C23H38N7O17P3S
Acetyl-CoA
809.1258
17220838
ChemSpider
C00318
KEGG Compound
937
ChemSpider
388353
ChemSpider
(2E)-Decenoyl-CoA
439153
PubChem-compound
L-Carnitine
1.0
Trifunctional enzyme subunit alpha, mitochondrial
Enoyl-CoA hydratase, mitochondrial
1.0
Trifunctional enzyme subunit beta, mitochondrial
C33H58N7O17P3S
Lauroyl-CoA
949.2823
CHEBI:16027
ChEBI
38795-33-4
CAS
Hexanoyl-CoA
HMDB0001070
HMDB
ATP
BioCyc
1.0
Reduced electron-transfer flavoprotein
HMDB0006404
HMDB
P45954
UniProt
559142
ChemSpider
1.0
HMDB0006402
HMDB
1.0
Tetradecanoyl-CoA
PW000048
PathWhiz
5742
ChemSpider
CPD-196
BioCyc
C02990
KEGG Compound
C00332
KEGG Compound
11966197
PubChem-compound
Trifunctional enzyme, mitochondrial
440045
PubChem-compound
1.0
SMP0000540
SMPDB
HMDB0001088
HMDB
5858
ChemSpider
2364-67-2
CAS
Carbon dioxide
7-METHYL-3-OXOOCTANOYL-COA
BioCyc
4.0
Reduced electron-transfer flavoprotein
1010
ChemSpider
Enoyl-CoA hydratase, mitochondrial
SMILES
CC(C)(COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N)[C@@H](O)C(=O)NCCC(=O)NCCS
PPI
BioCyc
(2E)-Octenoyl-CoA
Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial
C27H46N7O17P3S
Hexanoyl-CoA
865.18835
P16219
UniProt
CHEBI:5086
ChEBI
Medium-chain specific acyl-CoA dehydrogenase, mitochondrial
LAUROYLCOA-CPD
BioCyc
Short-chain specific acyl-CoA dehydrogenase, mitochondrial
Lauroyl-CoA
Long-chain-fatty-acid--CoA ligase 1
53477508
PubChem-compound
C00249
KEGG Compound
3-ketoacyl-CoA thiolase, mitochondrial
C00001
KEGG Compound
1.0
SubPathwayInteraction80
SubPathway80Reaction
SubPathwayReaction
CHEBI:18361
ChEBI
NADH
C00004
KEGG Compound
C00003
KEGG Compound
C00002
KEGG Compound
Acetyl-CoA acetyltransferase, mitochondrial
103192-48-9
CAS
L-Palmitoylcarnitine
P42765
UniProt
Coenzyme A
Mitochondrial Inner Membrane
SubPathwayInteraction79
SubPathwayReaction
SubPathway79Reaction
L-Carnitine
CHEBI:28276
ChEBI
3130-72-1
CAS
389502
ChemSpider
389501
ChemSpider
C29H50N7O17P3S
Octanoyl-CoA
893.21967
389500
ChemSpider
SMILES
C[C@H](O)CC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
C21H27N7O14P2
NAD
663.10913
389506
ChemSpider
1.0
389504
ChemSpider
C00011
KEGG Compound
C00010
KEGG Compound
HMDB0000902
HMDB
11966160
PubChem-compound
C00136
KEGG Compound
C00013
KEGG Compound
CHEBI:10723
ChEBI
389508
ChemSpider
CHEBI:28264
ChEBI
P28330
UniProt
H
Hydrogen Ion
1.007825
CARNITINE
BioCyc
C25H42N7O17P3S
Butyryl-CoA
837.15704
56-65-5
CAS
C00020
KEGG Compound
53-84-9
CAS
389510
ChemSpider
Carnitine O-palmitoyltransferase 1
1.0
C00024
KEGG Compound
3-Hydroxydecanoyl-CoA
1.3.8.7
false
1.3.8.7
Lauroyl-CoA + electron-transfer flavoprotein → (2E)-Tetradecenoyl-CoA + Reduced electron-transfer flavoprotein
