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Amine oxidase
[flavin-
containing] A
Aldehyde
dehydrogenase,
mitochondrial
Dimethylglycine
dehydrogenase,
mitochondrial
Sarcosine
dehydrogenase,
mitochondrial
Aminomethyltransferase,
mitochondrial
Serine
hydroxymethyltransferase,
mitochondrial
Dihydrolipoyl
dehydrogenase,
mitochondrial
Serine--
pyruvate
aminotransferase
Serine--
pyruvate
aminotransferase
Glycine
amidinotransferase,
mitochondrial
Guanidinoacetate
N-
methyltransferase
5-
aminolevulinate
synthase,
nonspecific,
mitochondrial
Betaine--
homocysteine S-
methyltransferase
1
Glycerate
kinase
D-3-
phosphoglycerate
dehydrogenase
Phosphoserine
aminotransferase
Phosphoserine
phosphatase
L-serine
dehydratase/L-
threonine
deaminase
Serine
hydroxymethyltransferase,
cytosolic
Serine racemase
Cystathionine
beta-synthase
Serine--tRNA
ligase,
cytoplasmic
Glycine--tRNA
ligase
Cystathionine
gamma-lyase
Glycine N-
methyltransferase
L-Cysteine
3-Phosphoglyceric acid
Pyruvic acid
Pyruvic acid
Pyruvic acid
Aminoacetone
O2
H2 O
NH3
H2 O2
Pyruvaldehyde
NAD
NADH
H2 O
L-2-Amino-3-oxobutanoic acid
CO2
Acetyl-CoA
Glycine
CoA
Dimethylglycine
H2 O
Formaldehyde
Sarcosine
H2 O
Formaldehyde
(R)-lipoic acid
8-[(Aminomethyl)sulfanyl]-6-
sulfanyloctanoic acid
CO2
Dihydrolipoate
NH3
5,10-Methylene-THF
H2 O
Tetrahydrofolic acid
NAD
NADH
Hydroxypyruvic acid
L-Alanine
Glyoxylic acid
L-Arginine
Guanidoacetic acid
Orotidylic acid
S-Adenosylhomocysteine
S-Adenosylmethionine
Creatine
Succinyl-CoA
5-Aminolevulinic acid
CoA
βine
Homocysteine
L-Methionine
Glyceric acid
ATP
ADP
NAD
Phosphohydroxypyruvic acid
NADH
L-Glutamic acid
Phosphoserine
Oxoglutaric acid
H2 O
Pi
NH3
Tetrahydrofolic acid
5,10-Methylene-THF
H2 O
D-Serine
Homocysteine
L-Cystathionine
H2 O
ATP
AMP
PPi
ATP
AMP
PPi
H2 O
2-Ketobutyric acid
NH3
S-Adenosylhomocysteine
S-Adenosylmethionine
FAD
FAD
FAD
Pyridoxal
5'-phosphate
FAD
Pyridoxal
5'-phosphate
Pyridoxal
5'-phosphate
Magnesium
Pyridoxal
5'-phosphate
Pyridoxal
5'-phosphate
Pyridoxal
5'-phosphate
Glycyl-tRNA
2-amino-3-
ketobutyrate
coenzyme A
ligase,
mitochondrial
Glycine
dehydrogenase
[decarboxylating],
mitochondrial
L-Serine
Glycine
L-Serine
Glycine
Pyridoxal
5'-phosphate
Pyridoxal
5'-phosphate
L-Seryl-tRNA
L-Seryl-
tRNA(Ser)
Glycyl-
tRNA(Gly)
Cysteine
Metabolism
Gluconeogenesis
Glycolysis
Pyruvate
Metabolism
Pyruvate
Metabolism
Pyruvate
Metabolism
Sphingolipid
Metabolism
Pyridoxal
5'-phosphate
Zinc (II) ion
Pyridoxal
5'-phosphate
Pyridoxal
5'-phosphate
Pyridoxal
5'-phosphate
Cytosol
Mitochondria
Outer mitochondria membrane
Inner mitochondria membrane
Mitochondria matrix
Psychomotor retardation and
seizures
Congenital microcephaly
Mitochondria
MAOA
ALDH2
DMGDH
SARDH
AMT
SHMT2
DLD
AGXT
AGXT
GATM
GAMT
ALAS1
BHMT
GLYCTK
PHGDH
PSAT1
PSPH
SDS
SHMT1
SRR
CBS
SARS
GARS
CTH
GNMT
L-Cysteine
3-
Phosphoglyceric
acid
Pyruvic acid
Pyruvic acid
Pyruvic acid
