SMP0000526
SMPDB
6022
PubChem-compound
O95470
UniProt
C00319
KEGG Compound
937
ChemSpider
C00550
KEGG Compound
4696849
ChemSpider
DEHYDROSPHINGANINE
BioCyc
Arylsulfatase A
P15289
UniProt
CerP(d18:1/18:0)
SPHINGO-MYELIN
BioCyc
HMDB0006752
HMDB
CHEBI:17115
ChEBI
11958364
PubChem-compound
SM(d18:1/18:0)
Sphingosine 1-phosphate
388480
ChemSpider
ATP
BioCyc
1.0
1.0
1.0
14808-79-8
CAS
Galabiosylceramide (d18:1/18:0)
ReactionCatalysis932
ACTIVATION
ReactionCatalysis930
ACTIVATION
BTO:0000759
BRENDA TISSUE ONTOLOGY
1.0
Adenosine diphosphate
959
ChemSpider
16755624
PubChem-compound
5742
ChemSpider
CHEBI:16474
ChEBI
2280-44-6
CAS
Phosphoadenosine phosphosulfate
P16278
UniProt
Alpha-galactosidase A
1.0
5736
ChemSpider
53477679
PubChem-compound
1.0
6031
PubChem-compound
1.0
133-89-1
CAS
PW000157
PathWhiz
559277
ChemSpider
1.0
C00346
KEGG Compound
C00588
KEGG Compound
P04062
UniProt
1.0
SubPathwayInteraction166
SubPathway166Reaction
SubPathwayReaction
ReactionCatalysis872
ACTIVATION
ReactionCatalysis873
ACTIVATION
C9H18O8
Galactosylglycerol
254.10017
24778664
PubChem-compound
HMDB0006790
HMDB
1.0
20057275
PubChem-compound
1.0
Cytosol
Phosphatidylcholine:ceramide cholinephosphotransferase 1
PHOSPHATIDYLCHOLINE
BioCyc
1071-23-4
CAS
Sphingosine-1-phosphate lyase 1
1.0
3.1.3.-
false
3.1.3.-
Adenosine diphosphate + Sphinganine 1-phosphate → Adenosine triphosphate + Sphinganine
LEFT_TO_RIGHT
1.0
3.1.3.4
false
3.1.3.4
Sphinganine 1-phosphate + Water → Phosphate + Sphinganine
LEFT_TO_RIGHT
ReactionCatalysis869
ACTIVATION
Uridine diphosphate glucose
ReactionCatalysis868
ACTIVATION
PALMITALDEHYDE
BioCyc
C00009
KEGG Compound
C00008
KEGG Compound
1.0
C00006
KEGG Compound
CHEBI:18009
ChEBI
C00001
KEGG Compound
C00005
KEGG Compound
CHEBI:18367
ChEBI
NADPH
1032
ChemSpider
CHEBI:16189
ChEBI
C00002
KEGG Compound
Lipid phosphate phosphohydrolase 1
1.1.1.102
false
1.1.1.102
NADPH + Sphinganine → 3-Dehydrosphinganine + NADP
LEFT_TO_RIGHT
2.3.1.50
false
2.3.1.50
L-Serine + Palmitoyl-CoA → 3-Dehydrosphinganine + Carbon dioxide
LEFT_TO_RIGHT
1.0
C19H39NO3
Dihydroceramide
329.293
388895
ChemSpider
Dihydroceramide
ReactionCatalysis890
ACTIVATION
1.0
Sphinganine 1-phosphate
Ectonucleotide pyrophosphatase/phosphodiesterase family member 7
C00011
KEGG Compound
CHEBI:16393
ChEBI
C00015
KEGG Compound
1.0
3.5.1.-
false
3.5.1.-
Dihydroceramide → Sphinganine
LEFT_TO_RIGHT
2.7.1.138
false
2.7.1.138