LEFT_TO_RIGHT
1264-57-9
CAS
CHEBI:17490
ChEBI
CHEBI:28493
ChEBI
Adenosine monophosphate
4460-95-1
CAS
4.2.1.17
false
4.2.1.17
3-Hydroxydodecanoyl-CoA → (2E)-Tetradecenoyl-CoA + Water
LEFT_TO_RIGHT
72059-49-5
CAS
L-Palmitoylcarnitine
3-oxohexadecanoyl-CoA
C00154
KEGG Compound
C37H66N7O18P3S
3-Hydroxyhexadecanoyl-CoA
1021.3398
C35H62N7O18P3S
3-Hydroxytetradecanoyl-CoA
993.3085
Carnitine O-palmitoyltransferase 1, liver isoform
C35H60N7O18P3S
3-oxotetradecanoyl-CoA
991.29285
4.0
Carnitine O-palmitoyltransferase 2, mitochondrial
Long-chain-fatty-acid--CoA ligase 1
SMILES
NC(=O)C1=CN(C=CC1)[C@@H]1O[C@H](CO[P@](O)(=O)O[P@](O)(=O)OC[C@H]2O[C@H]([C@H](O)[C@@H]2O)N2C=NC3=C(N)N=CN=C23)[C@@H](O)[C@H]1O
AMP
BioCyc
2871-66-1
CAS
SMILES
CC(=O)CC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
35106-50-4
CAS
Palmitic acid
HMDB0000250
HMDB
SMILES
OP(O)(=O)OP(O)(O)=O
16061159
PubChem-compound
1.0
CPD-12174
BioCyc
SMILES
CCCCCCCC(=O)CC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
SMILES
[H][C@](O)(CCCCC)CC(=O)SCCNC(=O)CCNC(=O)[C@]([H])(O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H](C(O)[C@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
SMILES
CCCCCC(=O)CC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
SMILES
CC(C)(COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N)C(O)C(=O)NCCC(=O)NCCSC(=O)CCCC(O)=O
SMILES
CCCCCCCCCCCCCCCC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
C02593
KEGG Compound
SMILES
CCC[C@H](O)CC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
C03561
KEGG Compound
C37H64N7O18P3S
3-oxohexadecanoyl-CoA
1019.32416
SMILES
CCCCCCCCC[C@H](O)CC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
SMILES
CCCCCCCCCC(=O)CC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
1.0
3-hydroxyoctanoyl-CoA
C31H54N7O17P3S
Decanoyl-CoA
921.251
SMILES
CCCCCCC[C@H](O)CC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
1.0
7732-18-5
CAS
54684-64-9
CAS
3-OXOPALMITOYL-COA
BioCyc
61-19-8
CAS
HMDB0001487
HMDB
2140-48-9
CAS
SMILES
NC1=C2N=CN([C@@H]3O[C@H](COP(O)(O)=O)[C@@H](O)[C@H]3O)C2=NC=N1
1.0
1.0
Acetoacetyl-CoA
1.0
57-10-3
CAS
3-oxooctanoyl-CoA
Q92947
UniProt
2.0
HMDB0001484
HMDB
C10H16N5O13P3
Adenosine triphosphate
506.99576
165436
PubChem-compound
NAD
SMILES
C[N+](C)(C)C[C@H](O)CC([O-])=O
HMDB0000045
HMDB
1.0
Adenosine triphosphate
962
PubChem-compound
GLUTARYL-COA
BioCyc
Long-chain specific acyl-CoA dehydrogenase, mitochondrial
(2E)-Hexenoyl-CoA
CO2
Carbon dioxide
43.98983
C00080
KEGG Compound
P50416
UniProt
Water
Long-chain specific acyl-CoA dehydrogenase, mitochondrial
Enoyl-CoA hydratase, mitochondrial
1.0
HMDB0002111
HMDB
4.0
6245-70-1
CAS
6.0
1.0
