UniProt NADH BioCyc HMDB0001166 HMDB NAD BioCyc Acetyl-CoA acetyltransferase, mitochondrial HMDB0059597 HMDB Acetyl-CoA 11953816 PubChem-compound SMILES CCCCCCCCCCCCCC(=O)SCCNC(=O)CCNC(=O)C(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N ReactionCatalysis279 ACTIVATION Reaction759 false (S)-3-Hydroxydodecanoyl-CoA + NAD ↔ 3-Oxododecanoyl-CoA + Hydrogen Ion + NADH REVERSIBLE ReactionCatalysis276 ACTIVATION 2.3.1.16 false 2.3.1.16 Acetyl-CoA + Decanoyl-CoA → 3-Oxododecanoyl-CoA + Coenzyme A LEFT_TO_RIGHT ReactionCatalysis275 ACTIVATION 65113 PubChem-compound (S)-3-Hydroxytetradecanoyl-CoA Reaction755 false (S)-Hydroxydecanoyl-CoA + NAD ↔ 3-Oxodecanoyl-CoA + Hydrogen Ion + NADH REVERSIBLE ReactionCatalysis272 ACTIVATION C23H45NO4 L-Palmitoylcarnitine 399.33487 78303-19-2 CAS 4.2.1.17 false 4.2.1.17 (S)-Hydroxydecanoyl-CoA ↔ (2E)-Decenoyl-CoA + Water REVERSIBLE ReactionCatalysis273 ACTIVATION ReactionCatalysis270 ACTIVATION 1.0 P49748 UniProt 3-Oxotetradecanoyl-CoA Coenzyme A 10140190 ChemSpider SMILES O Palmityl-CoA 2.3.1.16 false 2.3.1.16 Acetyl-CoA + Octanoyl-CoA ↔ 3-Oxodecanoyl-CoA + Coenzyme A REVERSIBLE 371 ChemSpider Reaction751 false (S)-Hydroxyoctanoyl-CoA + NAD ↔ 3-Oxooctanoyl-CoA + Hydrogen Ion + NADH REVERSIBLE 4.2.1.17 false 4.2.1.17 (S)-Hydroxyoctanoyl-CoA ↔ (2E)-Octenoyl-CoA + Water REVERSIBLE Glycerolipid Metabolism SubPathway C10H14N5O7P Adenosine monophosphate 347.06308 CPD-419 BioCyc 2.3.1.16 false 2.3.1.16 Acetyl-CoA + Hexanoyl-CoA ↔ 3-Oxooctanoyl-CoA + Coenzyme A REVERSIBLE P40939 UniProt ReactionCatalysis267 ACTIVATION ReactionCatalysis268 ACTIVATION ReactionCatalysis265 ACTIVATION 4.2.1.17 false 4.2.1.17 (S)-3-Hydroxyhexadecanoyl-CoA ↔ (2E)-Hexadecenoyl-CoA + Water REVERSIBLE ReactionCatalysis263 ACTIVATION 2.3.1.16 false 2.3.1.16 Acetyl-CoA + Tetradecanoyl-CoA ↔ 3-Oxohexadecanoyl-CoA + Coenzyme A REVERSIBLE Reaction767 false (S)-3-Hydroxyhexadecanoyl-CoA + NAD ↔ 3-Oxohexadecanoyl-CoA + Hydrogen Ion + NADH REVERSIBLE ReactionCatalysis262 ACTIVATION CHEBI:57371 ChEBI HMDB0000538 HMDB Carnitine O-palmitoyltransferase 1, liver isoform ReactionCatalysis260 ACTIVATION 6816 PubChem-compound HMDB0003934 HMDB HMDB0002845 HMDB HMDB0003935 HMDB HMDB0003932 HMDB 5060-32-2 CAS 4.2.1.17 false 4.2.1.17 (S)-3-Hydroxytetradecanoyl-CoA ↔ (2E)-Tetradecenoyl-CoA + Water REVERSIBLE (S)-3-Hydroxyhexadecanoyl-CoA CHEBI:15846 ChEBI Very long-chain specific acyl-CoA dehydrogenase, mitochondrial 1.0 2.3.1.16 false 2.3.1.16 Acetyl-CoA + Lauroyl-CoA → 3-Oxotetradecanoyl-CoA + Coenzyme A LEFT_TO_RIGHT C7H15NO3 L-Carnitine 161.1052 Reaction763 false (S)-3-Hydroxytetradecanoyl-CoA + NAD ↔ 3-Oxotetradecanoyl-CoA + Hydrogen Ion + NADH REVERSIBLE 102680-35-3 CAS 1.0 PALMITYL-COA BioCyc ReactionCatalysis178 ACTIVATION 1.3.8.6 false 1.3.8.6 Glutaryl-CoA → Carbon dioxide + Crotonoyl-CoA LEFT_TO_RIGHT