Adenosine triphosphate + Ceramide (d18:1/18:0) → Adenosine diphosphate + CerP(d18:1/18:0)
LEFT_TO_RIGHT
1.0
3.1.3.4
false
3.1.3.4
Phosphate + Sphingosine → Sphingosine 1-phosphate + Water
LEFT_TO_RIGHT
1.0
3.5.1.23
false
3.5.1.23
Ceramide (d18:1/18:0) + Water → Sphingosine
LEFT_TO_RIGHT
NAD(P)
BioCyc
2.7.1.91
false
2.7.1.91
Adenosine triphosphate + Sphingosine → Adenosine diphosphate + Sphingosine 1-phosphate
LEFT_TO_RIGHT
Sialidase-3
1.0
3.1.3.-
false
3.1.3.-
Adenosine diphosphate + Sphingosine 1-phosphate → Adenosine triphosphate + Sphingosine
LEFT_TO_RIGHT
4.1.2.27
false
4.1.2.27
Sphingosine 1-phosphate → O-Phosphoethanolamine + Palmitaldehyde
LEFT_TO_RIGHT
HMDB0010701
HMDB
ReactionCatalysis886
ACTIVATION
HMDB0010709
HMDB
C00029
KEGG Compound
59-23-4
CAS
C02686
KEGG Compound
56-65-5
CAS
5771775
PubChem-compound
Galabiosylceramide sulfate (d18:1/18:0)
CHEBI:73144
ChEBI
Reaction1186
false
Dihydroceramide ? Ceramide (d18:1/18:0)
Galactosylceramide (d18:1/18:0)
PHOSPHORYL-CHOLINE
BioCyc
Ceramide (d18:1/18:0)
482-67-7
CAS
Serine palmitoyltransferase 2
1.0
NADP
C12126
KEGG Compound
ReactionCatalysis874
ACTIVATION
Sphinganine
SMILES
CCCCCCCCCCCCCCCCCC(=O)N[C@@]([H])(COP(=O)(O)O)[C@]([H])(O)\C=C\CCCCCCCCCCCCC
C00154
KEGG Compound
SMILES
CCCCCCCCCCCCCCCC(=O)[C@@H](N)CO
1.0
Galactocerebrosidase
C01120
KEGG Compound
C00031
KEGG Compound
C00157
KEGG Compound
1.0
CHEBI:31488
ChEBI
HMDB0001348
HMDB
104404-17-3
CAS
1.0
Adenosine triphosphate
SMILES
CCCCCCCCCCCCC\C=C\[C@@H](O)[C@@H](N)CO
HMDB0004972
HMDB
1.0
Adenosine triphosphate
C48H91NO13
Lactosylceramide (d18:1/18:0)
889.64905
HMDB0001341
HMDB
HMDB0000252
HMDB
5283583
PubChem-compound
1.0
Galactosylceramide (d18:1/18:0)
Glucosylceramide (d18:1/18:0)
Water
Arylsulfatase A
Sialidase-3
SMILES
CCCCCCCCCCCCCCCCCC(=O)NC(CO[C@@H]1O[C@H](CO)[C@H](O)[C@H](O)[C@H]1O)C(O)\C=C/CCCCCCCCCCCCC
SMILES
NC1=NC=NC2=C1N=CN2[C@@H]1O[C@H](COP(O)(=O)OP(O)(O)=O)[C@@H](O)[C@H]1O
Galactosylceramide sulfotransferase
SMILES
CCCCCCCCCCCCCCCC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
SMILES
CCCCCCCCCCCCCCC[C@@H](O)[C@@H](N)CO
Sphinganine
Ceramide glucosyltransferase
HMDB0000269
HMDB
SMILES
CCCCCCCCCCCCC\C=C\[C@@H](O)[C@@H](N)COP(O)(O)=O
C9H14N2O12P2
Uridine 5'-diphosphate
404.0022
5283588
PubChem-compound
HMDB0000143
HMDB
1.0
1.0
C10H15N5O13P2S
Phosphoadenosine phosphosulfate
506.98624
Glucosylceramidase
CHEBI:28061
ChEBI
140102
ChemSpider
