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Mitochondrial pyruvate carrier 1 Pyruvate dehydrogenase complex Citrate synthase 3 Unknown Homoisocitrate dehydrogenase, mitochondrial Succinyl-CoA ligase Fumarate hydratase, mitochondrial Acetyl-CoA carboxylase Succinate dehydrogenase 3- isopropylmalate dehydratase 3- isopropylmalate dehydratase Pyruvic acid Oxalacetic acid Fumaric acid Succinic acid FADH 2 Oxoglutaric acid Acetyl-CoA Pyruvic acid CoA NAD CO 2 NADH H 2 O Citric acid CoA Isocitric acid NAD CO 2 NADH H + Succinyl-CoA P i GDP CoA GTP L-Malic acid H 2 O NAD NADH H + ATP HCO 3 - ADP P i Q FAD QH 2 cis-Aconitic acid H 2 O H 2 O Thiamine pyrophosphate Lipoamide FAD Magnesium Biotin Manganese 4Fe-4S 4Fe-4S Gluconeogenesis Glycolysis Pyruvate Metabolism Malate- Aspartate Shuttle Gluconeogenesis Alanine Metabolism Aspartate Metabolism Pyruvate Metabolism Aspartate Metabolism Tyrosine Metabolism Arginine and Proline Metabolism Urea Cycle Propanoate Metabolism Mitochondrial Electron Transport Chain Malate- Aspartate Shuttle Glutamate Metabolism Alanine Metabolism Gluconeogenesis Glucose-Alanine Cycle Valine, Leucine, and Isoleucine Degradation Tryptophan Metabolism Pyruvate Metabolism Fatty Acid Metabolism Ketone Body Metabolism Lysine Degradation Oxidation of Branched-Chain Fatty Acids Propanoate Metabolism Homoisocitrate dehydrogenase, mitochondrial Inner mitochondrial membrane Mitochondrial intermembrane space Cytosol Mitochondrial matrix Mitochondrion Intracellular Space Inner mitochondrial membrane Outer mitochondrial membrane
Mitochondria MPC1 Unknown CIT3 Unknown LYS12 LSC1 LSC2 FUM1 ACC1 FRD1 SDH2 Unknown Unknown LEU1 LEU1 Pyruvic acid Oxalacetic acid Fumaric acid Succinic acid FADH Oxoglutaric acid Acetyl-CoA Pyruvic acid Coenzyme A NAD Carbon dioxide NADH Water Citric acid Coenzyme A Isocitric acid NAD Carbon dioxide NADH Hydrogen Ion Succinyl-CoA Phosphate Guanosine diphosphate Coenzyme A Guanosine triphosphate L-Malic acid Water NAD NADH Hydrogen Ion Adenosine triphosphate Hydrogen carbonate Adenosine diphosphate Phosphate Coenzyme Q10 FAD QH(2) cis-Aconitic acid Water Water Gluconeogenesis Glycolysis Pyruvate Metabolism Malate- Aspartate Shuttle Gluconeogenesis Alanine Metabolism Aspartate Metabolism Pyruvate Metabolism Aspartate Metabolism Tyrosine Metabolism Arginine and Proline Metabolism Urea Cycle Propanoate Metabolism Mitochondrial Electron Transport Chain Malate- Aspartate Shuttle Glutamate Metabolism Alanine Metabolism Gluconeogenesis Glucose-Alanine Cycle Valine, Leucine, and Isoleucine Degradation Tryptophan Metabolism Pyruvate Metabolism Fatty Acid Metabolism Ketone Body Metabolism Lysine Degradation Oxidation of Branched-Chain Fatty Acids Propanoate Metabolism LYS12