SMPDB

Showing 21 - 40 of 1576 proteins

Protein ID	Protein Description	Pathway Class	Pathways
P62333 View in UniProt	26S protease regulatory subunit 10B Gene Name: PSMC6 The 26S protease is involved in the ATP-dependent degradation of ubiquitinated proteins. The regulatory (or ATPase) complex confers ATP dependency and substrate specificity to the 26S complex.	Metabolic	Ubiquitin–Proteasome Pathway
P62191 View in UniProt	26S protease regulatory subunit 4 Gene Name: PSMC1 The 26S protease is involved in the ATP-dependent degradation of ubiquitinated proteins. The regulatory (or ATPase) complex confers ATP dependency and substrate specificity to the 26S complex.	Metabolic	Ubiquitin–Proteasome Pathway
P17980 View in UniProt	26S protease regulatory subunit 6A Gene Name: PSMC3 The 26S protease is involved in the ATP-dependent degradation of ubiquitinated proteins. The regulatory (or ATPase) complex confers ATP dependency and substrate specificity to the 26S complex (By similarity). In case of HIV-1 infection, suppresses Tat-mediated transactivation.	Metabolic	Ubiquitin–Proteasome Pathway
P43686 View in UniProt	26S protease regulatory subunit 6B Gene Name: PSMC4 The 26S protease is involved in the ATP-dependent degradation of ubiquitinated proteins. The regulatory (or ATPase) complex confers ATP dependency and substrate specificity to the 26S complex.	Metabolic	Ubiquitin–Proteasome Pathway
P35998 View in UniProt	26S protease regulatory subunit 7 Gene Name: PSMC2 The 26S protease is involved in the ATP-dependent degradation of ubiquitinated proteins. The regulatory (or ATPase) complex confers ATP dependency and substrate specificity to the 26S complex. In case of HIV-1 infection, positive modulator of Tat-mediated transactivation.	Metabolic	Ubiquitin–Proteasome Pathway
P62195 View in UniProt	26S protease regulatory subunit 8 Gene Name: PSMC5 The 26S protease is involved in the ATP-dependent degradation of ubiquitinated proteins. The regulatory (or ATPase) complex confers ATP dependency and substrate specificity to the 26S complex.	Metabolic	Ubiquitin–Proteasome Pathway
Q9UNM6 View in UniProt	26S proteasome non-ATPase regulatory subunit 13 Gene Name: PSMD13 Acts as a regulatory subunit of the 26S proteasome which is involved in the ATP-dependent degradation of ubiquitinated proteins.	Metabolic	Ubiquitin–Proteasome Pathway
P55036 View in UniProt	26S proteasome non-ATPase regulatory subunit 4 Gene Name: PSMD4 Binds and presumably selects ubiquitin-conjugates for destruction. Displays selectivity for longer polyubiquitin chains. Modulates intestinal fluid secretion.	Metabolic	Ubiquitin–Proteasome Pathway
Q9H2F3 View in UniProt HMDBP04980 View in HMDB	3 beta-hydroxysteroid dehydrogenase type 7 Gene Name: HSD3B7 The 3-beta-HSD enzymatic system plays a crucial role in the biosynthesis of all classes of hormonal steroids. HSD VII is active against four 7-alpha-hydroxylated sterols. Does not metabolize several different C(19/21) steroids as substrates. Involved in bile acid synthesis.	Metabolic
P14060 View in UniProt HMDBP04403 View in HMDB	3 beta-hydroxysteroid dehydrogenase/Delta 5-->4-isomerase type 1 Gene Name: HSD3B1 3-beta-HSD is a bifunctional enzyme, that catalyzes the oxidative conversion of Delta(5)-ene-3-beta-hydroxy steroid, and the oxidative conversion of ketosteroids. The 3-beta-HSD enzymatic system plays a crucial role in the biosynthesis of all classes of hormonal steroids. Efficiently catalyzes the transformation of pregnenolone to progesterone, 17-alpha-hydroxypregnenolone to 17-alpha-hydroxyprogesterone, DHEA to 4-androstenedione, dihydrotestosterone to 5-alpha-androstane-3 beta,17 beta-diol, dehydroepiandrosterone to androstenedione and 5-alpha-androstan-3 beta,17 beta-diol to 5-alpha-dihydrotestosterone.	