ReactionCatalysis176 ACTIVATION ReactionCatalysis294 ACTIVATION 1.3.8.8 false 1.3.8.8 Octanoyl-CoA + electron-transfer flavoprotein → (2E)-Octenoyl-CoA + Reduced electron-transfer flavoprotein LEFT_TO_RIGHT 440608 PubChem-compound 1.3.8.8 false 1.3.8.8 Hexanoyl-CoA + electron-transfer flavoprotein → Reduced electron-transfer flavoprotein + trans-2-Hexenoyl-CoA LEFT_TO_RIGHT 1.0 SMILES CCCCCCCCCCCC(=O)CC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C(N)N=CN=C12 HMDB0003938 HMDB 440606 PubChem-compound ReactionCatalysis293 ACTIVATION SMILES CCCCCCCCCCC[C@H](O)CC(=O)SCCNC(=O)CCNC(=O)C(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C(N)N=CN=C12 HMDB0003939 HMDB ReactionCatalysis290 ACTIVATION HMDB0003936 HMDB 440604 PubChem-compound 380 PubChem-compound 5280381 PubChem-compound ReactionCatalysis291 ACTIVATION SMILES CCCCCCCCCCCCC[C@H](O)CC(=O)SCCNC(=O)CCNC(=O)C(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C(N)N=CN=C12 1038 PubChem-compound 440603 PubChem-compound HMDB0003937 HMDB 440602 PubChem-compound 265 PubChem-compound 440601 PubChem-compound 440600 PubChem-compound HMDB0003941 HMDB HMDB0003942 HMDB Fatty Acid Elongation in Mitochondria SubPathway HMDB0001521 HMDB HMDB0003940 HMDB HMDB0003945 HMDB HMDB0003946 HMDB HMDB0003943 HMDB HMDB0003944 HMDB C25H40N7O17P3S Crotonoyl-CoA 835.1414 274 ChemSpider Reaction776 false Decanoyl-CoA + electron-transfer flavoprotein → (2E)-Decenoyl-CoA + Reduced electron-transfer flavoprotein LEFT_TO_RIGHT 1.3.8.9 false 1.3.8.9 Palmityl-CoA + electron-transfer flavoprotein → (2E)-Hexadecenoyl-CoA + Reduced electron-transfer flavoprotein LEFT_TO_RIGHT 1.3.8.8 false 1.3.8.8 Tetradecanoyl-CoA + electron-transfer flavoprotein → (2E)-Tetradecenoyl-CoA + Reduced electron-transfer flavoprotein LEFT_TO_RIGHT 6.2.1.3 false 6.2.1.3 Adenosine triphosphate + Coenzyme A + Palmitic acid → Adenosine monophosphate + Palmityl-CoA + Pyrophosphate LEFT_TO_RIGHT Butyryl-CoA 2.3.1.21 false 2.3.1.21 L-Carnitine + Palmityl-CoA ↔ Coenzyme A + L-Palmitoylcarnitine REVERSIBLE CHEBI:16908 ChEBI ReactionCatalysis289 ACTIVATION K-HEXANOYL-COA BioCyc ReactionCatalysis288 ACTIVATION ReactionCatalysis285 ACTIVATION ReactionCatalysis283 ACTIVATION ReactionCatalysis284 ACTIVATION ReactionCatalysis281 ACTIVATION HMDB0003949 HMDB ReactionCatalysis280 ACTIVATION HMDB0003948 HMDB SMILES CCCCCCCCCCCCCC(=O)CC(=O)SCCNC(=O)CCNC(=O)C(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C(N)N=CN=C12 1.0 SMILES CCCCCCCCCC(=O)SCCNC(=O)CCNC(=O)C(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N Coenzyme A CHEBI:61526 ChEBI C16H32O2 Palmitic acid 256.24023 260 ChemSpider 1.0 Reaction780 false 3-Hydroxybutyryl-CoA + NAD ↔ Acetoacetyl-CoA + Hydrogen Ion + NADH REVERSIBLE CHEBI:15521 ChEBI CHEBI:15524 ChEBI CHEBI:15525 ChEBI 541-15-1 CAS C27H46N7O18P3S (S)-Hydroxyhexanoyl-CoA 881.1833 