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Cystinosin Glutamate-- cysteine ligase Cysteine dioxygenase type 1 Aspartate aminotransferase, cytoplasmic Cystathionine gamma-lyase Thiosulfate sulfurtransferase Aspartate aminotransferase, cytoplasmic Ubiquitin- conjugating enzyme E2 variant 3 Cysteine--tRNA ligase, cytoplasmic L-Glutamic acid γ- Glutamylcysteine L-Cysteine 3- Sulfinoalanine Pyruvic acid L-Cysteine ATP ADP Pi O2 Oxoglutaric acid 3- Sulfinylpyruvic acid L-Glutamic acid H2O Sulfite H2O Hydrogen sulfide NH3 3- Mercaptopyruvic acid Cyanide Thiocyanate Oxoglutaric acid L-Glutamic acid 3- Mercaptolactic acid NAD NADH ATP AMP PPi Fe2+ Pyridoxal 5'-phosphate Pyridoxal 5'-phosphate Pyridoxal 5'-phosphate Zinc (II) ion tRNA(Cys) L- Cysteinyl- tRNA(Cys) Glutamate Metabolism Glutamate Metabolism Methionine Metabolism Glycine and Serine Metabolism Pantothenate and CoA Biosynthesis Taurine and Hypotaurine Metabolism Sulfate/Sulfite Metabolism Pyruvate Metabolism Extracellular Space Intracellular Space Intracellular Space Extracellular Space
Ctns Gclc Gclm Cdo1 Got1 Cth Tst Got1 Uevld Cars L-Glutamic acid γ- Glutamylcysteine L-Cysteine 3- Sulfinoalanine Pyruvic acid L-Cysteine Adenosine triphosphate Adenosine diphosphate Phosphoric acid Oxygen Oxoglutaric acid 3- Sulfinylpyruvic acid L-Glutamic acid Water Sulfite Water Hydrogen sulfide Ammonia 3- Mercaptopyruvic acid Cyanide Thiocyanate Oxoglutaric acid L-Glutamic acid 3- Mercaptolactic acid NAD NADH Adenosine triphosphate Adenosine monophosphate Pyrophosphate tRNA(Cys) L- Cysteinyl- tRNA(Cys) Glutamate Metabolism Glutamate Metabolism Methionine Metabolism Glycine and Serine Metabolism Pantothenate and CoA Biosynthesis Taurine and Hypotaurine Metabolism Sulfate/Sulfite Metabolism Pyruvate Metabolism
Ctns Gclc Gclm Cdo1 Got1 Cth Tst Got1 Uevld Cars Glu γGluCys Cys 3S-Ala Pyr Cys ATP ADP Pi O2 AKG 3Sulfpa Glu H2O Sulfite H2O H2SO NH3 3McPyra Cyanide SCN AKG Glu 3-Mcla NAD NADH ATP AMP PPi Fe2+ Pyr-5'P Pyr-5'P Pyr-5'P Zinc TRNACYS LCTC PW000003 PW000003 PW000056 PW000157 PW000032 PW000038 PW000040 PW000054 Extracellular Space Intracellular Space Intracellular Space Extracellular Space
Ctns Gclc Gclm Cdo1 Got1 Cth Tst Got1 Uevld Cars Glu γGluCys Cys 3S-Ala Pyr Cys ATP ADP PhosfrA O2 AKG 3Sulfpa Glu H2O Sulfite H2O H2SO NH3 3McPyra Cyanide SCN AKG Glu 3-Mcla NAD NADH ATP AMP Ppi TRNACYS LCTC PW000003 PW000003 PW000056 PW000157 PW000032 PW000038 PW000040 PW000054