6022
PubChem-compound
392615
ChemSpider
937
ChemSpider
C6H14O12P2
α-D-Glucose 1,6-bisphosphate
339.99606
Glucose 1,6-bisphosphate synthase
GLUCURONATE
BioCyc
5.3.1.9
false
5.3.1.9
β-D-Fructose 6-phosphate ↔ Glucose 6-phosphate
REVERSIBLE
439153
PubChem-compound
88070-93-3
CAS
Phosphoglucomutase-1
6556-12-3
CAS
6133
PubChem-compound
C00208
KEGG Compound
4.0
ATP
BioCyc
53188-23-1
CAS
53477771
PubChem-compound
559142
ChemSpider
1.0
SubPathwayInteraction179
SubPathwayReaction
SubPathway179Reaction
5743
ChemSpider
5742
ChemSpider
NADH
CHEBI:17200
ChEBI
2.4.1.1
false
2.4.1.1
Glycogen + Phosphate → Amylose + Glucose 1-phosphate
LEFT_TO_RIGHT
Sucrase-isomaltase, intestinal
ALPHA-GLUCOSE-16-BISPHOSPHATE
BioCyc
5.4.2.2
false
5.4.2.2
Uridine diphosphate glucose → Glucose 1-phosphate
LEFT_TO_RIGHT
2.4.1.11
false
2.4.1.11
Uridine diphosphate glucose → Amylose + Uridine 5'-diphosphate
LEFT_TO_RIGHT
2.7.1.106
false
2.7.1.106
Glucose 1-phosphate + Glyceric acid 1,3-biphosphate → 3-Phosphoglyceric acid + α-D-Glucose 1,6-bisphosphate
LEFT_TO_RIGHT
439177
PubChem-compound
ReactionCatalysis968
ACTIVATION
Beta-glucuronidase
9166684
ChemSpider
ReactionCatalysis967
ACTIVATION
2.4.1.17
false
2.4.1.17
Uridine diphosphate glucuronic acid → Isovalerylglucuronide + Uridine 5'-diphosphate
LEFT_TO_RIGHT
3.2.1.31
false
3.2.1.31
Isovalerylglucuronide + Water → Alcohol + D-Glucuronic acid
LEFT_TO_RIGHT
SMILES
OC1O[C@H](COP(O)(O)=O)[C@@H](O)[C@H](O)[C@H]1O
CHEBI:28102
ChEBI
2.4.1.18
false
2.4.1.18
Amylose → Glycogen
LEFT_TO_RIGHT
Uridine 5'-diphosphate
CPD0-971
BioCyc
53477679
PubChem-compound
UDP-GLUCURONATE
BioCyc
6031
PubChem-compound
133-89-1
CAS
704
ChemSpider
1.0
PW000152
PathWhiz
C00103
KEGG Compound
1,4-alpha-glucan-branching enzyme
1.0
2.0
439165
PubChem-compound
PPI
BioCyc
Uridine 5'-diphosphate
SMP0000554
SMPDB
Reaction1266
false
D-Fructose + α-D-Glucose ← Sucrose + Water
RIGHT_TO_LEFT
1.0
ReactionCatalysis994
ACTIVATION
C15H22N2O18P2
Uridine diphosphate glucuronic acid
580.0343
ReactionCatalysis992
ACTIVATION
1.0
5768
ChemSpider
389526
ChemSpider
59-56-3
CAS
C3H8O10P2
Glyceric acid 1,3-biphosphate
265.95926
444791
PubChem-compound
Cytosol
Transport64
false
α-D-Glucose (→) Transport: Homo sapiens, Extracellular Space to Homo sapiens, Cell, Cytosol
LEFT_TO_RIGHT
C00236
KEGG Compound
Transport63
false