C27H44N7O18P3S 3-Oxohexanoyl-CoA 879.16766 C27H44N7O17P3S trans-2-Hexenoyl-CoA 863.1727 C37H60N7O17P3S (2E)-Hexadecenoyl-CoA 999.2979 1.0 Palmityl-CoA 4444072 ChemSpider 58-68-4 CAS C35H60N7O17P3S (2E)-Tetradecenoyl-CoA 975.2979 HMDB0001423 HMDB C31H52N7O17P3S (2E)-Decenoyl-CoA 919.23535 C29H48N7O17P3S (2E)-Octenoyl-CoA 891.20404 SMILES C\C=C\C(=O)SCCNC(=O)CCNC(=O)C(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C(N)N=CN=C12 CHEBI:28726 ChEBI 124-38-9 CAS Pyrophosphate 1.0 P30084 UniProt 10140154 ChemSpider CHEBI:15533 ChEBI CHEBI:15532 ChEBI 1.0 (2E)-Hexadecenoyl-CoA 3-Oxohexanoyl-CoA Acetyl-CoA acetyltransferase, mitochondrial 1.0 CHEBI:28706 ChEBI 440615 PubChem-compound 1763-10-6 CAS TETRADECANOYL-COA BioCyc CPD-1083 BioCyc C05259 KEGG Compound C05258 KEGG Compound 440610 PubChem-compound HMDB0000222 HMDB C05264 KEGG Compound Short-chain specific acyl-CoA dehydrogenase, mitochondrial C05263 KEGG Compound C05266 KEGG Compound C05265 KEGG Compound SMILES CCCCCCCCCCCCCCCC(=O)O[C@H](CC([O-])=O)C[N+](C)(C)C P23786 UniProt C05260 KEGG Compound 4.0 2.0 GO:0005759 GENE ONTOLOGY Octanoyl-CoA SMILES CCCCCCCCCCCCCCCC(O)=O C05262 KEGG Compound P24752 UniProt 4.0 C05261 KEGG Compound CHEBI:27868 ChEBI 19774-86-8 CAS SMP0000054 SMPDB HMDB0000220 HMDB C35H62N7O17P3S Tetradecanoyl-CoA 977.3136 electron-transfer flavoprotein Short-chain specific acyl-CoA dehydrogenase, mitochondrial Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial SMILES O=C=O C05268 KEGG Compound Very long-chain specific acyl-CoA dehydrogenase, mitochondrial C05267 KEGG Compound Hydrogen Ion C05269 KEGG Compound 1.0 C05275 KEGG Compound O7P2 Pyrophosphate 173.91193 C05274 KEGG Compound C25H40N7O18P3S Acetoacetyl-CoA 851.13635 C05276 KEGG Compound C21H29N7O14P2 NADH 665.12476 C05271 KEGG Compound C05270 KEGG Compound C05273 KEGG Compound 5957 PubChem-compound C05272 KEGG Compound HMDB0001206 HMDB GO:0005743 GENE ONTOLOGY GO:0005741 GENE ONTOLOGY Decanoyl-CoA PW000517 PathWhiz 1.0 34619-89-1 CAS 1.0 4.2.1.17 false 4.2.1.17 (S)-Hydroxyhexanoyl-CoA ↔ Water + trans-2-Hexenoyl-CoA REVERSIBLE 1.0 2.3.1.16 false 2.3.1.16 Acetyl-CoA + Butyryl-CoA → 3-Oxohexanoyl-CoA + Coenzyme A LEFT_TO_RIGHT Reaction747 false (S)-Hydroxyhexanoyl-CoA + NAD ↔ 3-Oxohexanoyl-CoA + Hydrogen Ion + NADH REVERSIBLE CHEBI:15756 ChEBI Palmityl-CoA SubPathwayInteraction809 SubPathwayReaction SubPathway809Reaction L-Palmitoylcarnitine (2E)-Hexadecenoyl-CoA C37H66N7O17P3S Palmityl-CoA 1005.34485 C33H58N7O18P3S (S)-3-Hydroxydodecanoyl-CoA 965.27716 C26H42N7O19P3S Glutaryl-CoA 881.1469 CHEBI:27721 ChEBI C33H56N7O18P3S 3-Oxododecanoyl-CoA 963.26154 C31H54N7O18P3S (S)-Hydroxydecanoyl-CoA 937.2459 GO:0005737 GENE ONTOLOGY 1.0 C31H52N7O18P3S 3-Oxodecanoyl-CoA 935.2302 C29H50N7O18P3S (S)-Hydroxyoctanoyl-CoA 909.2146 HMDB0001339 HMDB HMDB0001338 HMDB C29H48N7O18P3S 