CHEBI:16015
ChEBI
CHEBI:16136
ChEBI
30572
ChemSpider
6022
PubChem-compound
SubPathwayInteraction834
SubPathwayReaction
SubPathway834Reaction
SMILES
N[C@@H](CS)C(O)=O
SubPathwayInteraction837
SubPathway837Reaction
SubPathwayReaction
937
ChemSpider
SubPathwayInteraction838
SubPathwayReaction
SubPathway838Reaction
SubPathwayInteraction835
SubPathwayReaction
SubPathway835Reaction
CYS
BioCyc
5975
PubChem-compound
SubPathwayInteraction836
SubPathway836Reaction
SubPathwayReaction
tRNA(Cys)
CHEBI:16134
ChEBI
SubPathwayInteraction839
SubPathwayReaction
SubPathway839Reaction
C8H14N2O5S
γ-Glutamylcysteine
250.06235
1.0
Methionine Metabolism
SubPathway
CNS
Thiocyanate
57.975143
O60931
UniProt
TransportCatalysis97
ACTIVATION
4.4.1.1
false
4.4.1.1
L-Cysteine + Water → Ammonia + Hydrogen sulfide + Pyruvic acid
LEFT_TO_RIGHT
18779926
PubChem-compound
439153
PubChem-compound
SMILES
O
L-Cysteinyl-tRNA(Cys)
H3N
Ammonia
17.026548
L-lactate dehydrogenase A chain
C10H14N5O7P
Adenosine monophosphate
347.06308
50
ChemSpider
CHEBI:17359
ChEBI
PW000056
PathWhiz
CHEBI:16027
ChEBI
PW000054
PathWhiz
Cysteine--tRNA ligase, cytoplasmic
HMDB0000538
HMDB
439270
PubChem-compound
1004
PubChem-compound
ATP
BioCyc
SubPathwayInteraction828
SubPathway828Reaction
SubPathwayReaction
SubPathwayInteraction829
SubPathway829Reaction
SubPathwayReaction
Aspartate aminotransferase, cytoplasmic
1.0
Sulfate/Sulfite Metabolism
SubPathway
51
PubChem-compound
Water
SMILES
OC(CS)C(O)=O
559142
ChemSpider
CHEBI:15846
ChEBI
Cystinosis, Ocular Nonnephropathic
ADP
BioCyc
C3H4O3
Pyruvic acid
88.016045
H2O3S
Sulfite
81.972466
Transport126
false
L-Cysteine (→) Transport: Homo sapiens, Cell, Lysosome to Homo sapiens, Cell, Cytosol
LEFT_TO_RIGHT
3-Mercaptolactic acid
Lysosome
1.0
SMILES
N[C@@H](CS(O)=O)C(O)=O
141158
ChemSpider
5742
ChemSpider
3-mercaptopyruvate sulfurtransferase
CHEBI:17561
ChEBI
PW000040
PathWhiz
952
ChemSpider
GO:0005829
GENE ONTOLOGY
HMDB0001405
HMDB
Cystinosin
C5H6O5
Oxoglutaric acid
146.02153
391
ChemSpider
SMILES
OC(=O)C(=O)CS(O)=O
CHEBI:16908
ChEBI
5858
ChemSpider
Adenosine monophosphate
PW000032
PathWhiz
PW000038
PathWhiz
PW000157
PathWhiz
5862
PubChem-compound
PPI
BioCyc
Pyruvate Metabolism
SubPathway
302-04-5
CAS
6.3.2.2
false
6.3.2.2
Adenosine triphosphate + L-Cysteine + L-Glutamic acid → Adenosine diphosphate + Phosphoric acid + γ-Glutamylcysteine
LEFT_TO_RIGHT
HMDB0003276
HMDB
2.8.1.2
false
2.8.1.2
3-Mercaptopyruvic acid + Cyanide → Pyruvic acid + Thiocyanate
LEFT_TO_RIGHT
SMP0000722
SMPDB
Reaction713
true
3-Sulfinylpyruvic acid + Water → Pyruvic acid + Sulfite
LEFT_TO_RIGHT
Reaction711
false
3-Sulfinoalanine + Oxoglutaric acid → 3-Sulfinylpyruvic acid + L-Glutamic acid
LEFT_TO_RIGHT
HMDB0000208
HMDB
L-Glutamic acid
SubPathwayOutput
Cytosol
CPD-6641
BioCyc
217
ChemSpider
ReactionCatalysis55
ACTIVATION
HMDB0000574