CHEBI:18132
ChEBI
SMILES
OS(O)(=O)=O
644260
PubChem-compound
SMILES
NCCOP(O)(O)=O
C00054
KEGG Compound
3-O-Sulfogalactosylceramide (d18:1/18:0)
C00053
KEGG Compound
16105-69-4
CAS
7732-18-5
CAS
Phosphorylcholine
CERAMIDE
BioCyc
C00059
KEGG Compound
19794-97-9
CAS
1.0
Sphinganine 1-phosphate
HMDB0000277
HMDB
Water
SMILES
CCCCCCCCCCCCCCCCCC(=O)N[C@@H](CO[C@@H]1O[C@H](CO)[C@@H](O)[C@H](O)[C@H]1O)[C@H](O)\C=C\CCCCCCCCCCCCC
Alpha-galactosidase A
SMILES
CCCCCCCCCCCCCCCCCC(=O)NC(CO[C@@H]1O[C@H](CO)[C@H](O[C@H]2O[C@H](CO)[C@H](O)[C@H](O)[C@H]2O)[C@H](O)[C@H]1O)C(O)\C=C/CCCCCCCCCCCCC
Beta-1,4-galactosyltransferase 6
HMDB0001480
HMDB
C10H16N5O13P3
Adenosine triphosphate
506.99576
Water
Palmitoyl-CoA
BiologicalState10
Homo sapiens, Liver
C00065
KEGG Compound
Sphingosine kinase 2
P54803
UniProt
Ceramide glucosyltransferase
1.0
10214
PubChem-compound
107-73-3
CAS
HMDB0001134
HMDB
SMILES
NC1=C2N=CN([C@@H]3O[C@H](COP(O)(O)=O)[C@@H](OP(O)(O)=O)[C@H]3O)C2=NC=N1
C00195
KEGG Compound
Sphingolipid delta(4)-desaturase/C4-hydroxylase DES2
Glucosylceramide (d18:1/18:0)
21436314
ChemSpider
HMDB0000286
HMDB
962
PubChem-compound
GLUCOSYL_CERAMIDE
BioCyc
1.0
1.0
3-ketodihydrosphingosine reductase
5800
ChemSpider
Sphingosine-1-phosphate lyase 1
58-98-0
CAS
CO2
Carbon dioxide
43.98983
C05401
KEGG Compound
SMILES
CCCCCCCCCCCCCCCCCC(=O)N[C@@]([H])(CO[C@@H]1O[C@H](CO)[C@H](O)C(OS(=O)(O)=O)C1O)[C@@](O)([H])\C=C\CCCCCCCCCCCCC
Sphinganine
C01290
KEGG Compound
ReactionCatalysis908
ACTIVATION
1.0
ReactionCatalysis909
ACTIVATION
Sphingosine 1-phosphate
ReactionCatalysis907
ACTIVATION
Galactosylceramide (d18:1/18:0)
ReactionCatalysis904
ACTIVATION
ReactionCatalysis905
ACTIVATION
C5H15NO4P
Phosphorylcholine
184.07387
ReactionCatalysis902
ACTIVATION
ReactionCatalysis903
ACTIVATION
Sphingosine
ReactionCatalysis900
ACTIVATION
ReactionCatalysis901
ACTIVATION
HMDB0002111
HMDB
HMDB0000295
HMDB
HMDB0001383
HMDB
5809
ChemSpider
SMILES
OC[C@H]1O[C@H](O)[C@H](O)[C@@H](O)[C@H]1O
1.0
14265-44-2
CAS
1.0
58-64-0
CAS
1.0
1.0
1.0
C41H78NO8P
PC(15:0/18:2(9Z,12Z))
743.5465
Q6UWV6
UniProt
CHEBI:4167
ChEBI
1.0
L-Serine
SubPathwayOutput
SMILES
CCCCCCCCCCCCCCC[C@@H](O)[C@@H](N)COP(O)(O)=O
HMDB0000061
HMDB
C3H7NO3
L-Serine
105.042595
244215-65-4
CAS
Serine palmitoyltransferase 1
HMDB0000187
HMDB
SMILES
CCCCCCCCCCCCCCCC=O
Galactocerebrosidase
984
PubChem-compound
Beta-1,4-galactosyltransferase 6
Galactosylglycerol
