Carnitine O-
palmitoyltransferase
1, liver
isoform
Long-chain
fatty acid
transport
protein 1
Mitochondrial
carnitine/acylcarnitine
carrier protein
Organic
cation/carnitine
transporter 2
Long-chain-
fatty-acid--
CoA ligase 1
Carnitine O-
palmitoyltransferase
1, liver
isoform
Acetyl-CoA
carboxylase 1
Malonyl-CoA
decarboxylase,
mitochondrial
Carnitine O-
palmitoyltransferase
2,
mitochondrial
Carnitine O-
acetyltransferase
Acetyl-CoA
(20‐{[1‐Carboxylato‐3‐(trimethylammonio)propan‐2‐
yl]oxy}‐20‐oxoicosa‐6,8,12,15‐tetraen‐10‐yl)peroxy-
CoA
[(4Z,7Z,11E,13Z)-
1-
carboxynonadeca-
4,7,11,13-
tetraen-10-
yl]peroxy
[(4Z,7Z,11E,13Z)-
1-
carboxynonadeca-
4,7,11,13-
tetraen-10-
yl]peroxy
(20‐{[1‐Carboxylato‐3‐(trimethylammonio)propan‐2‐
yl]oxy}‐20‐oxoicosa‐6,8,12,15‐tetraen‐10‐yl)peroxy
(20‐{[1‐Carboxylato‐3‐(trimethylammonio)propan‐2‐
yl]oxy}‐20‐oxoicosa‐6,8,12,15‐tetraen‐10‐yl)peroxy
L-Carnitine
ATP
CoA
(20‐{[1‐Carboxylato‐3‐(trimethylammonio)propan‐2‐
yl]oxy}‐20‐oxoicosa‐6,8,12,15‐tetraen‐10‐yl)peroxy-
CoA
AMP
PPi
L-Carnitine
CoA
Acetyl-CoA
Malonyl-CoA
CO2
CoA
L-Carnitine
L-Carnitine
L-
Acetylcarnitine
CoA
Magnesium
Biotin
Manganese
TCA Cycle
Mitochondrial
Beta-Oxidation
of Long Chain
Saturated Fatty
Acids
Mitochondrial Outer Membrane
Mitochondrial Inner Membrane
Extracellular Space
Cytosol
Intermembrane Space
Mitochondrial Matrix
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