HMDB
58-68-4
CAS
SMILES
OC(=O)CCC(=O)C(O)=O
7664-38-2
CAS
1.13.11.20
false
1.13.11.20
L-Cysteine + Oxygen → 3-Sulfinoalanine
LEFT_TO_RIGHT
CHEBI:30915
ChEBI
1.0
96
ChemSpider
GO:0005764
GENE ONTOLOGY
HSCN
BioCyc
SMP0000041
SMPDB
C00009
KEGG Compound
C00008
KEGG Compound
C00007
KEGG Compound
Aspartate aminotransferase, cytoplasmic
5755
ChemSpider
3-Sulfinylpyruvic acid
6.1.1.16
false
6.1.1.16
Adenosine triphosphate + L-Cysteine + tRNA(Cys) → Adenosine monophosphate + L-Cysteinyl-tRNA(Cys) + Pyrophosphate
LEFT_TO_RIGHT
Glutamate--cysteine ligase regulatory subunit
C00001
KEGG Compound
CHEBI:18361
ChEBI
C00004
KEGG Compound
C00003
KEGG Compound
1.0
C00002
KEGG Compound
1031
ChemSpider
P48506
UniProt
P48507
UniProt
C3H4O3S
3-Mercaptopyruvic acid
119.98811
16743745
ChemSpider
3-SULFINYL-PYRUVATE
BioCyc
2.0
Reaction720
false
L-Cysteine + Oxoglutaric acid ↔ 3-Mercaptopyruvic acid + L-Glutamic acid
REVERSIBLE
GLT
BioCyc
7664-41-7
CAS
1.1.1.27
false
1.1.1.27
3-Mercaptolactic acid + NAD → 3-Mercaptopyruvic acid + NADH
LEFT_TO_RIGHT
7783-06-4
CAS
γ-Glutamylcysteine
SubPathwayInput
HMDB0002084
HMDB
Glycine and Serine Metabolism
SubPathway
Oxygen
Cysteine dioxygenase type 1
1068
ChemSpider
C21H27N7O14P2
NAD
663.10913
1.0
Adenosine triphosphate
Glutamate--cysteine ligase catalytic subunit
1.0
1.0
C05823
KEGG Compound
HMDB0000902
HMDB
222
PubChem-compound
C00014
KEGG Compound
C00013
KEGG Compound
SMILES
OP(O)(O)=O
H4O7P2
Pyrophosphate
177.94322
SMP0000060
SMPDB
C21H29N7O14P2
NADH
665.12476
3-mercaptopyruvate sulfurtransferase
1.0
5957
PubChem-compound
P00338
UniProt
Pyruvic acid
SubPathwayInput
H2S
Hydrogen sulfide
33.98772
C00022
KEGG Compound
56-65-5
CAS
L-lactate dehydrogenase A chain
5653
ChemSpider
57517667
PubChem-compound
53-84-9
CAS
Cystinosin
C00020
KEGG Compound
Cystathionine gamma-lyase
C00026
KEGG Compound
C00025
KEGG Compound
CHEBI:26078
ChEBI
1.0
SMP0000072
SMPDB
HMDB0000243
HMDB
HMDB0001453
HMDB
Taurine and Hypotaurine Metabolism
SubPathway
C10H15N5O10P2
Adenosine diphosphate
427.02942
4.0
Thiocyanate
GO:0005737
GENE ONTOLOGY
Glutamate--cysteine ligase regulatory subunit
CHN
Cyanide
27.010899
Aspartate aminotransferase, cytoplasmic
Glutamate--cysteine ligase catalytic subunit
1.0
HMDB0000240
HMDB
Pantothenate and CoA Biosynthesis
SubPathway
1.0
C3H7NO4S
3-Sulfinoalanine
153.00958
1.0
C00957
KEGG Compound
1.0
52-90-4
CAS
NADH
SMILES
NC(=O)C1=C[N+](=CC=C1)[C@@H]1O[C@H](COP([O-])(=O)OP(O)(=O)OC[C@H]2O[C@H]([C@H](O)[C@@H]2O)N2C=NC3=C2N=CN=C3N)[C@@H](O)[C@H]1O
P49589
UniProt
1.0
1099
PubChem-compound
5682
ChemSpider
328-50-7
CAS
C3H4O5S
3-Sulfinylpyruvic acid
151.97795
SMILES
NC(=O)C1=CN(C=CC1)[C@@H]1O[C@H](CO[P@](O)(=O)O[P@](O)(=O)OC[C@H]2O[C@H]([C@H](O)[C@@H]2O)N2C=NC3=C(N)N=CN=C23)[C@@H](O)[C@H]1O
1.0
2614-83-7
CAS
AMP
BioCyc
C00283
KEGG Compound
1.0
110467
ChemSpider
SMP0000004