Metabolic	Progesterone Action Pathway 11-beta-Hydroxylase Deficiency (CYP11B1) 11-beta-Hydroxylase Deficiency (CYP11B1) 17-alpha-Hydroxylase Deficiency (CYP17) 17-beta Hydroxysteroid Dehydrogenase III Deficiency 17-beta Hydroxysteroid Dehydrogenase III Deficiency 21-Hydroxylase Deficiency (CYP21) 3-beta-Hydroxysteroid Dehydrogenase Deficiency 3-beta-Hydroxysteroid Dehydrogenase Deficiency Adrenal Hyperplasia Type 3 or Congenital Adrenal Hyperplasia Due to 21-Hydroxylase Deficiency Adrenal Hyperplasia Type 3 or Congenital Adrenal Hyperplasia Due to 21-Hydroxylase Deficiency Adrenal Hyperplasia Type 5 or Congenital Adrenal Hyperplasia Due to 17 alpha-Hydroxylase Deficiency Adrenal Hyperplasia Type 5 or Congenital Adrenal Hyperplasia Due to 17 alpha-Hydroxylase Deficiency Aldosterone from Steroidogenesis Androgen and Estrogen Metabolism Apparent Mineralocorticoid Excess Syndrome Aromatase Deficiency Aromatase Deficiency Congenital Lipoid Adrenal Hyperplasia (CLAH) or Lipoid CAH Congenital Lipoid Adrenal Hyperplasia (CLAH) or Lipoid CAH Corticosterone Methyl Oxidase I Deficiency (CMO I) Corticosterone Methyl Oxidase I Deficiency (CMO I) Corticosterone Methyl Oxidase II Deficiency (CMO II) Corticosterone Methyl Oxidase II Deficiency (CMO II) Dienogest Action Pathway Drospirenone Action Pathway Dutasteride Action Pathway Etonogestrel Action Pathway Finasteride Action Pathway Levonorgestrel Action Pathway Megestrol acetate Action Pathway Norelgestromin Action Pathway Norethisterone Action Pathway Norgestrel Action Pathway Segesterone acetate Action Pathway Steroidogenesis ( show more show less )
P26439 View in UniProt HMDBP04404 View in HMDB	3 beta-hydroxysteroid dehydrogenase/Delta 5-->4-isomerase type 2 Gene Name: HSD3B2 3-beta-HSD is a bifunctional enzyme, that catalyzes the oxidative conversion of Delta(5)-ene-3-beta-hydroxy steroid, and the oxidative conversion of ketosteroids. The 3-beta-HSD enzymatic system plays a crucial role in the biosynthesis of all classes of hormonal steroids.	Metabolic	11-beta-Hydroxylase Deficiency (CYP11B1) 11-beta-Hydroxylase Deficiency (CYP11B1) 17-alpha-Hydroxylase Deficiency (CYP17) 21-Hydroxylase Deficiency (CYP21) 3-beta-Hydroxysteroid Dehydrogenase Deficiency 3-beta-Hydroxysteroid Dehydrogenase Deficiency Adrenal Hyperplasia Type 3 or Congenital Adrenal Hyperplasia Due to 21-Hydroxylase Deficiency Adrenal Hyperplasia Type 3 or Congenital Adrenal Hyperplasia Due to 21-Hydroxylase Deficiency Adrenal Hyperplasia Type 5 or Congenital Adrenal Hyperplasia Due to 17 alpha-Hydroxylase Deficiency Adrenal Hyperplasia Type 5 or Congenital Adrenal Hyperplasia Due to 17 alpha-Hydroxylase Deficiency Apparent Mineralocorticoid Excess Syndrome Congenital Lipoid Adrenal Hyperplasia (CLAH) or Lipoid CAH Congenital Lipoid Adrenal Hyperplasia (CLAH) or Lipoid CAH Corticosterone Methyl Oxidase I Deficiency (CMO I) Corticosterone Methyl Oxidase I Deficiency (CMO I) Corticosterone Methyl Oxidase II Deficiency (CMO II) Corticosterone Methyl Oxidase II Deficiency (CMO II) Steroidogenesis ( show more show less )
O95861 View in UniProt HMDBP00342 View in HMDB	3'(2'),5'-bisphosphate nucleotidase 1 Gene Name: BPNT1 Converts adenosine 3'-phosphate 5'-phosphosulfate (PAPS) to adenosine 5'-phosphosulfate (APS) and 3'(2')-phosphoadenosine 5'- phosphate (PAP) to AMP. Has 1000-fold lower activity towards inositol 1,4-bisphosphate (Ins(1,4)P2) and inositol 1,3,4-trisphosphate (Ins(1,3,4)P3), but does not hydrolyze Ins(1)P, Ins(3,4)P2, Ins(1,3,4,5)P4 or InsP6.	Metabolic	Sulfate/Sulfite Metabolism Sulfite Oxidase Deficiency Sulfite Oxidase Deficiency