1.0
1.0
Medium-chain specific acyl-CoA dehydrogenase, mitochondrial
1.0
1.0
1.0
6.0
960
ChemSpider
HMDB0002009
HMDB
1.0
HMDB0003571
HMDB
HMDB0000062
HMDB
1.0
1.0
1264-52-4
CAS
985
PubChem-compound
644102
PubChem-compound
444493
PubChem-compound
6083
PubChem-compound
Glutaryl-CoA dehydrogenase, mitochondrial
3-oxododecanoyl-CoA
SMILES
CCCC(=O)CC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
SMILES
CCC\C=C\C(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
SMILES
CCCCCCCCCCCCC\C=C\C(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
ACETYL-COA
BioCyc
SMILES
CCCCCCCCCCC\C=C\C(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
H2O
Water
18.010565
SMILES
CCCCCCC\C=C\C(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
4.0
Carnitine O-palmitoyltransferase 2, mitochondrial
SMILES
CCCCC\C=C\C(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
P55084
UniProt
NADH
BioCyc
HMDB0001166
HMDB
NAD
BioCyc
Acetyl-CoA acetyltransferase, mitochondrial
HMDB0059597
HMDB
Acetyl-CoA
11953816
PubChem-compound
SMILES
CCCCCCCCCCCCCC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
ReactionCatalysis279
ACTIVATION
Reaction759
false
3-Hydroxydodecanoyl-CoA + NAD ↔ 3-oxododecanoyl-CoA + Hydrogen Ion + NADH
REVERSIBLE
ReactionCatalysis276
ACTIVATION
2.3.1.16
false
2.3.1.16
Acetyl-CoA + Decanoyl-CoA → 3-oxododecanoyl-CoA + Coenzyme A
LEFT_TO_RIGHT
ReactionCatalysis275
ACTIVATION
65113
PubChem-compound
3-Hydroxytetradecanoyl-CoA
Reaction755
false
3-Hydroxydecanoyl-CoA + NAD ↔ 3-oxodecanoyl-CoA + Hydrogen Ion + NADH
REVERSIBLE
ReactionCatalysis272
ACTIVATION
C23H45NO4
L-Palmitoylcarnitine
399.33487
78303-19-2
CAS
4.2.1.17
false
4.2.1.17
3-Hydroxydecanoyl-CoA ↔ (2E)-Decenoyl-CoA + Water
REVERSIBLE
ReactionCatalysis273
ACTIVATION
ReactionCatalysis270
ACTIVATION
1.0
P49748
UniProt
3-oxotetradecanoyl-CoA
Coenzyme A
10140190
ChemSpider
SMILES
O
Palmitoyl-CoA
2.3.1.16
false
2.3.1.16
Acetyl-CoA + Octanoyl-CoA ↔ 3-oxodecanoyl-CoA + Coenzyme A
REVERSIBLE
371
ChemSpider
Reaction751
false
3-hydroxyoctanoyl-CoA + NAD ↔ 3-oxooctanoyl-CoA + Hydrogen Ion + NADH
REVERSIBLE
4.2.1.17
false
4.2.1.17
3-hydroxyoctanoyl-CoA ↔ (2E)-Octenoyl-CoA + Water
REVERSIBLE
Glycerolipid Metabolism
SubPathway
C10H14N5O7P
Adenosine monophosphate
347.06308
CPD-419
BioCyc
2.3.1.16
false
2.3.1.16
Acetyl-CoA + Hexanoyl-CoA ↔ 3-oxooctanoyl-CoA + Coenzyme A
REVERSIBLE
P40939
UniProt
ReactionCatalysis267
ACTIVATION
ReactionCatalysis268
ACTIVATION
ReactionCatalysis265
ACTIVATION
4.2.1.17
false
4.2.1.17
3-Hydroxyhexadecanoyl-CoA ↔ (2E)-Hexadecenoyl-CoA + Water
REVERSIBLE
ReactionCatalysis263
ACTIVATION
2.3.1.16
false
2.3.1.16