Lactosylceramide (d18:1/18:0)
N-Acetylneuraminyl-galactosylceramide (d18:1/18:0)
Q9UBX8
UniProt
SMILES
[H]C1(O)O[C@]([H])(CO)[C@@]([H])(O)[C@]([H])(O)[C@@]1([H])O
22833512
PubChem-compound
C01190
KEGG Compound
Lipid phosphate phosphohydrolase 1
H2O
Water
18.010565
990
ChemSpider
Q99999
UniProt
ReactionCatalysis926
ACTIVATION
ReactionCatalysis927
ACTIVATION
HMDB0007940
HMDB
ReactionCatalysis925
ACTIVATION
ReactionCatalysis922
ACTIVATION
Uridine 5'-diphosphate
ReactionCatalysis923
ACTIVATION
1.0
ReactionCatalysis920
ACTIVATION
SMILES
[H][C@@](COP([O-])(=O)OCC[N+](C)(C)C)(NC(=O)CCCCCCCCCCCCCCCCC)[C@H](O)\C=C\CCCCCCCCCCCCC
SMILES
OC[C@H]1O[C@H](OP(O)(=O)OP(O)(=O)OC[C@H]2O[C@H]([C@H](O)[C@@H]2O)N2C=CC(=O)NC2=O)[C@H](O)[C@@H](O)[C@@H]1O
Alkaline ceramidase 3
Galabiosylceramide (d18:1/18:0)
Q86VZ5
UniProt
Sphingolipid delta(4)-desaturase/C4-hydroxylase DES2
Ceramide kinase
5283560
PubChem-compound
Glucosylceramide (d18:1/18:0)
1.0
Q06136
UniProt
989
ChemSpider
1.0
Uridine 5'-diphosphate
1.0
5283565
PubChem-compound
ReactionCatalysis910
ACTIVATION
2.7.1.91
false
2.7.1.91
Adenosine triphosphate + Sphinganine → Adenosine diphosphate + Sphinganine 1-phosphate
LEFT_TO_RIGHT
1.0
17215925
ChemSpider
C2H8NO4P
O-Phosphoethanolamine
141.01909
PHOSPHORYL-ETHANOLAMINE
BioCyc
4446696
ChemSpider
Serine palmitoyltransferase 1
1014
PubChem-compound
1015
PubChem-compound
H2O4S
Sulfate
97.96738
C48H91NO13
Galabiosylceramide (d18:1/18:0)
889.64905
1.0
C42H81NO8
Glucosylceramide (d18:1/18:0)
727.5962
SMILES
O
656504
PubChem-compound
4.1.2.27
false
4.1.2.27
Sphinganine 1-phosphate → O-Phosphoethanolamine + Palmitaldehyde
LEFT_TO_RIGHT
Ceramide (d18:1/18:0)
Sphinganine 1-phosphate
HMDB0000538
HMDB
1.0
Serine palmitoyltransferase 2
629-80-1
CAS
Sphingosine-1-phosphate phosphatase 2
D-Glucose
1.0
Q9UQ49
UniProt
ADP
BioCyc
10260120
PubChem-compound
C10H15N5O10P2
Adenosine 3',5'-diphosphate
427.02942
PALMITYL-COA
BioCyc
4446678
ChemSpider
53-59-8
CAS
Lysosome
Beta-galactosidase
4446673
ChemSpider
Q16880
UniProt
Alkaline ceramidase 1
Q9NUN7
UniProt
Phosphatidylcholine:ceramide cholinephosphotransferase 1
GO:0005829
GENE ONTOLOGY
439853
PubChem-compound
CHEBI:84759
ChEBI
274
ChemSpider
C36H71NO3
Ceramide (d18:1/18:0)
565.5434
1.0
SMILES
[H][C@@](CO[C@@H]1O[C@H](CO)[C@@H](O[C@@H]2O[C@H](CO)[C@H](O)[C@H](O)[C@H]2O)[C@H](O)[C@H]1O)(NC(=O)CCCCCCCCCCCCCCCCC)[C@]([H])(O)\C=C\CCCCCCCCCCCCC
Q6QHC5
UniProt