Q15125 View in UniProt HMDBP00949 View in HMDB	3-beta-hydroxysteroid-Delta(8),Delta(7)-isomerase Gene Name: EBP Catalyzes the conversion of Delta(8)-sterols to their corresponding Delta(7)-isomers.	Metabolic	Alendronate Action Pathway Bloch Pathway (Cholesterol Biosynthesis) Cerivastatin Action Pathway CHILD Syndrome CHILD Syndrome Cholesteryl Ester Storage Disease Chondrodysplasia Punctata II, X-Linked Dominant (CDPX2) Chondrodysplasia Punctata II, X-Linked Dominant (CDPX2) Desmosterolosis Desmosterolosis Fluvastatin Action Pathway Hyper-IgD Syndrome Hyper-IgD Syndrome Hypercholesterolemia Hypercholesterolemia Ibandronate Action Pathway Kandutsch-Russell Pathway (Cholesterol Biosynthesis) Lovastatin Action Pathway Lysosomal Acid Lipase Deficiency (Wolman Disease) Lysosomal Acid Lipase Deficiency (Wolman Disease) Mevalonic Aciduria Mevalonic Aciduria Pamidronate Action Pathway Pravastatin Action Pathway Risedronate Action Pathway Rosuvastatin Action Pathway Simvastatin Action Pathway Smith-Lemli-Opitz Syndrome (SLOS) Smith-Lemli-Opitz Syndrome (SLOS) Steroid Biosynthesis Wolman Disease Zoledronate Action Pathway ( show more show less )
P04035 View in UniProt HMDBP00910 View in HMDB	3-Hydroxy-3-methylglutaryl-coenzyme A reductase Gene Name: HMGCR Transmembrane glycoprotein that is the rate-limiting enzyme in cholesterol biosynthesis as well as in the biosynthesis of nonsterol isoprenoids that are essential for normal cell function including ubiquinone and geranylgeranyl proteins.	Metabolic	Alendronate Action Pathway Atorvastatin Action Pathway Cerivastatin Action Pathway CHILD Syndrome CHILD Syndrome Cholesteryl Ester Storage Disease Chondrodysplasia Punctata II, X-Linked Dominant (CDPX2) Chondrodysplasia Punctata II, X-Linked Dominant (CDPX2) Desmosterolosis Desmosterolosis Fluvastatin Action Pathway Hyper-IgD Syndrome Hyper-IgD Syndrome Hypercholesterolemia Hypercholesterolemia Ibandronate Action Pathway Lovastatin Action Pathway Lysosomal Acid Lipase Deficiency (Wolman Disease) Lysosomal Acid Lipase Deficiency (Wolman Disease) Mevalonate Pathway Mevalonic Aciduria Mevalonic Aciduria Pamidronate Action Pathway Pravastatin Action Pathway Risedronate Action Pathway Rosuvastatin Action Pathway Simvastatin Action Pathway Smith-Lemli-Opitz Syndrome (SLOS) Smith-Lemli-Opitz Syndrome (SLOS) Steroid Biosynthesis Wolman Disease Zoledronate Action Pathway ( show more show less )
Q99714 View in UniProt HMDBP00379 View in HMDB	3-hydroxyacyl-CoA dehydrogenase type-2 Gene Name: HSD17B10 Functions in mitochondrial tRNA maturation. Part of mitochondrial ribonuclease P, an enzyme composed of MRPP1/TRMT10C, MRPP2/HSD17B10 and MRPP3/KIAA0391, which cleaves tRNA molecules in their 5'-ends. By interacting with intracellular amyloid-beta, it may contribute to the neuronal dysfunction associated with Alzheimer disease (AD).	Metabolic	2-Methyl-3-hydroxybutyryl-CoA Dehydrogenase Deficiency 2-Methyl-3-hydroxybutyryl-CoA Dehydrogenase Deficiency 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency 3-Hydroxyisobutyric Acid Dehydrogenase Deficiency 3-Hydroxyisobutyric Acid Dehydrogenase Deficiency 3-Hydroxyisobutyric Aciduria 3-Hydroxyisobutyric Aciduria 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I 3-Methylglutaconic Aciduria Type I 3-Methylglutaconic Aciduria Type I 3-Methylglutaconic Aciduria Type III 3-Methylglutaconic Aciduria Type III 3-Methylglutaconic Aciduria Type IV 3-Methylglutaconic Aciduria Type IV beta-Ketothiolase Deficiency beta-Ketothiolase Deficiency Fatty Acid Elongation in Mitochondria Isobutyryl-CoA Dehydrogenase Deficiency Isobutyryl-CoA Dehydrogenase Deficiency Isovaleric Acidemia Isovaleric Acidemia Isovaleric Aciduria Isovaleric Aciduria Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase Deficiency (Fatty Acid Elongation in Mitochondria) Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase Deficiency (LCHAD) Maple Syrup Urine Disease Maple Syrup Urine Disease Methylmalonate Semialdehyde Dehydrogenase Deficiency Methylmalonate Semialdehyde Dehydrogenase Deficiency Methylmalonic Aciduria Methylmalonic Aciduria Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids Propionic Acidemia Propionic Acidemia Short-Chain 3-Hydroxyacyl-CoA Dehydrogenase Deficiency (HADH) Short-Chain 3-Hydroxyacyl-CoA Dehydrogenase Deficiency (HADH) Valine, Leucine, and Isoleucine Degradation Valproic Acid Metabolism Pathway ( show more show less )