Acetyl-CoA + Tetradecanoyl-CoA ↔ 3-oxohexadecanoyl-CoA + Coenzyme A
REVERSIBLE
Reaction767
false
3-Hydroxyhexadecanoyl-CoA + NAD ↔ 3-oxohexadecanoyl-CoA + Hydrogen Ion + NADH
REVERSIBLE
ReactionCatalysis262
ACTIVATION
CHEBI:57371
ChEBI
HMDB0000538
HMDB
Carnitine O-palmitoyltransferase 1, liver isoform
ReactionCatalysis260
ACTIVATION
6816
PubChem-compound
HMDB0003934
HMDB
HMDB0002845
HMDB
HMDB0003935
HMDB
HMDB0003932
HMDB
5060-32-2
CAS
4.2.1.17
false
4.2.1.17
3-Hydroxytetradecanoyl-CoA ↔ (2E)-Tetradecenoyl-CoA + Water
REVERSIBLE
3-Hydroxyhexadecanoyl-CoA
CHEBI:15846
ChEBI
Very long-chain specific acyl-CoA dehydrogenase, mitochondrial
1.0
2.3.1.16
false
2.3.1.16
Acetyl-CoA + Lauroyl-CoA → 3-oxotetradecanoyl-CoA + Coenzyme A
LEFT_TO_RIGHT
C7H15NO3
L-Carnitine
161.1052
Reaction763
false
3-Hydroxytetradecanoyl-CoA + NAD ↔ 3-oxotetradecanoyl-CoA + Hydrogen Ion + NADH
REVERSIBLE
102680-35-3
CAS
1.0
PALMITYL-COA
BioCyc
ReactionCatalysis178
ACTIVATION
1.3.8.6
false
1.3.8.6
Glutaryl-CoA → Carbon dioxide + Crotonoyl-CoA
LEFT_TO_RIGHT
ReactionCatalysis176
ACTIVATION
ReactionCatalysis294
ACTIVATION
1.3.8.8
false
1.3.8.8
Octanoyl-CoA + electron-transfer flavoprotein → (2E)-Octenoyl-CoA + Reduced electron-transfer flavoprotein
LEFT_TO_RIGHT
440608
PubChem-compound
1.3.8.8
false
1.3.8.8
Hexanoyl-CoA + electron-transfer flavoprotein → (2E)-Hexenoyl-CoA + Reduced electron-transfer flavoprotein
LEFT_TO_RIGHT
1.0
SMILES
CCCCCCCCCCCC(=O)CC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
HMDB0003938
HMDB
440606
PubChem-compound
ReactionCatalysis293
ACTIVATION
SMILES
CCCCCCCCCCC[C@H](O)CC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
HMDB0003939
HMDB
ReactionCatalysis290
ACTIVATION
HMDB0003936
HMDB
440604
PubChem-compound
380
PubChem-compound
5280381
PubChem-compound
ReactionCatalysis291
ACTIVATION
SMILES
CCCCCCCCCCCCC[C@H](O)CC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
1038
PubChem-compound
440603
PubChem-compound
HMDB0003937
HMDB
440602
PubChem-compound
265
PubChem-compound
440601
PubChem-compound
440600
PubChem-compound
HMDB0003941
HMDB
HMDB0003942
HMDB
Fatty Acid Elongation in Mitochondria
SubPathway
HMDB0001521
HMDB
HMDB0003940
HMDB
HMDB0003945
HMDB
HMDB0003946
HMDB
HMDB0003943
HMDB
HMDB0003944
HMDB
C25H40N7O17P3S
Crotonoyl-CoA
835.1414
274
ChemSpider
Reaction776
false
Decanoyl-CoA + electron-transfer flavoprotein → (2E)-Decenoyl-CoA + Reduced electron-transfer flavoprotein
LEFT_TO_RIGHT
1.3.8.9
false
1.3.8.9
Palmitoyl-CoA + electron-transfer flavoprotein → (2E)-Hexadecenoyl-CoA + Reduced electron-transfer flavoprotein
LEFT_TO_RIGHT
1.3.8.8
false
1.3.8.8
Tetradecanoyl-CoA + electron-transfer flavoprotein → (2E)-Tetradecenoyl-CoA + Reduced electron-transfer flavoprotein
