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3-ketoacyl-CoA synthase ELO1 Long-chain- fatty-acid-- CoA ligase 2 Very long-chain fatty acid transport protein long chain fatty acyl:CoA synthetase Long-chain- fatty-acid-- CoA ligase 1 Long-chain- fatty-acid-- CoA ligase 3 3-oxoacyl- [acyl- carrier- protein] reductase Peroxisomal hydratase- dehydrogenase- epimerase 2-enoyl thioester reductase Peroxisomal acyl-coenzyme A thioester hydrolase 1 2-enoyl thioester reductase 3-ketoacyl-CoA synthase ELO1 3-oxoacyl- [acyl- carrier- protein] reductase Peroxisomal hydratase- dehydrogenase- epimerase 2-enoyl thioester reductase 3-ketoacyl-CoA synthase ELO1 3-ketoacyl-CoA synthase ELO1 3-oxoacyl- [acyl- carrier- protein] reductase 3-oxoacyl- [acyl- carrier- protein] reductase Peroxisomal hydratase- dehydrogenase- epimerase 2-enoyl thioester reductase 3-ketoacyl-CoA synthase ELO1 3-oxoacyl- [acyl- carrier- protein] reductase Peroxisomal hydratase- dehydrogenase- epimerase 2-enoyl thioester reductase dihydrosphingosine C-4 hydroxylase 3- ketosphinganine reductase Serine palmitoyltransferase 1 Peroxisomal hydratase- dehydrogenase- epimerase Ceramide synthase subunit LIP1 Palmityl-CoA Malonyl-CoA H+ CO2 3- Oxooctadecanoyl- CoA CoA Palmitic acid ATP CoA AMP PPi H+ NADPH NADP (3R)-3- hydroxy- stearoyl-CoA (2E)- Octadecenoyl- CoA H2O H+ NADPH Stearoyl-CoA NADP H2O H+ CoA Stearic acid (2E)- eicosenoyl- CoA H+ NADPH Eicosanoyl-CoA NADP Malonyl-CoA H+ CoA CO2 3- oxodocosanoyl- CoA H+ NADPH NADP (3R)-3- hydroxy- docosanoyl- CoA H2O trans-docos- 2-enoyl-CoA H+ NADPH Docosanoyl-CoA NADP Malonyl-CoA H+ CoA CO2 3- oxotetracosanoyl- CoA H+ Malonyl-CoA 3- oxoicosanoyl- CoA CoA CO2 NADPH H+ (3R)-3- hydroxy- arachidoyl- CoA NADP NADPH H+ (3R)- hydroxytetracosanoyl- CoA NADP H2O (2E)- lignocerenoyl- CoA H+ NADPH NADP Tetracosanoyl- CoA Malonyl-CoA H+ CoA CO2 3- oxohexacosanoyl- CoA H+ NADPH NADP (3R)- hydroxyhexacosanoyl- CoA H2O (2E)- cerotenoyl- CoA H+ NADPH Hexacosanoyl- CoA NADP H+ O2 Sphinganine H2O Phytosphingosine H+ NADPH 3- Dehydrosphinganine NADP Palmityl-CoA L-Serine H+ CoA CO2 H2O H+ CoA N- hexacosanoyl- C20-4- hydroxysphinganine ferrocytochrome b5 ferricytochrome b5 Endocytosis
