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Carnitine O- acetyltransferase, mitochondrial 3- hydroxyisobutyryl- CoA hydrolase, mitochondrial Unknown 3-ketoacyl-CoA thiolase, peroxisomal 3-ketoacyl-CoA thiolase, peroxisomal Carnitine O- acetyltransferase YAT2 Long-chain- fatty-acid-- CoA ligase 4 3- hydroxyisobutyryl- CoA hydrolase, mitochondrial Unknown 3-ketoacyl-CoA thiolase, peroxisomal 3-ketoacyl-CoA thiolase, peroxisomal Unknown 3-ketoacyl-CoA thiolase, peroxisomal 3-ketoacyl-CoA thiolase, peroxisomal 3- hydroxyisobutyryl- CoA hydrolase, mitochondrial Unknown 3-ketoacyl-CoA thiolase, peroxisomal 3-ketoacyl-CoA thiolase, peroxisomal 3- hydroxyisobutyryl- CoA hydrolase, mitochondrial Unknown 3-ketoacyl-CoA thiolase, peroxisomal 3-ketoacyl-CoA thiolase, peroxisomal Unknown Unknown Unknown Unknown 3- hydroxyisobutyryl- CoA hydrolase, mitochondrial Unknown 3-ketoacyl-CoA thiolase, peroxisomal 3-ketoacyl-CoA thiolase, peroxisomal Unknown Unknown Unknown 3- hydroxyisobutyryl- CoA hydrolase, mitochondrial 3-ketoacyl-CoA thiolase, peroxisomal Unknown Unknown 3-ketoacyl-CoA thiolase, peroxisomal Unknown Unknown Unknown Unknown Unknown Unknown Unknown 3- hydroxyisobutyryl- CoA hydrolase, mitochondrial Unknown Unknown Unknown Unknown Palmitic acid L- Palmitoylcarnitine L- Palmitoylcarnitine Palmityl-CoA L-Carnitine CoA 3- Hydroxyhexadecanoyl- CoA (2E)- Hexadecenoyl- CoA H2O NAD 3- Oxohexadecanoyl- CoA NADH H+ Tetradecanoyl- CoA Acetyl-CoA CoA Palmityl-CoA L-Carnitine CoA ATP CoA AMP PPi 3- Hydroxytetradecanoyl- CoA (2E)- Tetradecenoyl- CoA H2O NAD 3- Oxotetradecanoyl- CoA NADH H+ Lauroyl-CoA Acetyl-CoA CoA 3- Hydroxydodecanoyl- CoA NAD 3- Oxododecanoyl- CoA NADH H+ Decanoyl-CoA Acetyl-CoA CoA 3- Hydroxydecanoyl- CoA (2E)- Decenoyl-CoA H2O NAD 3- Oxodecanoyl- CoA H+ NADH Octanoyl-CoA Acetyl-CoA CoA 3- Hydroxyoctanoyl- CoA (2E)- Octenoyl-CoA H2O NAD 3- Oxooctanoyl- CoA H+ NADH Acetyl-CoA Hexanoyl-CoA CoA (2E)- Hexenoyl-CoA 3- Hydroxyhexanoyl- CoA H2O NAD 3- Oxohexanoyl- CoA NADH H+ Acetyl-CoA Butyryl-CoA CoA Crotonoyl-CoA 3- Hydroxybutyryl- CoA H2O Acetyl-CoA Acetoacetyl-CoA CoA Glutaryl-CoA CO2 NAD NADH H+ (2E)- Tetradecenoyl- CoA H2O Magnesium FAD FAD FAD FAD FAD FAD FAD FAD FAD FAD FAD FAD FAD FAD FAD FAD FAD FAD FAD electron- transfer flavoprotein Reduced electron- transfer flavoprotein electron- transfer flavoprotein Reduced electron- transfer flavoprotein electron- transfer flavoprotein Reduced electron- transfer flavoprotein electron- transfer flavoprotein Reduced electron- transfer flavoprotein electron- transfer flavoprotein Reduced electron- transfer flavoprotein electron- transfer flavoprotein Reduced electron- transfer flavoprotein Fatty Acid Elongation in Mitochondria Glycerolipid Metabolism Phospholipid Biosynthesis Mitochondrial Matrix Inner Mitochondria Membrane Mitochondrial Intermembrane Space Outer Mitochondria Membrane Intracellular Space Extracellular Space
