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Mitochondria Chloroplast Peroxisome Branched- chain-amino- acid aminotransferase 1, mitochondrial Branched- chain-amino- acid aminotransferase 6 Branched- chain-amino- acid aminotransferase 2, chloroplastic Branched- chain-amino- acid aminotransferase 3, chloroplastic Branched- chain-amino- acid aminotransferase 5, chloroplastic 2- oxoisovalerate dehydrogenase subunit alpha 2, mitochondrial 2- oxoisovalerate dehydrogenase subunit beta 2, mitochondrial Lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial Dihydrolipoyl dehydrogenase 2, mitochondrial Isovaleryl-CoA dehydrogenase, mitochondrial 3- hydroxyisobutyryl- CoA hydrolase 1 Probable 3- hydroxyisobutyrate dehydrogenase, mitochondrial Methylmalonate- semialdehyde dehydrogenase [acylating], mitochondrial α- Ketoisovaleric acid α- Ketoisovaleric acid L-Valine Oxoglutaric acid L-Glutamic acid L-Valine Oxoglutaric acid L-Glutamic acid L-Valine Oxoglutaric acid L-Glutamic acid L-Valine Oxoglutaric acid L-Glutamic acid L-Valine Oxoglutaric acid L-Glutamic acid CoA NAD 2- Methylpropanal CO2 NADH FAD H+ FADH2 Methacrylyl-CoA H2O (S)-3- Hydroxyisobutyryl- CoA H2O CoA (S)-3- Hydroxyisobutyric acid H+ NAD H+ NADH (S)- Methylmalonic acid semialdehyde L-Glutamic acid Oxoglutaric acid (S)-beta- Aminoisobutyric acid H2O NAD CoA Propionyl-CoA NADH H+ HCO3-
Mitochondria Chloroplast Peroxisome BCAT1 BCAT6 BCAT2 BCAT3 BCAT5 At5g09300 DIN4 BCE2 LPD2 IVD CHY1 At4g20930 ALDH6B2 α- Ketoisovaleric acid α- Ketoisovaleric acid L-Valine Oxoglutaric acid L-Glutamic acid L-Valine Oxoglutaric acid L-Glutamic acid L-Valine Oxoglutaric acid L-Glutamic acid L-Valine Oxoglutaric acid L-Glutamic acid L-Valine Oxoglutaric acid L-Glutamic acid Coenzyme A NAD 2- Methylpropanal Carbon dioxide NADH FAD Hydrogen Ion FADH Methacrylyl-CoA Water (S)-3- Hydroxyisobutyryl- CoA Water Coenzyme A (S)-3- Hydroxyisobutyric acid Hydrogen Ion NAD Hydrogen Ion NADH (S)- Methylmalonic acid semialdehyde L-Glutamic acid Oxoglutaric acid (S)-beta- Aminoisobutyric acid Water NAD Coenzyme A Propionyl-CoA NADH Hydrogen Ion Hydrogen carbonate
Mitochondria Chloroplast Peroxisome BCAT1 BCAT6 BCAT2 BCAT3 BCAT5 At5g09300 DIN4 BCE2 LPD2 IVD CHY1 At4g20930 ALDH6B2 Ketoval Ketoval Val AKG Glu Val AKG Glu Val AKG Glu Val AKG Glu Val AKG Glu CoA NAD 2Methy CO2 NADH FAD H+ FADH2 McryCoA H2O 3HIsoCA H2O CoA 3-HIBA H+ NAD H+ NADH 22M3O Glu AKG L2MBA H2O NAD CoA PropCoA NADH H+ HCO3-
Mitochondria Chloroplast Peroxisome BCAT1 BCAT6 BCAT2 BCAT3 BCAT5 At5g09300 DIN4 BCE2 LPD2 IVD CHY1 At4g20930 ALDH6B2 Ketoval Ketoval Val AKG Glu Val AKG Glu Val AKG Glu Val AKG Glu Val AKG Glu CoA NAD 2Methy CO2 NADH FAD H+ FADH McryCoA H2O 3HIsoCA H2O CoA 3-HIBA H+ NAD H+ NADH 22M3O Glu AKG L2MBA H2O NAD CoA PropCoA NADH H+ HCO3