5353955
PubChem-compound
Phosphate
PC(15:0/18:2(9Z,12Z))
H3O4P
Phosphate
97.9769
SER
BioCyc
Sphingosine
1.0
SMILES
O[C@H]1[C@@H](O)[C@@H](O[C@@H]1COP(O)(=O)OP(O)(O)=O)N1C=CC(=O)NC1=O
C21H30N7O17P3
NADPH
745.0911
3-5-ADP
BioCyc
C21H28N7O17P3
NADP
743.07544
1.0
CPD-649
BioCyc
CHEBI:37550
ChEBI
NADPH
BioCyc
1053-73-2
CAS
Ceramide (d18:1/18:0)
HMDB0012314
HMDB
CHEBI:15525
ChEBI
Sphinganine 1-phosphate
Alkaline ceramidase 1
Carbon dioxide
570889
ChemSpider
C15H24N2O17P2
Uridine diphosphate glucose
566.055
UDP-GLUCOSE
BioCyc
SMILES
CCCCCCCCCCCCCCCCCC(=O)N[C@@H](CO)[C@H](O)\C=C\CCCCCCCCCCCCC
SMILES
OP(O)(O)=O
1.0
HMDB0000217
HMDB
GO:0005886
GENE ONTOLOGY
124-38-9
CAS
GO:0005764
GENE ONTOLOGY
C6H12O6
D-Glucose
180.06339
C41H83N2O6P
SM(d18:1/18:0)
730.5989
Lactosylceramide (d18:1/18:0)
HMDB0011591
HMDB
1.0
Adenosine 3',5'-diphosphate
3-ketodihydrosphingosine reductase
Sphingosine kinase 2
HMDB0001429
HMDB
GLC
BioCyc
1.0
9799
ChemSpider
SPHINGOSINE
BioCyc
1763-10-6
CAS
Liver
Alkaline ceramidase 3
SMILES
NC(=O)C1=C[N+](=CC=C1)[C@@H]1O[C@H](COP([O-])(=O)OP(O)(=O)OC[C@H]2O[C@H]([C@H](OP(O)(O)=O)[C@@H]2O)N2C=NC3=C2N=CN=C3N)[C@@H](O)[C@H]1O
Adenosine triphosphate
HMDB0000221
HMDB
HMDB0000224
HMDB
SMILES
NC(=O)C1=CN(C=CC1)[C@@H]1O[C@H](COP(O)(=O)OP(O)(=O)OC[C@H]2O[C@H]([C@H](OP(O)(O)=O)[C@@H]2O)N2C=NC3=C2N=CN=C3N)[C@@H](O)[C@H]1O
159296
PubChem-compound
1.0
Glycine and Serine Metabolism
SubPathway
HMDB0001551
HMDB
53-57-6
CAS
1.0
Sphingosine kinase 2
SMILES
O=C=O
C18H37NO2
3-Dehydrosphinganine
299.28244
D-Galactose
C36H72NO6P
CerP(d18:1/18:0)
645.5097
5951
PubChem-compound
C06124
KEGG Compound
Ceramide kinase
HMDB0001565
HMDB
SMILES
C[N+](C)(C)CCOP(O)(O)=O
1117
PubChem-compound
Sulfate
CHEBI:84719
ChEBI
5957
PubChem-compound
HMDB0001448
HMDB
HMDB0004834
HMDB
HMDB0004950
HMDB
1.0
C18H37NO2
Sphingosine
299.28244
Q8TCT0
UniProt
CHEBI:15754
ChEBI
Galactosylceramide (d18:1/18:0)
Ectonucleotide pyrophosphatase/phosphodiesterase family member 7
C42H81NO8
Galactosylceramide (d18:1/18:0)
727.5962
C06125
KEGG Compound
CHEBI:72961
ChEBI
C06126
KEGG Compound
C37H66N7O17P3S
Palmitoyl-CoA
1005.34485
SMILES
N[C@@H](CO)C(O)=O
HMDB0000122
HMDB
Adenosine triphosphate
1.0
C10H15N5O10P2
Adenosine diphosphate
427.02942
SMILES
CCCCCCCCCCCCCCC(=O)OC[C@]([H])(COP([O-])(=O)OCC[N+](C)(C)C)OC(=O)CCCCCCC\C=C/C\C=C/CCCCC
HMDB0001338
HMDB
C18H38NO5P
Sphingosine 1-phosphate
379.24875
PW000502
PathWhiz