P46952 View in UniProt HMDBP01128 View in HMDB	3-hydroxyanthranilate 3,4-dioxygenase Gene Name: HAAO Catalyzes the oxidative ring opening of 3-hydroxyanthranilate to 2-amino-3-carboxymuconate semialdehyde, which spontaneously cyclizes to quinolinate.	Metabolic	Alkaptonuria Disulfiram Action Pathway Dopamine beta-Hydroxylase Deficiency Dopamine beta-Hydroxylase Deficiency Hawkinsinuria Hawkinsinuria Metabolism and Physiological Effects of Quinolinic Acid Monoamine Oxidase-A Deficiency (MAO-A) Monoamine Oxidase-A Deficiency (MAO-A) Tryptophan Metabolism Tyrosine Metabolism Tyrosinemia Type I Tyrosinemia Type I Tyrosinemia, Transient, of the Newborn Tyrosinemia, Transient, of the Newborn ( show more show less )
P31937 View in UniProt HMDBP00395 View in HMDB	3-hydroxyisobutyrate dehydrogenase, mitochondrial Gene Name: HIBADH	Metabolic	2-Methyl-3-hydroxybutyryl-CoA Dehydrogenase Deficiency 2-Methyl-3-hydroxybutyryl-CoA Dehydrogenase Deficiency 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency 3-Hydroxyisobutyric Acid Dehydrogenase Deficiency 3-Hydroxyisobutyric Acid Dehydrogenase Deficiency 3-Hydroxyisobutyric Aciduria 3-Hydroxyisobutyric Aciduria 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I 3-Methylglutaconic Aciduria Type I 3-Methylglutaconic Aciduria Type I 3-Methylglutaconic Aciduria Type III 3-Methylglutaconic Aciduria Type III 3-Methylglutaconic Aciduria Type IV 3-Methylglutaconic Aciduria Type IV beta-Ketothiolase Deficiency beta-Ketothiolase Deficiency Isobutyryl-CoA Dehydrogenase Deficiency Isobutyryl-CoA Dehydrogenase Deficiency Isovaleric Acidemia Isovaleric Acidemia Isovaleric Aciduria Isovaleric Aciduria Maple Syrup Urine Disease Maple Syrup Urine Disease Methylmalonate Semialdehyde Dehydrogenase Deficiency Methylmalonate Semialdehyde Dehydrogenase Deficiency Methylmalonic Aciduria Methylmalonic Aciduria Propionic Acidemia Propionic Acidemia Valine, Leucine, and Isoleucine Degradation ( show more show less )
Q6NVY1 View in UniProt HMDBP04709 View in HMDB	3-hydroxyisobutyryl-CoA hydrolase, mitochondrial Gene Name: HIBCH Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite. Has high activity toward isobutyryl-CoA. Could be an isobutyryl-CoA dehydrogenase that functions in valine catabolism. Also hydrolyzes 3-hydroxypropanoyl-CoA.	Metabolic	2-Methyl-3-hydroxybutyryl-CoA Dehydrogenase Deficiency 2-Methyl-3-hydroxybutyryl-CoA Dehydrogenase Deficiency 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency 3-Hydroxyisobutyric Acid Dehydrogenase Deficiency 3-Hydroxyisobutyric Acid Dehydrogenase Deficiency 3-Hydroxyisobutyric Aciduria 3-Hydroxyisobutyric Aciduria 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I 3-Methylglutaconic Aciduria Type I 3-Methylglutaconic Aciduria Type I 3-Methylglutaconic Aciduria Type III 3-Methylglutaconic Aciduria Type III 3-Methylglutaconic Aciduria Type IV 3-Methylglutaconic Aciduria Type IV beta-Ketothiolase Deficiency beta-Ketothiolase Deficiency Isobutyryl-CoA Dehydrogenase Deficiency Isobutyryl-CoA Dehydrogenase Deficiency Isovaleric Acidemia Isovaleric Acidemia Isovaleric Aciduria Isovaleric Aciduria Malonic Aciduria Malonic Aciduria Malonyl-CoA Decarboxylase Deficiency Malonyl-CoA Decarboxylase Deficiency Maple Syrup Urine Disease Maple Syrup Urine Disease Methylmalonate Semialdehyde Dehydrogenase Deficiency Methylmalonate Semialdehyde Dehydrogenase Deficiency Methylmalonic Aciduria Methylmalonic Aciduria Methylmalonic Aciduria Due to Cobalamin-Related Disorders Methylmalonic Aciduria Due to Cobalamin-Related Disorders Propanoate Metabolism Propionic Acidemia Propionic Acidemia Valine, Leucine, and Isoleucine Degradation ( show more show less )
