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Aspartate aminotransferase, cytoplasmic Amine oxidase [flavin- containing] B Tyrosine aminotransferase Phenylalanine- 4-hydroxylase Tyrosine aminotransferase Amine oxidase [flavin- containing] B Aminoacyl tRNA synthase complex- interacting multifunctional protein 1 Alanine--tRNA ligase, cytoplasmic 4- hydroxyphenylpyruvate dioxygenase Homogentisate 1,2-dioxygenase Maleylacetoacetate isomerase Fumarylacetoacetase L-Tyrosine Fumaric acid Acetoacetic acid L-Phenylalanine Oxoglutaric acid Phenylpyruvic acid L-Glutamic acid H2O O2 NH3 H2O2 Oxoglutaric acid L-Glutamic acid L-erythro- tetrahydrobiopterin O2 4a- Hydroxytetrahydrobiopterin Oxoglutaric acid 4- Hydroxyphenylpyruvic acid L-Glutamic acid Oxoglutaric acid L-Glutamic acid H2O O2 NH3 H2O2 ATP AMP PPi ATP AMP PPi O2 Homogentisic acid CO2 O2 Maleylacetoacetic acid 4- Fumarylacetoacetic acid H2O Pyridoxal 5'-phosphate FAD Pyridoxal 5'-phosphate Fe2+ Pyridoxal 5'-phosphate FAD Fe3+ Iron Calcium Magnesium tRNA(Tyr) L-Tyrosyl- tRNA(Tyr) tRNA(Phe) L- Phenylalanyl- tRNA(Phe) Catecholamine Biosynthesis Tyrosine Metabolism Citric Acid Cycle Intracellular Space Extracellular Space Liver
Got1 Maob Tat Pah Tat Maob Aimp1 Farsa Lrrc47 Hpd Hgd Gstz1 Fah L-Tyrosine Fumaric acid Acetoacetic acid L-Phenylalanine Oxoglutaric acid Phenylpyruvic acid L-Glutamic acid Water Oxygen Ammonia Hydrogen peroxide Oxoglutaric acid L-Glutamic acid L-erythro- tetrahydrobiopterin Oxygen 4a- Hydroxytetrahydrobiopterin Oxoglutaric acid 4- Hydroxyphenylpyruvic acid L-Glutamic acid Oxoglutaric acid L-Glutamic acid Water Oxygen Ammonia Hydrogen peroxide Adenosine triphosphate Adenosine monophosphate Pyrophosphate Adenosine triphosphate Adenosine monophosphate Pyrophosphate Oxygen Homogentisic acid Carbon dioxide Oxygen Maleylacetoacetic acid 4- Fumarylacetoacetic acid Water tRNA(Tyr) L-Tyrosyl- tRNA(Tyr) tRNA(Phe) L- Phenylalanyl- tRNA(Phe) Catecholamine Biosynthesis Tyrosine Metabolism Citric Acid Cycle
Got1 Maob Tat Pah Tat Maob Aimp1 Farsa Lrrc47 Hpd Hgd Gstz1 Fah Tyr Fumarat LIN Phe AKG Ppyr Glu H2O O2 NH3 H2O2 AKG Glu EryTbpn O2 4aHtHbp AKG 4HPPA Glu AKG Glu H2O O2 NH3 H2O2 ATP AMP PPi ATP AMP PPi O2 HMGNCA CO2 O2 MalaceA Fumaryl H2O Pyr-5'P FAD Pyr-5'P Fe2+ Pyr-5'P FAD Fe3+ Iron Ca2+ Mg2+ TRNATYR LTTT TRNAPHE LPTP PW000017 PW000142 PW000005 Intracellular Space Extracellular Space Liver
Got1 Maob Tat Pah Tat Maob Aimp1 Farsa Lrrc47 Hpd Hgd Gstz1 Fah Tyr Fumarat LIN Phe AKG Ppyr Glu H2O O2 NH3 H2O2 AKG Glu EryTbpn O2 4aHtHbp AKG 4HPPA Glu AKG Glu H2O O2 NH3 H2O2 ATP AMP Ppi ATP AMP Ppi O2 HMGNCA CO2 O2 MalaceA Fumaryl H2O TRNATYR LTTT TRNAPHE LPTP PW000017 PW000142 PW000005