D-Fructose (→) Transport: Homo sapiens, Extracellular Space to Homo sapiens, Cell, Cytosol
LEFT_TO_RIGHT
388311
ChemSpider
1.0
C00597
KEGG Compound
Transport66
false
D-Maltose (→) Transport: Homo sapiens, Extracellular Space to Homo sapiens, Cell, Cytosol
LEFT_TO_RIGHT
Transport65
false
Glycogen (→) Transport: Homo sapiens, Extracellular Space to Homo sapiens, Cell, Cytosol
LEFT_TO_RIGHT
1.0
Reaction1296
false
4 Amylose → Glycogen + 2 α-D-Glucose
LEFT_TO_RIGHT
Reaction1294
false
Dextrin → 3 α-D-Glucose
LEFT_TO_RIGHT
3.2.1.1
false
3.2.1.1
Glycogen → Dextrin
LEFT_TO_RIGHT
ReactionCatalysis988
ACTIVATION
ReactionCatalysis986
ACTIVATION
ReactionCatalysis987
ACTIVATION
C6H12O6
D-Fructose
180.06339
ReactionCatalysis982
ACTIVATION
C00009
KEGG Compound
C00008
KEGG Compound
C00001
KEGG Compound
Reaction1290
false
4 α-D-Glucose → Glycogen
LEFT_TO_RIGHT
Beta-D-Glucuronides
BioCyc
CHEBI:18361
ChEBI
1.0
C00004
KEGG Compound
388322
ChemSpider
CHEBI:18367
ChEBI
C00003
KEGG Compound
1032
ChemSpider
C00002
KEGG Compound
Q6PCE3
UniProt
UDP-glucuronosyltransferase 2B11
C6H12O6
α-D-Glucose
180.06339
GLC-1-P
BioCyc
1.0
C24H42O21
Glycogen
666.22186
388775
ChemSpider
C21H27N7O14P2
NAD
663.10913
HMDB0002091
HMDB
HMDB0000902
HMDB
FRUCTOSE-6P
BioCyc
C00015
KEGG Compound
Extracellular Space
α-D-Glucose
C00013
KEGG Compound
Glycogen debranching enzyme
Glycogen phosphorylase, liver form
6.0
C00029
KEGG Compound
P54840
UniProt
62698
PubChem-compound
P52789
UniProt
56-65-5
CAS
53-84-9
CAS
O75310
UniProt
C00267
KEGG Compound
C02336
KEGG Compound
HMDB0001586
HMDB
SMILES
NC(=O)C1=CN(C=CC1)[C@@H]1O[C@H](CO[P@](O)(=O)O[P@](O)(=O)OC[C@H]2O[C@H]([C@H](O)[C@@H]2O)N2C=NC3=C(N)N=CN=C23)[C@@H](O)[C@H]1O
HMDB0003403
HMDB
Beta-glucuronidase
HMDB0000258
HMDB
SMILES
OC[C@H]1O[C@@](CO)(O[C@H]2O[C@H](CO)[C@@H](O)[C@H](O)[C@H]2O)[C@@H](O)[C@@H]1O
P06737
UniProt
CHEBI:28087
ChEBI
2.0
HMDB0000250
HMDB
10991489
PubChem-compound
SMILES
OP(O)(=O)OP(O)(O)=O
HMDB0001341
HMDB
P06744
UniProt
C18H32O16
Dextrin
504.16904
C11H18O8
Isovalerylglucuronide
278.10016
C00167
KEGG Compound
SMILES
NC1=NC=NC2=C1N=CN2[C@@H]1O[C@H](COP(O)(=O)OP(O)(O)=O)[C@@H](O)[C@H]1O
Sucrose
1.0
1.0
9004-53-9
CAS
C9H14N2O12P2
Uridine 5'-diphosphate
404.0022
Isovalerylglucuronide
UTP
BioCyc
5903
ChemSpider
C3H7O7P
3-Phosphoglyceric acid
185.99294
Hexokinase-2
7732-18-5
