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Branched- chain-amino- acid aminotransferase, mitochondrial Branched- chain-amino- acid aminotransferase, cytosolic Pyruvate decarboxylase isozyme 1 pyruvate decarboxylase 2 Pyruvate decarboxylase isozyme 3 alcohol dehydrogenase subunit I alcohol dehydrogenase subunit 2 (S)-3-methyl- 2- oxopentanoate (S)-3-methyl- 2- oxopentanoate L-Isoleucine Oxoglutaric acid L-Glutamic acid L-Isoleucine H+ CO2 H+ ()-2- Methylbutanal CO2 NADH H+ (S)-2-Methyl- 1-butanol NAD
Mitochondria BAT1 BAT2 PDC1 PDC5 PDC6 ADH7 ADH6 (S)-3-methyl- 2- oxopentanoate (S)-3-methyl- 2- oxopentanoate L-Isoleucine Oxoglutaric acid L-Glutamic acid L-Isoleucine Hydrogen Ion Carbon dioxide Hydrogen Ion ()-2- Methylbutanal Carbon dioxide NADH Hydrogen Ion (S)-2-Methyl- 1-butanol NAD
BAT1 BAT2 PDC1 PDC5 PDC6 ADH7 ADH6 S3M2O S3M2O Ile AKG Glu Ile H+ CO2 H+ 2Mibual CO2 NADH H+ S2M1Bol NAD
Mitochondria BAT1 BAT2 PDC1 PDC5 PDC6 ADH7 ADH6 S3M2O S3M2O Ile AKG Glu Ile H+ CO2 H+ 2Mibual CO2 NADH H+ S2M1Bol NAD