Mitochondrial
pyruvate
carrier 1
Pyruvate
dehydrogenase
complex
Citrate
synthase 3
Unknown
Homoisocitrate
dehydrogenase,
mitochondrial
Succinyl-CoA
ligase
Fumarate
hydratase,
mitochondrial
Acetyl-CoA
carboxylase
Succinate
dehydrogenase
3-
isopropylmalate
dehydratase
3-
isopropylmalate
dehydratase
Pyruvic acid
Oxalacetic acid
Fumaric acid
Succinic acid
FADH
2
Oxoglutaric acid
Acetyl-CoA
Pyruvic acid
CoA
NAD
CO
2
NADH
H
2
O
Citric acid
CoA
Isocitric acid
NAD
CO
2
NADH
H
+
Succinyl-CoA
P
i
GDP
CoA
GTP
L-Malic acid
H
2
O
NAD
NADH
H
+
ATP
HCO
3
-
ADP
P
i
Q
FAD
QH
2
cis-Aconitic acid
H
2
O
H
2
O
Thiamine
pyrophosphate
Lipoamide
FAD
Magnesium
Biotin
Manganese
4Fe-4S
4Fe-4S
Gluconeogenesis
Glycolysis
Pyruvate
Metabolism
Malate-
Aspartate
Shuttle
Gluconeogenesis
Alanine
Metabolism
Aspartate
Metabolism
Pyruvate
Metabolism
Aspartate
Metabolism
Tyrosine
Metabolism
Arginine and
Proline
Metabolism
Urea Cycle
Propanoate
Metabolism
Mitochondrial
Electron
Transport
Chain
Malate-
Aspartate
Shuttle
Glutamate
Metabolism
Alanine
Metabolism
Gluconeogenesis
Glucose-Alanine
Cycle
Valine,
Leucine, and
Isoleucine
Degradation
Tryptophan
Metabolism
Pyruvate
Metabolism
Fatty Acid
Metabolism
Ketone Body
Metabolism
Lysine
Degradation
Oxidation of
Branched-Chain
Fatty Acids
Propanoate
Metabolism
Homoisocitrate
dehydrogenase,
mitochondrial
Inner mitochondrial
membrane
Mitochondrial intermembrane
space
Cytosol
Mitochondrial matrix
Mitochondrion
Intracellular Space
Inner mitochondrial
membrane
Outer mitochondrial
membrane