P56937 View in UniProt HMDBP00848 View in HMDB	3-keto-steroid reductase Gene Name: HSD17B7 Responsible for the reduction of the keto group on the C-3 of sterols.	Metabolic	Alendronate Action Pathway Bloch Pathway (Cholesterol Biosynthesis) Cerivastatin Action Pathway CHILD Syndrome CHILD Syndrome Cholesteryl Ester Storage Disease Chondrodysplasia Punctata II, X-Linked Dominant (CDPX2) Chondrodysplasia Punctata II, X-Linked Dominant (CDPX2) Desmosterolosis Desmosterolosis Fluvastatin Action Pathway Hyper-IgD Syndrome Hyper-IgD Syndrome Hypercholesterolemia Hypercholesterolemia Ibandronate Action Pathway Kandutsch-Russell Pathway (Cholesterol Biosynthesis) Lovastatin Action Pathway Lysosomal Acid Lipase Deficiency (Wolman Disease) Lysosomal Acid Lipase Deficiency (Wolman Disease) Mevalonic Aciduria Mevalonic Aciduria Pamidronate Action Pathway Pravastatin Action Pathway Risedronate Action Pathway Rosuvastatin Action Pathway Simvastatin Action Pathway Smith-Lemli-Opitz Syndrome (SLOS) Smith-Lemli-Opitz Syndrome (SLOS) Steroid Biosynthesis Wolman Disease Zoledronate Action Pathway ( show more show less )
P42765 View in UniProt HMDBP00031 View in HMDB	3-ketoacyl-CoA thiolase, mitochondrial Gene Name: ACAA2 Abolishes BNIP3-mediated apoptosis and mitochondrial damage.	Metabolic	2-Methyl-3-hydroxybutyryl-CoA Dehydrogenase Deficiency 2-Methyl-3-hydroxybutyryl-CoA Dehydrogenase Deficiency 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency 3-Hydroxyisobutyric Acid Dehydrogenase Deficiency 3-Hydroxyisobutyric Acid Dehydrogenase Deficiency 3-Hydroxyisobutyric Aciduria 3-Hydroxyisobutyric Aciduria 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I 3-Methylglutaconic Aciduria Type I 3-Methylglutaconic Aciduria Type I 3-Methylglutaconic Aciduria Type III 3-Methylglutaconic Aciduria Type III 3-Methylglutaconic Aciduria Type IV 3-Methylglutaconic Aciduria Type IV beta-Ketothiolase Deficiency beta-Ketothiolase Deficiency Carnitine Palmitoyl Transferase Deficiency I Carnitine Palmitoyl Transferase Deficiency I Carnitine Palmitoyl Transferase Deficiency II Carnitine Palmitoyl Transferase Deficiency II Ethylmalonic Encephalopathy Ethylmalonic Encephalopathy Fatty Acid Elongation in Mitochondria Fatty Acid Metabolism Glutaric Aciduria Type I Glutaric Aciduria Type I (Fatty Acid Metabolism) Isobutyryl-CoA Dehydrogenase Deficiency Isobutyryl-CoA Dehydrogenase Deficiency Isovaleric Acidemia Isovaleric Acidemia Isovaleric Aciduria Isovaleric Aciduria Long Chain Acyl-CoA Dehydrogenase Deficiency (LCAD) Long Chain Acyl-CoA Dehydrogenase Deficiency (LCAD) (Fatty Acid Metabolism) Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase Deficiency (Fatty Acid Elongation in Mitochondria) Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase Deficiency (LCHAD) Maple Syrup Urine Disease Maple Syrup Urine Disease Medium Chain Acyl-CoA Dehydrogenase Deficiency (MCAD) Medium Chain Acyl-CoA Dehydrogenase Deficiency (MCAD) Methylmalonate Semialdehyde Dehydrogenase Deficiency Methylmalonate Semialdehyde Dehydrogenase Deficiency Methylmalonic Aciduria Methylmalonic Aciduria Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids Propionic Acidemia Propionic Acidemia Short-Chain 3-Hydroxyacyl-CoA Dehydrogenase Deficiency (HADH) Short-Chain 3-Hydroxyacyl-CoA Dehydrogenase Deficiency (HADH) Short-Chain Acyl-CoA Dehydrogenase Deficiency (SCAD Deficiency) Short-Chain Acyl-CoA Dehydrogenase Deficiency (SCAD Deficiency) Trifunctional Protein Deficiency Trifunctional Protein Deficiency Valine, Leucine, and Isoleucine Degradation Very-Long-Chain Acyl-CoA Dehydrogenase Deficiency (VLCAD) Very-Long-Chain Acyl-CoA Dehydrogenase Deficiency (VLCAD) ( show more show less )