LEFT_TO_RIGHT
6.2.1.3
false
6.2.1.3
Adenosine triphosphate + Coenzyme A + Palmitic acid → Adenosine monophosphate + Palmitoyl-CoA + Pyrophosphate
LEFT_TO_RIGHT
Butyryl-CoA
2.3.1.21
false
2.3.1.21
L-Carnitine + Palmitoyl-CoA ↔ Coenzyme A + L-Palmitoylcarnitine
REVERSIBLE
CHEBI:16908
ChEBI
ReactionCatalysis289
ACTIVATION
K-HEXANOYL-COA
BioCyc
ReactionCatalysis288
ACTIVATION
ReactionCatalysis285
ACTIVATION
ReactionCatalysis283
ACTIVATION
ReactionCatalysis284
ACTIVATION
ReactionCatalysis281
ACTIVATION
HMDB0003949
HMDB
ReactionCatalysis280
ACTIVATION
HMDB0003948
HMDB
SMILES
CCCCCCCCCCCCCC(=O)CC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
1.0
SMILES
CCCCCCCCCC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
Coenzyme A
CHEBI:61526
ChEBI
C16H32O2
Palmitic acid
256.24023
260
ChemSpider
1.0
Reaction780
false
3-Hydroxybutyryl-CoA + NAD ↔ Acetoacetyl-CoA + Hydrogen Ion + NADH
REVERSIBLE
CHEBI:15521
ChEBI
CHEBI:15524
ChEBI
CHEBI:15525
ChEBI
541-15-1
CAS
C27H46N7O18P3S
3-Hydroxyhexanoyl-CoA
881.1833
C27H44N7O18P3S
3-oxohexanoyl-CoA
879.16766
C27H44N7O17P3S
(2E)-Hexenoyl-CoA
863.1727
C37H64N7O17P3S
(2E)-Hexadecenoyl-CoA
1003.3292
1.0
Palmitoyl-CoA
4444072
ChemSpider
58-68-4
CAS
C35H60N7O17P3S
(2E)-Tetradecenoyl-CoA
975.2979
HMDB0001423
HMDB
C31H52N7O17P3S
(2E)-Decenoyl-CoA
919.23535
C29H48N7O17P3S
(2E)-Octenoyl-CoA
891.20404
SMILES
C\C=C\C(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
CHEBI:28726
ChEBI
124-38-9
CAS
Pyrophosphate
1.0
P30084
UniProt
10140154
ChemSpider
CHEBI:15533
ChEBI
CHEBI:15532
ChEBI
1.0
(2E)-Hexadecenoyl-CoA
3-oxohexanoyl-CoA
Acetyl-CoA acetyltransferase, mitochondrial
1.0
CHEBI:28706
ChEBI
440615
PubChem-compound
1763-10-6
CAS
TETRADECANOYL-COA
BioCyc
CPD-1083
BioCyc
C05259
KEGG Compound
C05258
KEGG Compound
440610
PubChem-compound
HMDB0000222
HMDB
C05264
KEGG Compound
Short-chain specific acyl-CoA dehydrogenase, mitochondrial
C05263
KEGG Compound
C05266
KEGG Compound
C05265
KEGG Compound
SMILES
CCCCCCCCCCCCCCCC(=O)O[C@H](CC([O-])=O)C[N+](C)(C)C
P23786
UniProt
C05260
KEGG Compound
4.0
2.0
GO:0005759
GENE ONTOLOGY
Octanoyl-CoA
SMILES
CCCCCCCCCCCCCCCC(O)=O
C05262
KEGG Compound
P24752
UniProt
4.0
C05261
KEGG Compound
CHEBI:27868
ChEBI
19774-86-8
CAS
SMP0000054
SMPDB
HMDB0000220
HMDB
C35H62N7O17P3S
Tetradecanoyl-CoA
977.3136
electron-transfer flavoprotein
Short-chain specific acyl-CoA dehydrogenase, mitochondrial
Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial
SMILES
O=C=O
C05268
KEGG Compound
Very long-chain specific acyl-CoA dehydrogenase, mitochondrial
C05267
KEGG Compound
Hydrogen Ion
C05269
KEGG Compound
1.0
C05275
KEGG Compound
