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Neutral amino acid transporter B(0) Neutral amino acid transporter A Mitochondrial ornithine transporter 1 Mitochondrial ornithine transporter 1 Calcium-binding mitochondrial carrier protein Aralar1 Glutaminase liver isoform, mitochondrial Glutamate dehydrogenase 1, mitochondrial Carbamoyl- phosphate synthase [ammonia], mitochondrial Aspartate aminotransferase, mitochondrial Ornithine carbamoyltransferase, mitochondrial Arginase-1 Argininosuccinate lyase Argininosuccinate synthase Alanine aminotransferase 1 L-Glutamine L-Glutamic acid Oxalacetic acid NH3 L-Aspartic acid Fumaric acid L-Arginine Ornithine L-Glutamine L-Alanine L-Alanine Ornithine Citrulline Citrulline Ornithine Ornithine Citrulline Citrulline L-Aspartic acid L-Glutamic acid L-Glutamic acid H2O H2O NAD Oxoglutaric acid NADH ATP CO2 H2O ADP Pi Carbamoyl phosphate Pi H2O Urea Argininosuccinic acid ATP AMP PPi Oxoglutaric acid L-Glutamic acid Pyruvic acid Calcium Pyridoxal 5'-phosphate Manganese Pyridoxal 5'-phosphate Pyrimidine Metabolism Porphyrin Metabolism Porphyrin Metabolism Alanine Metabolism Glutamate Metabolism Glucose-Alanine Cycle Purine Metabolism Glucose-Alanine Cycle Aspartate Metabolism Citric Acid Cycle Arginine and Proline Metabolism D-Arginine and D-Ornithine Metabolism D-Arginine and D-Ornithine Metabolism Cytosol Mitochondria Mitochondrial Matrix Urea Cycle Extracellular Space Intracellular Space