CAS
Glucokinase
CHEBI:16077
ChEBI
CHEBI:4170
ChEBI
HMDB0001487
HMDB
C00182
KEGG Compound
492-62-6
CAS
1.0
16522
ChemSpider
2.7.7.9
false
2.7.7.9
Glucose 1-phosphate + Uridine triphosphate → Pyrophosphate + Uridine diphosphate glucose
LEFT_TO_RIGHT
1.1.1.22
false
1.1.1.22
2 NAD + Uridine diphosphate glucose + Water → 2 NADH + Uridine diphosphate glucuronic acid
LEFT_TO_RIGHT
NAD
CHEBI:18148
ChEBI
5.4.2.2
false
5.4.2.2
Glucose 1-phosphate ↔ Glucose 6-phosphate
REVERSIBLE
C10H16N5O13P3
Adenosine triphosphate
506.99576
1.0
DPG
BioCyc
CHEBI:16084
ChEBI
2.0
1.0
1.0
C00191
KEGG Compound
663
ChemSpider
α-D-Glucose
9005-82-7
CAS
CHEBI:17050
ChEBI
(C12H20O11)nC2H6
Amylose
HMDB0000163
HMDB
3-Phosphoglyceric acid
HMDB0000286
HMDB
HMDB0000285
HMDB
962
PubChem-compound
C12H22O11
D-Maltose
342.1162
724
PubChem-compound
1.0
5800
ChemSpider
58-98-0
CAS
C00075
KEGG Compound
HMDB0002111
HMDB
HMDB0000295
HMDB
5809
ChemSpider
14265-44-2
CAS
Glucose-6-phosphate isomerase
58-64-0
CAS
C00089
KEGG Compound
C6H13O9P
Glucose 1-phosphate
260.02972
1.0
C00092
KEGG Compound
71358
ChemSpider
G3P
BioCyc
Glucose-6-phosphate isomerase
HMDB0001270
HMDB
Glycogen phosphorylase, liver form
D-Fructose
CHEBI:47937
ChEBI
644102
PubChem-compound
Alpha-amylase 1
56-73-5
CAS
Phosphoglucomutase-1
1.0
HMDB0003345
HMDB
H2O
Water
18.010565
HMDB0006857
HMDB
NADH
BioCyc
SMILES
OC[C@H]1O[C@H](OP(O)(=O)OP(O)(=O)OC[C@H]2O[C@H]([C@H](O)[C@@H]2O)N2C=CC(=O)NC2=O)[C@H](O)[C@@H](O)[C@@H]1O
O43451
UniProt
β-D-Fructose 6-phosphate
SMILES
O[C@H]1[C@@H](O)[C@@H](O[C@@H]1COP(O)(=O)OP(O)(=O)OP(O)(O)=O)N1C=CC(=O)NC1=O
NAD
BioCyc
3.0
1.0
1.0
SMILES
OC[C@@]1(O)O[C@H](COP(O)(O)=O)[C@@H](O)[C@@H]1O
1.0
820-11-1
CAS
SMILES
O[C@H]1O[C@@H]([C@@H](O)[C@H](O)[C@H]1O)C(O)=O
SUCROSE
BioCyc
CPD-535
BioCyc
Glycogen debranching enzyme
1.0
SMILES
O
P35573
UniProt
439709
PubChem-compound
2616-64-0
CAS
Alpha-amylase 1
HMDB0000538
HMDB
Glucokinase
1981-49-3
CAS
10139-18-1
CAS
Glycolysis
SubPathway
Isovalerylglucuronide
CHEBI:15846
ChEBI
ADP
BioCyc
HMDB0000660
HMDB
Lysosome
Alcohol
C05345
KEGG Compound
GO:0005829
GENE ONTOLOGY
HMDB0001401
HMDB
P14410
UniProt
CHEBI:16908
ChEBI
CHEBI:15713
ChEBI
Pyrophosphate
H3O4P
Phosphate
97.9769
SMILES
CC(C)CC(=O)O[C@@H]1O[C@@H]([C@@H](O)[C@H](O)[C@H]1O)C(O)=O
5988
PubChem-compound
SMILES