Showing 21 - 40 of 1576 proteins

Browsing Proteins

Protein ID

Protein Description

Pathway Class

Pathways

P62333

26S protease regulatory subunit 10B

P62191

26S protease regulatory subunit 4

P17980

26S protease regulatory subunit 6A

P43686

26S protease regulatory subunit 6B

P35998

26S protease regulatory subunit 7

P62195

26S protease regulatory subunit 8

Q9UNM6

26S proteasome non-ATPase regulatory subunit 13

P55036

26S proteasome non-ATPase regulatory subunit 4

Q9H2F3

HMDBP04980

3 beta-hydroxysteroid dehydrogenase type 7

P14060

HMDBP04403

3 beta-hydroxysteroid dehydrogenase/Delta 5-->4-isomerase type 1

P26439

HMDBP04404

3 beta-hydroxysteroid dehydrogenase/Delta 5-->4-isomerase type 2

O95861

HMDBP00342

3'(2'),5'-bisphosphate nucleotidase 1

Q15125

HMDBP00949

3-beta-hydroxysteroid-Delta(8),Delta(7)-isomerase

P04035

HMDBP00910

3-Hydroxy-3-methylglutaryl-coenzyme A reductase

Q99714

HMDBP00379

3-hydroxyacyl-CoA dehydrogenase type-2

P46952

HMDBP01128

3-hydroxyanthranilate 3,4-dioxygenase

P31937

HMDBP00395

3-hydroxyisobutyrate dehydrogenase, mitochondrial

Q6NVY1

HMDBP04709

3-hydroxyisobutyryl-CoA hydrolase, mitochondrial

P56937

HMDBP00848

3-keto-steroid reductase

P42765

HMDBP00031

3-ketoacyl-CoA thiolase, mitochondrial