CAT2 EHD3 Unknown POT1 POT1 YAT2 FAA4 EHD3 Unknown POT1 POT1 Unknown POT1 POT1 EHD3 Unknown POT1 POT1 EHD3 Unknown POT1 POT1 Unknown Unknown Unknown Unknown EHD3 Unknown POT1 POT1 Unknown Unknown Unknown EHD3 POT1 Unknown Unknown POT1 Unknown Unknown Unknown Unknown Unknown Unknown Unknown EHD3 Unknown Unknown Unknown Unknown Palmitic acid L- Palmitoylcarnitine L- Palmitoylcarnitine Palmityl-CoA L-Carnitine Coenzyme A 3- Hydroxyhexadecanoyl- CoA (2E)- Hexadecenoyl- CoA Water NAD 3- Oxohexadecanoyl- CoA NADH Hydrogen Ion Tetradecanoyl- CoA Acetyl-CoA Coenzyme A Palmityl-CoA L-Carnitine Coenzyme A Adenosine triphosphate Coenzyme A Adenosine monophosphate Pyrophosphate 3- Hydroxytetradecanoyl- CoA (2E)- Tetradecenoyl- CoA Water NAD 3- Oxotetradecanoyl- CoA NADH Hydrogen Ion Lauroyl-CoA Acetyl-CoA Coenzyme A 3- Hydroxydodecanoyl- CoA NAD 3- Oxododecanoyl- CoA NADH Hydrogen Ion Decanoyl-CoA Acetyl-CoA Coenzyme A 3- Hydroxydecanoyl- CoA (2E)- Decenoyl-CoA Water NAD 3- Oxodecanoyl- CoA Hydrogen Ion NADH Octanoyl-CoA Acetyl-CoA Coenzyme A 3- Hydroxyoctanoyl- CoA (2E)- Octenoyl-CoA Water NAD 3- Oxooctanoyl- CoA Hydrogen Ion NADH Acetyl-CoA Hexanoyl-CoA Coenzyme A (2E)- Hexenoyl-CoA 3- Hydroxyhexanoyl- CoA Water NAD 3- Oxohexanoyl- CoA NADH Hydrogen Ion Acetyl-CoA Butyryl-CoA Coenzyme A Crotonoyl-CoA 3- Hydroxybutyryl- CoA Water Acetyl-CoA Acetoacetyl-CoA Coenzyme A Glutaryl-CoA Carbon dioxide NAD NADH Hydrogen Ion (2E)- Tetradecenoyl- CoA Water electron- transfer flavoprotein Reduced electron- transfer flavoprotein electron- transfer flavoprotein Reduced electron- transfer flavoprotein electron- transfer flavoprotein Reduced electron- transfer flavoprotein electron- transfer flavoprotein Reduced electron- transfer flavoprotein electron- transfer flavoprotein Reduced electron- transfer flavoprotein electron- transfer flavoprotein Reduced electron- transfer flavoprotein Fatty Acid Elongation in Mitochondria Glycerolipid Metabolism Phospholipid Biosynthesis
CAT2 EHD3 POT1 POT1 YAT2 FAA4 EHD3 POT1 POT1 POT1 POT1 EHD3 POT1 POT1 EHD3 POT1 POT1 EHD3 POT1 POT1 EHD3 POT1 POT1 EHD3 16:0 L-Plmtc L-Plmtc COA16:0 L-Carnt CoA BHC (E)-C16 H2O NAD 3OHDCoA NADH H+ COA14:0 Ac-CoA CoA COA16:0 L-Carnt CoA ATP CoA AMP PPi S3HTCoA 2TCoA H2O NAD 3OTDCoA NADH H+ COA12:0 Ac-CoA CoA S3HDCoA NAD 3ODDCoA NADH H+ Decanoy Ac-CoA CoA SHD-CoA 2DCoA H2O NAD 3ODCCoA H+ NADH COA8:0 Ac-CoA CoA S-HOCoA 2OCoA H2O NAD 3OOACoA H+ NADH Ac-CoA COA6:0 CoA T2HCoA S-HHxCA H2O NAD 3OHOCoA NADH H+ Ac-CoA Btyl-CA CoA CrtylCA 3HB-CoA H2O Ac-CoA ActaCoA CoA GlutCoA CO2 NAD NADH H+ 2TCoA H2O Mg2+ FAD FAD FAD FAD FAD FAD FAD FAD FAD FAD FAD FAD FAD FAD FAD FAD FAD FAD FAD ETF RETF ETF RETF ETF RETF ETF RETF ETF RETF ETF RETF PW000022 PW000144 PW000048 Mitochondrial Matrix Inner Mitochondria Membrane Mitochondrial Intermembrane Space Outer Mitochondria Membrane Intracellular Space Extracellular Space
CAT2 EHD3 POT1 POT1 YAT2 FAA4 EHD3 POT1 POT1 POT1 POT1 EHD3 POT1 POT1 EHD3 POT1 POT1 EHD3 POT1 POT1 EHD3 POT1 POT1 EHD3 16:0 L-Plmtc L-Plmtc COA16:0 L-Carnt CoA BHC (E)-C16 H2O NAD 3OHDCoA NADH H+ COA14:0 Ac-CoA CoA COA16:0 L-Carnt CoA ATP CoA AMP Ppi S3HTCoA 2TCoA H2O NAD 3OTDCoA NADH H+ COA12:0 Ac-CoA CoA S3HDCoA NAD 3ODDCoA NADH H+ Decanoy Ac-CoA CoA SHD-CoA 2DCoA H2O NAD 3ODCCoA H+ NADH COA8:0 Ac-CoA CoA S-HOCoA 2OCoA H2O NAD 3OOACoA H+ NADH Ac-CoA COA6:0 CoA T2HCoA S-HHxCA H2O NAD 3OHOCoA NADH H+ Ac-CoA Btyl-CA CoA CrtylCA 3HB-CoA H2O Ac-CoA ActaCoA CoA GlutCoA CO2 NAD NADH H+ 2TCoA H2O ETF RETF ETF RETF ETF RETF ETF RETF ETF RETF ETF RETF PW000022 PW000144 PW000048