OC[C@H]1OC(O[C@H]2[C@H](O)[C@@H](O)C(O[C@H]3[C@H](O)[C@@H](O)[C@@H](O)O[C@@H]3CO)O[C@@H]2CO)[C@H](O)[C@@H](O)[C@@H]1O
1.0
Q04446
UniProt
UTP--glucose-1-phosphate uridylyltransferase
137383
PubChem-compound
UDP-glucose 6-dehydrogenase
Amylose
O60701
UniProt
SMILES
O[C@H]1[C@@H](O)[C@@H](O[C@@H]1COP(O)(=O)OP(O)(O)=O)N1C=CC(=O)NC1=O
P04745
UniProt
UDP-glucose 6-dehydrogenase
Hexokinase-2
UDP-glucose 6-dehydrogenase
Glucose 1-phosphate
1,4-alpha-glucan-branching enzyme
683
PubChem-compound
C15H24N2O17P2
Uridine diphosphate glucose
566.055
UDP-GLUCOSE
BioCyc
58-68-4
CAS
C9H15N2O15P3
Uridine triphosphate
483.96854
SMP0000040
SMPDB
SMILES
OP(O)(O)=O
GO:0005886
GENE ONTOLOGY
1.0
GO:0005764
GENE ONTOLOGY
PW000530
PathWhiz
UTP--glucose-1-phosphate uridylyltransferase
HMDB0001429
HMDB
D-Maltose
C6H13O9P
β-D-Fructose 6-phosphate
260.02972
C6H10O7
D-Glucuronic acid
194.04265
17473
PubChem-compound
Gluconeogenesis
SubPathway
HMDB0003971
HMDB
Maltase-glucoamylase, intestinal
P35557
UniProt
1.0
SMILES
OC[C@H]1O[C@H](O[C@H]2[C@H](O)[C@H](O)[C@@H](O)O[C@@H]2CO)[C@H](O)[C@@H](O)[C@@H]1O
α-D-Glucose 1,6-bisphosphate
440641
PubChem-compound
H4O7P2
Pyrophosphate
177.94322
1.0
5958
PubChem-compound
C21H29N7O14P2
NADH
665.12476
5957
PubChem-compound
C12H22O11
Sucrose
342.1162
74362
ChemSpider
SMILES
OC[C@H]1OC(OP(O)(O)=O)[C@H](O)[C@@H](O)[C@@H]1O
1.0
Glycogen [starch] synthase, liver
Adenosine triphosphate
GO:0005615
GENE ONTOLOGY
C10H15N5O10P2
Adenosine diphosphate
427.02942
HMDB0000127
HMDB
HMDB0003514
HMDB
P36871
UniProt
CHEBI:17925
ChEBI
Glucose 1,6-bisphosphate synthase
56445
ChemSpider
SMP0000128
SMPDB
UTP--glucose-1-phosphate uridylyltransferase
Endoplasmic Reticulum
P08236
UniProt
D-Maltose
SMILES
NC(=O)C1=C[N+](=CC=C1)[C@@H]1O[C@H](COP([O-])(=O)OP(O)(=O)OC[C@H]2O[C@H]([C@H](O)[C@@H]2O)N2C=NC3=C2N=CN=C3N)[C@@H](O)[C@H]1O
CPD-8587
BioCyc
SMILES
OC[C@H]1O[C@H](OC[C@H]2O[C@H](O[C@H]3[C@H](O)[C@@H](O)[C@@H](O)O[C@@H]3CO)[C@H](O)[C@@H](O)[C@@H]2O[C@H]2O[C@H](CO)[C@@H](O)[C@H](O)[C@H]2O)[C@H](O)[C@@H](O)[C@@H]1O
1.0
HMDB0000807
HMDB
5682
ChemSpider
UDP
BioCyc
CHEBI:28645
ChEBI
4.0
9005-79-2
CAS
C00718
KEGG Compound
Glycogenosis, Type IV. Amylopectinosis, Anderson Disease
2.0
C6H13O9P
Glucose 6-phosphate
260.02972
14000-31-8
CAS
C00721
KEGG Compound
Glycogen
HMDB0000935
HMDB
CHEBI:42717
ChEBI
CHEBI:17992
ChEBI
Phosphoglucomutase-1