4510275
ChemSpider
C18H39NO2
Sphinganine
301.29807
CHEBI:17985
ChEBI
SMILES
[H][C@]1(O[C@@](C[C@H](O)[C@H]1NC(C)=O)(O[C@H]1[C@@H](O)[C@@H](CO)O[C@@H](OC[C@H](NC(=O)CCCCCCCCCCCCCCCCC)[C@H](O)\C=C\CCCCCCCCCCCCC)[C@@H]1O)C(O)=O)[C@H](O)[C@H](O)CO
CHEBI:17862
ChEBI
SMILES
CCCCCCCCCCCCCCCCCC(=O)NC(CO[C@@H]1O[C@H](CO)[C@H](O[C@H]2O[C@H](CO)[C@H](O)[C@H](OS(O)(=O)=O)[C@H]2O)[C@H](O)[C@H]1O)C(O)\C=C/CCCCCCCCCCCCC
C00836
KEGG Compound
10132611
ChemSpider
Beta-galactosidase
Endoplasmic Reticulum
Endoplasmic Reticulum Membrane
1085
ChemSpider
CPD-8587
BioCyc
2-hydroxyacylsphingosine 1-beta-galactosyltransferase
SMILES
CCCCCCCCCCCCCCC[C@@H](O)[C@H](CO)NC=O
CHEBI:16893
ChEBI
Adenosine diphosphate
UDP
BioCyc
CHEBI:17980
ChEBI
764-22-7
CAS
91486
PubChem-compound
1.0
SMP0000004
SMPDB
O15270
UniProt
CHEBI:17636
ChEBI
82609
ChemSpider
5675
ChemSpider
Adenosine diphosphate
Golgi Apparatus
ReactionCatalysis898
ACTIVATION
123-78-4
CAS
GO:0005794
GENE ONTOLOGY
ReactionCatalysis899
ACTIVATION
ReactionCatalysis897
ACTIVATION
CHEBI:17600
ChEBI
NH42SO4
BioCyc
14902
ChemSpider
CHEBI:15422
ChEBI
GALACTOSE
BioCyc
5589
ChemSpider
Serine palmitoyltransferase 1
Homo sapiens
1.0
1.0
1.0
C6H12O6
D-Galactose
180.06339
O15269
UniProt
C42H81NO11S
3-O-Sulfogalactosylceramide (d18:1/18:0)
807.55304
3-O-Sulfogalactosylceramide (d18:1/18:0)
GALACTOSYLCERAMIDE-SULFATE
BioCyc
GO:0005789
GENE ONTOLOGY
Q8IWX5
UniProt
GO:0005783
GENE ONTOLOGY
O-Phosphoethanolamine
Water
Q9NRA0
UniProt
85187-10-6
CAS
4446701
ChemSpider
CHEBI:16526
ChEBI
C00984
KEGG Compound
CHEBI:16761
ChEBI
1.0
16744851
ChemSpider
C18H40NO5P
Sphinganine 1-phosphate
381.2644
C16H32O
Palmitaldehyde
240.24532
9606
TAXONOMY
Palmitaldehyde
8435601
ChemSpider
C02934
KEGG Compound
C00517
KEGG Compound
24765745
ChemSpider
3.2.1.23
false
3.2.1.23
Lactosylceramide (d18:1/18:0) → Glucosylceramide (d18:1/18:0)
LEFT_TO_RIGHT
2.8.2.11
false
2.8.2.11
Galabiosylceramide (d18:1/18:0) + Phosphoadenosine phosphosulfate → Adenosine 3',5'-diphosphate + Galabiosylceramide sulfate (d18:1/18:0)
LEFT_TO_RIGHT
SMILES
NC1=NC=NC2=C1N=CN2[C@@H]1O[C@H](COP(O)(=O)OS(O)(=O)=O)[C@@H](OP(O)(O)=O)[C@H]1O
26993-30-6
CAS
PAPS
BioCyc
1.0
Sphingosine-1-phosphate phosphatase 2
1.0
439357
PubChem-compound
2.4.1.80
false
2.4.1.80
Ceramide (d18:1/18:0) + Uridine diphosphate glucose → Glucosylceramide (d18:1/18:0) + Uridine 5'-diphosphate
LEFT_TO_RIGHT
3.2.1.45
false
3.2.1.45