Aminoacetone
Oxygen
Water
Ammonia
Hydrogen
peroxide
Pyruvaldehyde
NAD
NADH
Water
L-2-Amino-3-
oxobutanoic
acid
Carbon dioxide
Acetyl-CoA
Glycine
Coenzyme A
Dimethylglycine
Water
Formaldehyde
Sarcosine
Water
Formaldehyde
(R)-lipoic acid
8-
[(Aminomethyl)sulfanyl]-
6-
sulfanyloctanoic
acid
Carbon dioxide
Dihydrolipoate
Ammonia
5,10-
Methylene-THF
Water
Tetrahydrofolic
acid
NAD
NADH
Hydroxypyruvic
acid
L-Alanine
Glyoxylic acid
L-Arginine
Guanidoacetic
acid
Orotidylic acid
S-
Adenosylhomocysteine
S-
Adenosylmethionine
Creatine
Succinyl-CoA
5-
Aminolevulinic
acid
Coenzyme A
βine
Homocysteine
L-Methionine
Glyceric acid
Adenosine
triphosphate
Adenosine
diphosphate
NAD
Phosphohydroxypyruvic
acid
NADH
L-Glutamic acid
Phosphoserine
Oxoglutaric
acid
Water
Phosphate
Ammonia
Tetrahydrofolic
acid
5,10-
Methylene-THF
Water
D-Serine
Homocysteine
L-Cystathionine
Water
Adenosine
triphosphate
Adenosine
monophosphate
Pyrophosphate
Adenosine
triphosphate
Adenosine
monophosphate
Pyrophosphate
Water
2-Ketobutyric
acid
Ammonia
S-
Adenosylhomocysteine
S-
Adenosylmethionine
Glycyl-tRNA
GCAT
GLDC
L-Serine
Glycine
L-Serine
Glycine
L-Seryl-tRNA
L-Seryl-
tRNA(Ser)
Glycyl-
tRNA(Gly)
Cysteine
Metabolism
Gluconeogenesis
Glycolysis
Pyruvate
Metabolism
Pyruvate
Metabolism
Pyruvate
Metabolism
Sphingolipid
Metabolism
MAOA
ALDH2
DMGDH
SARDH
AMT
SHMT2
DLD
AGXT
AGXT
GATM
GAMT
ALAS1
BHMT
GLYCTK
PHGDH
PSAT1
PSPH
SDS
SHMT1
SRR
CBS
SARS
GARS
CTH
GNMT
Cys
G3P
Pyr
Pyr
Pyr
Amnactn
O2
H2 O
NH3
H2 O2
Pyruval
NAD
NADH
H2 O
L2AAA
CO2
Ac-CoA
Gly
CoA
DMglyc
H2 O
Formol
Sar
H2 O
Formol
Lipoate
8As6SA
CO2
Dhlip
NH3
5XM-THF
H2 O
THFA
NAD
NADH
OH-Pyr
Ala
Glyoxal
Arg
GIAA
OMP
SAH
SAMe
Creatin
Suc-CoA
5-Amnva
CoA
βine
Hcys
Met
Glycera
ATP
ADP
NAD
3POHPyr
NADH
Glu
SEP
AKG
H2 O
Pi
NH3
THFA
5XM-THF
H2 O
D-Ser
Hcys
L-Cystt
H2 O
ATP
AMP
PPi
ATP
AMP
PPi
H2 O
2KBA
NH3
SAH
SAMe
FAD
FAD
FAD
Pyr-5'P
FAD
Pyr-5'P
Pyr-5'P
Mg2+
Pyr-5'P
Pyr-5'P
Pyr-5'P
GT
GCAT
GLDC
Ser
Gly
Ser
Gly
Pyr-5'P
Pyr-5'P
LST
LSTS
GTG
PW000018
PW000152
PW000146
PW000054
PW000054
PW000054
PW000148
Pyr-5'P
Zinc
Pyr-5'P
Pyr-5'P
Pyr-5'P
Cytosol
Mitochondria
Outer mitochondria membrane
Inner mitochondria membrane
Mitochondria matrix
Psychomotor retardation and
seizures
Congenital microcephaly
Mitochondria
MAOA
ALDH2
DMGDH
SARDH
AMT
SHMT2
DLD
AGXT
AGXT
GATM
GAMT
ALAS1
BHMT
GLYCTK
PHGDH
PSAT1
PSPH
SDS
SHMT1
SRR
CBS
SARS
GARS
CTH
GNMT
Cys
G3P
Pyr
Pyr
Pyr
Amnactn
O2
H2O
NH3
H2O2
Pyruval
NAD
NADH
H2O
L2AAA
CO2
Ac-CoA
Gly
CoA
DMglyc
H2O
Formol
Sar
H2O
Formol
Lipoate
8As6SA
CO2
Dhlip
NH3
5XM-THF
H2O
THFA
NAD
NADH
OH-Pyr
Ala
Glyoxal
Arg
GIAA
OMP
SAH
SAMe
Creatin
Suc-CoA
5-Amnva
CoA
βine
Hcys
Met
Glycera
ATP
ADP
NAD
3POHPyr
NADH
Glu
SEP
AKG
H2O
Pi
NH3
THFA
5XM-THF
H2O
D-Ser
Hcys
L-Cystt
H2O
ATP
AMP
Ppi
ATP
AMP
Ppi
H2O
2KBA
NH3
SAH
SAMe
GT
GCAT
GLDC
Ser
Gly
Ser
Gly
LST
LSTS
GTG
PW000018
PW000152
PW000146
PW000054
PW000054
PW000054
PW000148