3-Oxooctanoyl-CoA 907.1989 P33121 UniProt Phospholipid Biosynthesis SubPathway ReactionCatalysis311 ACTIVATION ReactionCatalysis312 ACTIVATION Mitochondrial Outer Membrane 58623 ChemSpider 10018-95-8 CAS 79171-47-4 CAS electron-transfer flavoprotein SMILES NC(=O)C1=C[N+](=CC=C1)[C@@H]1O[C@H](COP(O)(=O)OP(O)(=O)OC[C@H]2O[C@H]([C@H](O)[C@@H]2O)N2C=NC3=C2N=CN=C3N)[C@@H](O)[C@H]1O 3-Oxodecanoyl-CoA 1.0 Transport21 false L-Palmitoylcarnitine (→) Transport: Homo sapiens, Cell, Cytoplasm to Homo sapiens, Cell, Mitochondrial Matrix LEFT_TO_RIGHT 5682 ChemSpider SMILES CCCCCCCC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N 2-METHYL-3-HYDROXY-BUTYRYL-COA BioCyc Reduced electron-transfer flavoprotein 5280765 PubChem-compound CHEBI:1146900 ChEBI 4.0 CHEBI:28528 ChEBI ReactionCatalysis308 ACTIVATION ReactionCatalysis309 ACTIVATION Mitochondrial Matrix ReactionCatalysis307 ACTIVATION 5280769 PubChem-compound ReactionCatalysis304 ACTIVATION 50411-91-1 CAS ReactionCatalysis305 ACTIVATION 5280767 PubChem-compound ReactionCatalysis302 ACTIVATION 14000-31-8 CAS 5280768 PubChem-compound ReactionCatalysis303 ACTIVATION ReactionCatalysis300 ACTIVATION 395736 ChemSpider CO-A BioCyc CPD-8475 BioCyc 72-89-9 CAS CHEBI:15452 ChEBI 1.0 SMILES CCCC(=O)SCCNC(=O)CCNC(=O)C(O)C(C)(C)COP(O)(=O)OP(O)(=O)OCC1OC(C(O)C1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N 389056 ChemSpider ReactionCatalysis2149 ACTIVATION CHEBI:28632 ChEBI C21H36N7O16P3S Coenzyme A 767.11523 10917 PubChem-compound 4.0 CHEBI:27668 ChEBI 1.0 79171-48-5 CAS 10128117 ChemSpider Cytoplasm 3-Hydroxybutyryl-CoA 1.0 10455 ChemSpider CHEBI:27540 ChEBI Trifunctional enzyme subunit beta, mitochondrial C01944 KEGG Compound ACETOACETYL-COA BioCyc 14902 ChemSpider 1.0 CHEBI:15422 ChEBI Very long-chain specific acyl-CoA dehydrogenase, mitochondrial 6557 ChemSpider ReactionCatalysis2150 ACTIVATION 1.0 Homo sapiens SMILES CC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N 1.0 388299 ChemSpider Crotonoyl-CoA 439214 PubChem-compound (S)-3-Hydroxydodecanoyl-CoA CHEBI:27537 ChEBI SMP0000025 SMPDB Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial ReactionCatalysis2153 ACTIVATION SMILES CCCCCCCCCCCC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C(N)N=CN=C12 Palmitic acid SubPathwayOutput SubPathwayInput C01832 KEGG Compound P11310 UniProt CHEBI:16526 ChEBI SMP0000039 SMPDB 449118 PubChem-compound 122364-86-7 CAS Medium-chain specific acyl-CoA dehydrogenase, mitochondrial CHEBI:27402 ChEBI CHEBI:27648 ChEBI (S)-Hydroxyhexanoyl-CoA 1.0 9606 TAXONOMY Acetyl-CoA acyltransferase T2-DECENOYL-COA BioCyc C00877 KEGG Compound PW000144 PathWhiz PW000022 PathWhiz 1.3.8.8 false 1.3.8.8 Butyryl-CoA + electron-transfer flavoprotein ↔ Crotonoyl-CoA + Reduced electron-transfer flavoprotein REVERSIBLE 392413 ChemSpider 4.2.1.17 false 4.2.1.17 3-Hydroxybutyryl-CoA ↔ Crotonoyl-CoA + Water REVERSIBLE 145018 ChemSpider 10018-93-6 CAS 5893 PubChem-compound C25H42N7O18P3S 3-Hydroxybutyryl-CoA 853.152 Glutaryl-CoA dehydrogenase, mitochondrial CHEBI:28325 ChEBI Trifunctional enzyme subunit alpha, mitochondrial 1420-36-6 CAS CHEBI:15377 ChEBI CHEBI:16347 ChEBI 3-ketoacyl-CoA thiolase, mitochondrial CHEBI:15378 ChEBI SMILES [H+] C00527 KEGG Compound SMILES NC1=NC=NC2=C1N=CN2[C@@H]1O[C@H](COP(O)(=O)OP(O)(=O)OP(O)(O)=O)[C@@H](O)[C@H]1O CHEBI:15491 ChEBI 389499 ChemSpider 389498 ChemSpider CHEBI:27466 ChEBI 280 PubChem-compound Glutaryl-CoA dehydrogenase, mitochondrial 26332261 ChemSpider 2.3.1.9 false 2.3.1.9 2 Acetyl-CoA ↔ Acetoacetyl-CoA + Coenzyme A REVERSIBLE 4444333 ChemSpider 1.0 4444334 ChemSpider 1.0 4444335 ChemSpider SMILES CCCCCC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N CHEBI:15345 ChEBI (2E)-Tetradecenoyl-CoA Glutaryl-CoA 4.0 4444331 ChemSpider 46173176 PubChem-compound 6244-92-4 CAS 10018-94-7 CAS 1.0 439252 PubChem-compound 15667 PubChem-compound 1.0 Long-chain specific acyl-CoA dehydrogenase, mitochondrial L-Palmitoylcarnitine HMDB0001967 HMDB 1.0 electron-transfer flavoprotein CHEBI:15351 ChEBI 388388 ChemSpider CHEBI:15473 ChEBI 85-61-0 CAS Carnitine Palmitoyl Transferase Deficiency II Carnitine O- palmitoyltransferase 2, mitochondrial Enoyl-CoA hydratase, mitochondrial Trifunctional enzyme subunit alpha, mitochondrial Trifunctional enzyme subunit beta, mitochondrial 3-ketoacyl-CoA thiolase, mitochondrial Carnitine O- palmitoyltransferase 1, liver isoform Long-chain- fatty-acid-- CoA ligase 1 Enoyl-CoA hydratase, mitochondrial Trifunctional enzyme subunit alpha, mitochondrial Trifunctional enzyme subunit beta, mitochondrial 3-ketoacyl-CoA thiolase, mitochondrial Trifunctional enzyme subunit alpha, mitochondrial Trifunctional enzyme subunit beta, mitochondrial 3-ketoacyl-CoA thiolase, mitochondrial Enoyl-CoA hydratase, mitochondrial Trifunctional enzyme subunit alpha, mitochondrial Trifunctional enzyme subunit beta, mitochondrial 3-ketoacyl-CoA thiolase, mitochondrial Enoyl-CoA hydratase, mitochondrial Trifunctional enzyme subunit alpha, mitochondrial Trifunctional enzyme subunit beta, mitochondrial 3-ketoacyl-CoA thiolase, mitochondrial Long-chain specific acyl-CoA dehydrogenase, mitochondrial Medium-chain specific acyl-CoA dehydrogenase, mitochondrial Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial Short-chain specific acyl-CoA dehydrogenase, mitochondrial Enoyl-CoA hydratase, mitochondrial Trifunctional enzyme subunit alpha, mitochondrial Trifunctional enzyme subunit beta, mitochondrial 3-ketoacyl-CoA thiolase, mitochondrial Long-chain specific acyl-CoA dehydrogenase, mitochondrial Medium-chain specific acyl-CoA dehydrogenase, mitochondrial Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial Enoyl-CoA hydratase, mitochondrial