H4O7P2
Pyrophosphate
177.94322
C05274
KEGG Compound
C25H40N7O18P3S
Acetoacetyl-CoA
851.13635
C05276
KEGG Compound
C21H29N7O14P2
NADH
665.12476
C05271
KEGG Compound
C05270
KEGG Compound
C05273
KEGG Compound
5957
PubChem-compound
C05272
KEGG Compound
HMDB0001206
HMDB
PW000516
PathWhiz
GO:0005743
GENE ONTOLOGY
GO:0005741
GENE ONTOLOGY
Decanoyl-CoA
1.0
34619-89-1
CAS
1.0
4.2.1.17
false
4.2.1.17
3-Hydroxyhexanoyl-CoA ↔ (2E)-Hexenoyl-CoA + Water
REVERSIBLE
1.0
2.3.1.16
false
2.3.1.16
Acetyl-CoA + Butyryl-CoA → 3-oxohexanoyl-CoA + Coenzyme A
LEFT_TO_RIGHT
Reaction747
false
3-Hydroxyhexanoyl-CoA + NAD ↔ 3-oxohexanoyl-CoA + Hydrogen Ion + NADH
REVERSIBLE
CHEBI:15756
ChEBI
Palmitoyl-CoA
SubPathwayInteraction809
SubPathwayReaction
SubPathway809Reaction
L-Palmitoylcarnitine
(2E)-Hexadecenoyl-CoA
C37H66N7O17P3S
Palmitoyl-CoA
1005.34485
C33H58N7O18P3S
3-Hydroxydodecanoyl-CoA
965.27716
C26H42N7O19P3S
Glutaryl-CoA
881.1469
CHEBI:27721
ChEBI
C33H56N7O18P3S
3-oxododecanoyl-CoA
963.26154
C31H54N7O18P3S
3-Hydroxydecanoyl-CoA
937.2459
GO:0005737
GENE ONTOLOGY
1.0
C31H52N7O18P3S
3-oxodecanoyl-CoA
935.2302
C29H50N7O18P3S
3-hydroxyoctanoyl-CoA
909.2146
HMDB0001339
HMDB
HMDB0001338
HMDB
C29H48N7O18P3S
3-oxooctanoyl-CoA
907.1989
P33121
UniProt
Phospholipid Biosynthesis
SubPathway
ReactionCatalysis311
ACTIVATION
ReactionCatalysis312
ACTIVATION
Mitochondrial Outer Membrane
58623
ChemSpider
10018-95-8
CAS
79171-47-4
CAS
electron-transfer flavoprotein
SMILES
NC(=O)C1=C[N+](=CC=C1)[C@@H]1O[C@H](COP([O-])(=O)OP(O)(=O)OC[C@H]2O[C@H]([C@H](O)[C@@H]2O)N2C=NC3=C2N=CN=C3N)[C@@H](O)[C@H]1O
3-oxodecanoyl-CoA
1.0
Transport21
false
L-Palmitoylcarnitine (→) Transport: Homo sapiens, Cell, Cytoplasm to Homo sapiens, Cell, Mitochondrial Matrix
LEFT_TO_RIGHT
5682
ChemSpider
SMILES
CCCCCCCC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
2-METHYL-3-HYDROXY-BUTYRYL-COA
BioCyc
Reduced electron-transfer flavoprotein
5280765
PubChem-compound
CHEBI:1146900
ChEBI
4.0
CHEBI:28528
ChEBI
ReactionCatalysis308
ACTIVATION
ReactionCatalysis309
ACTIVATION
Mitochondrial Matrix
ReactionCatalysis307
ACTIVATION
5280769
PubChem-compound
ReactionCatalysis304
ACTIVATION
50411-91-1
CAS
ReactionCatalysis305
ACTIVATION
5280767
PubChem-compound
ReactionCatalysis302
ACTIVATION
14000-31-8
CAS
5280768
PubChem-compound
ReactionCatalysis303
ACTIVATION
ReactionCatalysis300
ACTIVATION
395736
ChemSpider
CO-A
BioCyc
CPD-8475
BioCyc
72-89-9
CAS
CHEBI:15452
ChEBI
1.0
SMILES
CCCC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
389056
ChemSpider
ReactionCatalysis2149
ACTIVATION
CHEBI:28632
ChEBI
C21H36N7O16P3S
Coenzyme A
767.11523
10917
PubChem-compound
4.0
CHEBI:27668
ChEBI