ELO1 FAA2 FAT1 FAA4 FAA1 FAA3 OAR1 FOX2 ETR1 TES1 ETR1 ELO1 OAR1 FOX2 ETR1 ELO1 ELO1 OAR1 OAR1 FOX2 ETR1 ELO1 OAR1 FOX2 ETR1 SUR2 TSC10 LCB1 FOX2 LIP1 Palmityl-CoA Malonyl-CoA Hydrogen Ion Carbon dioxide 3- Oxooctadecanoyl- CoA Coenzyme A Palmitic acid Adenosine triphosphate Coenzyme A Adenosine monophosphate Pyrophosphate Hydrogen Ion NADPH NADP (3R)-3- hydroxy- stearoyl-CoA (2E)- Octadecenoyl- CoA Water Hydrogen Ion NADPH Stearoyl-CoA NADP Water Hydrogen Ion Coenzyme A Stearic acid (2E)- eicosenoyl- CoA Hydrogen Ion NADPH Eicosanoyl-CoA NADP Malonyl-CoA Hydrogen Ion Coenzyme A Carbon dioxide 3- oxodocosanoyl- CoA Hydrogen Ion NADPH NADP (3R)-3- hydroxy- docosanoyl- CoA Water trans-docos- 2-enoyl-CoA Hydrogen Ion NADPH Docosanoyl-CoA NADP Malonyl-CoA Hydrogen Ion Coenzyme A Carbon dioxide 3- oxotetracosanoyl- CoA Hydrogen Ion Malonyl-CoA 3- oxoicosanoyl- CoA Coenzyme A Carbon dioxide NADPH Hydrogen Ion (3R)-3- hydroxy- arachidoyl- CoA NADP NADPH Hydrogen Ion (3R)- hydroxytetracosanoyl- CoA NADP Water (2E)- lignocerenoyl- CoA Hydrogen Ion NADPH NADP Tetracosanoyl- CoA Malonyl-CoA Hydrogen Ion Coenzyme A Carbon dioxide 3- oxohexacosanoyl- CoA Hydrogen Ion NADPH NADP (3R)- hydroxyhexacosanoyl- CoA Water (2E)- cerotenoyl- CoA Hydrogen Ion NADPH Hexacosanoyl- CoA NADP Hydrogen Ion Oxygen Sphinganine Water Phytosphingosine Hydrogen Ion NADPH 3- Dehydrosphinganine NADP Palmityl-CoA L-Serine Hydrogen Ion Coenzyme A Carbon dioxide Water Hydrogen Ion Coenzyme A N- hexacosanoyl- C20-4- hydroxysphinganine ferrocytochrome b5 ferricytochrome b5 Endocytosis
ELO1 FAA2 FAT1 FAA4 FAA1 FAA3 OAR1 FOX2 ETR1 TES1 ETR1 ELO1 OAR1 FOX2 ETR1 ELO1 ELO1 OAR1 OAR1 FOX2 ETR1 ELO1 OAR1 FOX2 ETR1 SUR2 TSC10 LCB1 FOX2 LIP1 COA16:0 MalyCoA H+ CO2 3OOACoA CoA 16:0 ATP CoA AMP PPi H+ NADPH NADP 3RhsCoA tO2eCoA H2O H+ NADPH COA18:0 NADP H2O H+ CoA 18:0 2ECoA H+ NADPH Eicosan NADP MalyCoA H+ CoA CO2 3-oCoA H+ NADPH NADP 3R3hCoA H2O td2eCoA H+ NADPH Docosan NADP MalyCoA H+ CoA CO2 3OLC H+ MalyCoA 3OIyCoA CoA CO2 NADPH H+ 3RHArCA NADP NADPH H+ 3RhxCoA NADP H2O 2ElCoA H+ NADPH NADP TetCsCA MalyCoA H+ CoA CO2 3OhxCCA H+ NADPH NADP 3RhhCoA H2O 2CCoA H+ NADPH HexCoA NADP H+ O2 d18:0 H2O Phytosp H+ NADPH 3-DHPG NADP COA16:0 Ser H+ CoA CO2 H2O H+ CoA NhC20h FB FB Endoc
ELO1 FAA2 FAT1 FAA4 FAA1 FAA3 OAR1 FOX2 ETR1 TES1 ETR1 ELO1 OAR1 FOX2 ETR1 ELO1 ELO1 OAR1 OAR1 FOX2 ETR1 ELO1 OAR1 FOX2 ETR1 SUR2 TSC10 LCB1 FOX2 LIP1 COA16:0 MalyCoA H+ CO2 3OOACoA CoA 16:0 ATP CoA AMP Ppi H+ NADPH NADP 3RhsCoA tO2eCoA H2O H+ NADPH COA18:0 NADP H2O H+ CoA 18:0 2ECoA H+ NADPH Eicosan NADP MalyCoA H+ CoA CO2 3-oCoA H+ NADPH NADP 3R3hCoA H2O td2eCoA H+ NADPH Docosan NADP MalyCoA H+ CoA CO2 3OLC H+ MalyCoA 3OIyCoA CoA CO2 NADPH H+ 3RHArCA NADP NADPH H+ 3RhxCoA NADP H2O 2ElCoA H+ NADPH NADP TetCsCA MalyCoA H+ CoA CO2 3OhxCCA H+ NADPH NADP 3RhhCoA H2O 2CCoA H+ NADPH HexCoA NADP H+ O2 d18:0 H2O Phytosp H+ NADPH 3-DHPG NADP COA16:0 Ser H+ CoA CO2 H2O H+ CoA NhC20h FB FB Endoc