Glucosylceramide (d18:1/18:0) + Water → Ceramide (d18:1/18:0) + D-Glucose
LEFT_TO_RIGHT
L-Serine
1.0
Cell Membrane
CHEBI:15377
ChEBI
Glucosylceramidase
2-hydroxyacylsphingosine 1-beta-galactosyltransferase
Sphingosine-1-phosphate phosphatase 2
3-Dehydrosphinganine
56-45-1
CAS
SMILES
NC1=NC=NC2=C1N=CN2[C@@H]1O[C@H](COP(O)(=O)OP(O)(=O)OP(O)(O)=O)[C@@H](O)[C@H]1O
5886
PubChem-compound
CerP(d18:1/18:0)
CHEBI:17553
ChEBI
280
PubChem-compound
Glucosylceramide (d18:1/18:0)
Krabbe Disease
3.2.1.46
false
3.2.1.46
Galactosylceramide (d18:1/18:0) → Ceramide (d18:1/18:0)
LEFT_TO_RIGHT
3.1.4.12
false
3.1.4.12
SM(d18:1/18:0) + Water → Ceramide (d18:1/18:0) + Phosphorylcholine
LEFT_TO_RIGHT
2.4.1.45
false
2.4.1.45
Ceramide (d18:1/18:0) → Galactosylceramide (d18:1/18:0)
LEFT_TO_RIGHT
C53H98N2O16
N-Acetylneuraminyl-galactosylceramide (d18:1/18:0)
1018.69165
2.7.8.27
false
2.7.8.27
Ceramide (d18:1/18:0) + PC(15:0/18:2(9Z,12Z)) → Galactosylglycerol + SM(d18:1/18:0)
LEFT_TO_RIGHT
Ceramide (d18:1/18:0)
C48H91NO16S
Galabiosylceramide sulfate (d18:1/18:0)
969.60583
3.1.3.4
false
3.1.3.4
CerP(d18:1/18:0) + Water → Ceramide (d18:1/18:0) + Phosphate
LEFT_TO_RIGHT
1.0
3.1.3.-
false
3.1.3.-
Ceramide (d18:1/18:0) → CerP(d18:1/18:0)
LEFT_TO_RIGHT
Galactosylceramide sulfotransferase
24766615
ChemSpider
5793
PubChem-compound
SMILES
OCC(O)CO[C@@H]1O[C@H](CO)[C@H](O)[C@H](O)[C@H]1O
53480653
PubChem-compound
Uridine diphosphate glucose
O14494
UniProt
Q8TDN7
UniProt
1.0
15667
PubChem-compound
1.0
1061
PubChem-compound
CHEBI:16566
ChEBI
CHEBI:17659
ChEBI
1.0
1.0
HMDB0001967
HMDB
P06280
UniProt
ReactionCatalysis170269
ACTIVATION
1.0
Reaction1221
false
Lactosylceramide (d18:1/18:0) + Uridine 5'-diphosphate ← Glucosylceramide (d18:1/18:0) + Uridine diphosphate glucose
RIGHT_TO_LEFT
Adenosine diphosphate
Dihydroceramide
85305-87-9
CAS
Q16739
UniProt
3.2.1.18
false
3.2.1.18
Galactosylceramide (d18:1/18:0) → N-Acetylneuraminyl-galactosylceramide (d18:1/18:0)
LEFT_TO_RIGHT
3.2.1.22
false
3.2.1.22
D-Galactose + Galactosylceramide (d18:1/18:0) ← Galabiosylceramide (d18:1/18:0)
RIGHT_TO_LEFT
77538-38-6
CAS
2.8.2.11
false
2.8.2.11
Galactosylceramide (d18:1/18:0) + Phosphoadenosine phosphosulfate → 3-O-Sulfogalactosylceramide (d18:1/18:0) + Adenosine 3',5'-diphosphate
LEFT_TO_RIGHT
3.1.6.8
false
3.1.6.8
3-O-Sulfogalactosylceramide (d18:1/18:0) + Water → Galactosylceramide (d18:1/18:0) + Sulfate
LEFT_TO_RIGHT