1.0
79171-48-5
CAS
10128117
ChemSpider
Cytoplasm
3-Hydroxybutyryl-CoA
1.0
10455
ChemSpider
CHEBI:27540
ChEBI
Trifunctional enzyme subunit beta, mitochondrial
C01944
KEGG Compound
ACETOACETYL-COA
BioCyc
14902
ChemSpider
1.0
CHEBI:15422
ChEBI
Very long-chain specific acyl-CoA dehydrogenase, mitochondrial
6557
ChemSpider
ReactionCatalysis2150
ACTIVATION
1.0
Homo sapiens
SMILES
CC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
1.0
388299
ChemSpider
Crotonoyl-CoA
439214
PubChem-compound
3-Hydroxydodecanoyl-CoA
CHEBI:27537
ChEBI
SMP0000025
SMPDB
Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial
ReactionCatalysis2153
ACTIVATION
SMILES
CCCCCCCCCCCC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
Palmitic acid
SubPathwayOutput
SubPathwayInput
C01832
KEGG Compound
P11310
UniProt
CHEBI:16526
ChEBI
SMP0000039
SMPDB
449118
PubChem-compound
122364-86-7
CAS
Medium-chain specific acyl-CoA dehydrogenase, mitochondrial
CHEBI:27402
ChEBI
CHEBI:27648
ChEBI
3-Hydroxyhexanoyl-CoA
1.0
9606
TAXONOMY
Acetyl-CoA acyltransferase
T2-DECENOYL-COA
BioCyc
C00877
KEGG Compound
PW000144
PathWhiz
PW000022
PathWhiz
1.3.8.8
false
1.3.8.8
Butyryl-CoA + electron-transfer flavoprotein ↔ Crotonoyl-CoA + Reduced electron-transfer flavoprotein
REVERSIBLE
392413
ChemSpider
4.2.1.17
false
4.2.1.17
3-Hydroxybutyryl-CoA ↔ Crotonoyl-CoA + Water
REVERSIBLE
145018
ChemSpider
10018-93-6
CAS
5893
PubChem-compound
C25H42N7O18P3S
3-Hydroxybutyryl-CoA
853.152
Glutaryl-CoA dehydrogenase, mitochondrial
CHEBI:28325
ChEBI
Trifunctional enzyme subunit alpha, mitochondrial
1420-36-6
CAS
CHEBI:15377
ChEBI
CHEBI:16347
ChEBI
3-ketoacyl-CoA thiolase, mitochondrial
CHEBI:15378
ChEBI
SMILES
[H+]
C00527
KEGG Compound
SMILES
NC1=NC=NC2=C1N=CN2[C@@H]1O[C@H](COP(O)(=O)OP(O)(=O)OP(O)(O)=O)[C@@H](O)[C@H]1O
CHEBI:15491
ChEBI
389499
ChemSpider
389498
ChemSpider
CHEBI:27466
ChEBI
280
PubChem-compound
Glutaryl-CoA dehydrogenase, mitochondrial
26332261
ChemSpider
2.3.1.9
false
2.3.1.9
2 Acetyl-CoA ↔ Acetoacetyl-CoA + Coenzyme A
REVERSIBLE
4444333
ChemSpider
1.0
4444334
ChemSpider
1.0
4444335
ChemSpider
SMILES
CCCCCC(=O)SCCNC(=O)CCNC(=O)[C@H](O)C(C)(C)COP(O)(=O)OP(O)(=O)OC[C@H]1O[C@H]([C@H](O)[C@@H]1OP(O)(O)=O)N1C=NC2=C1N=CN=C2N
CHEBI:15345
ChEBI
(2E)-Tetradecenoyl-CoA
Glutaryl-CoA
4.0
4444331
ChemSpider
46173176
PubChem-compound
6244-92-4
CAS
10018-94-7
CAS
1.0
439252
PubChem-compound
15667
PubChem-compound
1.0
Long-chain specific acyl-CoA dehydrogenase, mitochondrial
L-Palmitoylcarnitine
HMDB0001967
HMDB
1.0
electron-transfer flavoprotein
CHEBI:15351
ChEBI
388388
ChemSpider
CHEBI:15473
ChEBI
Very-Long-Chain Acyl-CoA Dehydrogenase Deficiency (VLCAD)
85-61-0
CAS