Quantitative metabolomics services for biomarker discovery and validation.
Specializing in ready to use metabolomics kits.
Your source for quantitative metabolomics technologies and bioinformatics.
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Monocarboxylate transporter 1 Pyruvate carboxylase, mitochondrial L-lactate dehydrogenase A-like 6A Pyruvate kinase isozymes R/L Phosphoenolpyruvate carboxykinase, cytosolic [GTP] Malate dehydrogenase, cytoplasmic NADP-dependent malic enzyme Probable D-lactate dehydrogenase, mitochondrial Hydroxyacylglutathione hydrolase, mitochondrial Lactoylglutathione lyase Glyoxylate reductase/hydroxypyruvate reductase Aldose reductase Aldose reductase NADP-dependent malic enzyme Dihydrolipoyl dehydrogenase E3 Dihydrolipoyl transacetylase E2 Acetyl-CoA carboxylase 1 Acetyl-CoA acetyltransferase, mitochondrial Acyl-coenzyme A thioesterase 12 Acylphosphatase- 1 Aldehyde dehydrogenase, mitochondrial Acetyl-coenzyme A synthetase, cytoplasmic Acetyl-coenzyme A synthetase, cytoplasmic Pyruvate dehydrogenase E1 Pyruvic acid Oxalacetic acid Phosphoenolpyruvic acid Pyruvaldehyde Acetyl-CoA Acetoacetyl-CoA L-Lactic acid L-Lactic acid ATP HCO3- ADP Pi NAD NADH H+ ATP ADP GTP GDP CO2 L-Malic acid NAD NADH H+ NAD CO2 NADH H+ D-Lactic acid H+ S-Lactoylglutathione H2O Glutathione Glutathione D-Lactaldehyde NAD NADH H+ Lactaldehyde NAD H+ NADH Propylene glycol NADP H+ NADPH NADP CO2 NADPH Dihydrolipoamide NAD Lipoamide NADH H+ S-Acetyldihydrolipoamide-E Coenzyme A ATP HCO3- Pi ADP Malonyl-CoA CoA CoA Acetic acid H2O Acetylphosphate H2O Pi Acetaldehyde NAD H2O NADH H+ ATP PPi Acetyl adenylate AMP PPi ATP CO2 Biotin Manganese Magnesium Potassium Manganese Manganese Zinc (II) ion Zinc (II) ion Manganese FAD Biotin Manganese Ferricytochrome c Ferrocytochrome c Nicotinate and Nicotinamide Metabolism Valine, Leucine, and Isoleucine Degradation Citric Acid Cycle Glycolysis Glycine and Serine Metabolism Propanoate Metabolism Ketone Body Metabolism Thiamine pyrophosphate Cytoplasm Mitochondria Mitochondrial matrix Mitochondria Mitochondrial Matrix Symptoms and signs include severe lactic acidosis in the newborns that usually leading to death, hypotonic, lethargic, seizures, mental retardation and spasticity.