Adenosine diphosphate
SMILES
O[C@H](COP(O)(O)=O)C(=O)OP(O)(O)=O
Uridine triphosphate
D-Fructose
CHEBI:15422
ChEBI
Homo sapiens
SMILES
O[C@H]1[C@H](O)[C@@H](COP(O)(O)=O)O[C@H](OP(O)(O)=O)[C@@H]1O
388299
ChemSpider
Uridine diphosphate glucuronic acid
1.0
UDP-glucuronosyltransferase 2B11
Glucose 1-phosphate
1.0
GO:0005783
GENE ONTOLOGY
Water
Water
82400
PubChem-compound
69-79-4
CAS
Uridine diphosphate glucose
CHEBI:16761
ChEBI
GLC-6-P
BioCyc
Reaction1303
false
D-Maltose → 2 α-D-Glucose
LEFT_TO_RIGHT
1.0
Reaction1300
false
D-Maltose → 2 α-D-Glucose
LEFT_TO_RIGHT
9606
TAXONOMY
Glucose 6-phosphate
SubPathwayInput
D-Glucuronic acid
PW000146
PathWhiz
Uridine diphosphate glucose
Glycogen [starch] synthase, liver
Uridine diphosphate glucuronic acid
SMILES
OC(COP(O)(O)=O)C(O)=O
Dextrin
5893
PubChem-compound
Alcohol
ReactionCatalysis1005
ACTIVATION
ReactionCatalysis1007
ACTIVATION
1.0
ReactionCatalysis1009
ACTIVATION
CHEBI:30879
ChEBI
2.7.1.1
false
2.7.1.1
Adenosine triphosphate + D-Fructose → Adenosine diphosphate + β-D-Fructose 6-phosphate
LEFT_TO_RIGHT
2.7.1.2
false
2.7.1.2
Adenosine triphosphate + α-D-Glucose → Adenosine diphosphate + Glucose 6-phosphate
LEFT_TO_RIGHT
CHEBI:15377
ChEBI
Cell Membrane
121058
ChemSpider
Glucose-6-phosphate isomerase
MALTOSE
BioCyc
SMILES
NC1=NC=NC2=C1N=CN2[C@@H]1O[C@H](COP(O)(=O)OP(O)(=O)OP(O)(O)=O)[C@@H](O)[C@H]1O
Glyceric acid 1,3-biphosphate
Phosphate
ReactionCatalysis1015
ACTIVATION
ReactionCatalysis1018
ACTIVATION
SubPathwayInteraction180
SubPathway180Reaction
SubPathwayReaction
SMILES
CO[C@H]1O[C@H](CO)[C@@H](O[C@H]2O[C@H](CO)[C@@H](OC)[C@H](O)[C@H]2O)[C@H](O)[C@H]1O
79025
PubChem-compound
1.0
ReactionCatalysis1011
ACTIVATION
ReactionCatalysis377
ACTIVATION
ReactionCatalysis375
ACTIVATION
ReactionCatalysis376
ACTIVATION
ReactionCatalysis374
ACTIVATION
SMILES
O[C@@H]1[C@@H](COP(O)(=O)OP(O)(=O)O[C@H]2O[C@@H]([C@@H](O)[C@H](O)[C@H]2O)C(O)=O)O[C@H]([C@@H]1O)N1C=CC(=O)NC1=O
Maltase-glucoamylase, intestinal
1.0
1.0
Glycogen
ReactionCatalysis2112
ACTIVATION
ReactionCatalysis2113
ACTIVATION
63-39-8
CAS
1061
PubChem-compound
Q16851
UniProt
57-50-1
CAS
CHEBI:17659
ChEBI
C00660
KEGG Compound
HMDB0000757
HMDB
Maltase-glucoamylase, intestinal
SMILES
OC[C@H]1O[C@](O)(CO)[C@@H](O)[C@@H]1O
Sucrase-isomaltase, intestinal
SMILES
OC[C@H]1O[C@H](O)[C@H](O)[C@@H](O)[C@@H]1O
8.0