SMPDB
tRNA(Cys)
HMDB0000250
HMDB
L-Cysteinyl-tRNA(Cys)
1.0
SMILES
OP(O)(=O)OP(O)(O)=O
HMDB0001341
HMDB
14000-31-8
CAS
PW000699
PathWhiz
C00606
KEGG Compound
CHEBI:17514
ChEBI
CHEBI:17515
ChEBI
Cysteine--tRNA ligase, cytoplasmic
Sulfite
160645
PubChem-compound
SMILES
S
SMILES
NC1=NC=NC2=C1N=CN2[C@@H]1O[C@H](COP(O)(=O)OP(O)(O)=O)[C@@H](O)[C@H]1O
HMDB0000148
HMDB
1115-65-7
CAS
SMILES
C#[N-]
Cytoplasm
1.0
CHEBI:29167
ChEBI
SO3
BioCyc
CHEBI:15422
ChEBI
SMP0000027
SMPDB
Homo sapiens
C00177
KEGG Compound
4911362
ChemSpider
P32929
UniProt
1.0
SMILES
N[C@@H](CCC(=O)N[C@@H](CS)C(O)=O)C(O)=O
3-Sulfinoalanine
SubPathwayInput
7732-18-5
CAS
388299
ChemSpider
SMILES
[S-]C#N
HMDB0001487
HMDB
61-19-8
CAS
123938
PubChem-compound
SMILES
NC1=C2N=CN([C@@H]3O[C@H](COP(O)(O)=O)[C@@H](O)[C@H]3O)C2=NC=N1
O2
Oxygen
31.98983
HMDB0001368
HMDB
127-17-3
CAS
AMMONIA
BioCyc
SMILES
N
56-86-0
CAS
L-Cysteine
SubPathwayOutput
SubPathwayInput
CHEBI:29152
ChEBI
Adenosine diphosphate
SMP0000021
SMPDB
Hydrogen sulfide
C5H9NO4
L-Glutamic acid
147.05316
33032
PubChem-compound
C10H16N5O13P3
Adenosine triphosphate
506.99576
CHEBI:18022
ChEBI
Glutamate--cysteine ligase
Phosphoric acid
Cystathionine gamma-lyase
8961
ChemSpider
CHEBI:16761
ChEBI
7782-44-7
CAS
Pyrophosphate
HMDB0001377
HMDB
SMILES
CC(=O)C(O)=O
HMDB0000045
HMDB
SMILES
OS(O)=O
1.0
Ammonia
SMP0000033
SMPDB
9606
TAXONOMY
962
PubChem-compound
ReactionCatalysis231
ACTIVATION
2-KETOGLUTARATE
BioCyc
5800
ChemSpider
3-SULFINOALANINE
BioCyc
C05527
KEGG Compound
979
ChemSpider
636-58-8
CAS
1.0
5893
PubChem-compound
SMILES
O=O
H3O4P
Phosphoric acid
97.9769
Glutamate Metabolism
SubPathway
Oxoglutaric acid
HMDB0000051
HMDB
ReactionCatalysis229
ACTIVATION
SMILES
N[C@@H](CCC(O)=O)C(O)=O
HMDB0002111
HMDB
CHEBI:32816
ChEBI
3-MERCAPTO-PYRUVATE
BioCyc
ReactionCatalysis228
ACTIVATION
ReactionCatalysis226
ACTIVATION
1.0
CHEBI:15377
ChEBI
L-Cysteine
CHEBI:15379
ChEBI
ReactionCatalysis221
ACTIVATION
2464-23-5
CAS
ReactionCatalysis220
ACTIVATION
PYRUVATE
BioCyc
58-64-0
CAS
SMILES
NC1=NC=NC2=C1N=CN2[C@@H]1O[C@H](COP(O)(=O)OP(O)(=O)OP(O)(O)=O)[C@@H](O)[C@H]1O
1.0
Cystathionine gamma-lyase
9322
PubChem-compound
1.0
3-Mercaptopyruvic acid
HMDB0002127
HMDB
C00094
KEGG Compound
P25325
UniProt
98
PubChem-compound
ReactionCatalysis219
ACTIVATION
Q16878
UniProt
C3H7NO2S
L-Cysteine
121.01975
644102
PubChem-compound
6083
PubChem-compound
1.0
PW000003
PathWhiz
1.0
C00097
KEGG Compound
HS
BioCyc
HMDB0001049
HMDB
HMDB0000996
HMDB
H2O
Water
18.010565
57-12-5
CAS
NADH
BioCyc
NAD
BioCyc
C00669
KEGG Compound
1060
PubChem-compound
14265-45-3
CAS
CHEBI:41721
ChEBI
C01755
KEGG Compound
977
PubChem-compound
CHEBI:16208
ChEBI
L-GAMMA-GLUTAMYLCYSTEINE
BioCyc
SMILES
OC(=O)C(=O)CS
1.0
Cyanide
C3H6O3S
3-Mercaptolactic acid
122.00376
Cysteine dioxygenase type 1
1.0
NAD
L-Cysteine
P17174
UniProt
HMDB0002142
HMDB