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Search for 'valine AND leucine' in 'all pathways' in 'Homo sapiens' returned 48 results

SMP0000238

Pw000091 View Pathway
Disease

Isovaleric Aciduria

  • Matched Description: of leucine. A defect in this enzyme causes accumulation of ammonia, ketone bodies, Isovaleryl/2
  • Matched Compounds: L-Leucine … L-Valine
  • Matched Compound Synonyms: (2s)-alpha-leucine … (s)-(+)-leucine … (s)-leucineLeucine … (2s)-a-leucine
  • SMP0000173

    Pw000060 View Pathway
    Disease

    beta-Ketothiolase Deficiency

  • Matched Compounds: L-Leucine … L-Valine
  • Matched Compound Synonyms: (2s)-alpha-leucine … (s)-(+)-leucine … (s)-leucineLeucine … (2s)-a-leucine
  • SMP0000237

    Pw000065 View Pathway
    Disease

    3-Methylcrotonyl-CoA Carboxylase Deficiency Type I

  • Matched Description: constitute the breakdown of leucine. Mutations in the aforementioned genes leads to a reduction in the … breakdown leucine properly. Consequently, this leads to the build up of toxic byproducts which are not … processed as the breakdown of leucine is left incomplete. If these toxic byproducts manifest themselves
  • Matched Compounds: L-Leucine … L-Valine
  • Matched Compound Synonyms: (2s)-alpha-leucine … (s)-(+)-leucine … (s)-leucineLeucine … (2s)-a-leucine
  • SMP0000137

    Pw000061 View Pathway
    Disease

    2-Methyl-3-hydroxybutyryl-CoA Dehydrogenase Deficiency

  • Matched Compounds: L-Leucine … L-Valine
  • Matched Compound Synonyms: (2s)-alpha-leucine … (s)-(+)-leucine … (s)-leucineLeucine … (2s)-a-leucine
  • SMP0000139

    Pw000066 View Pathway
    Disease

    3-Methylglutaconic Aciduria Type I

  • Matched Compounds: L-Leucine … L-Valine
  • Matched Compound Synonyms: (2s)-alpha-leucine … (s)-(+)-leucine … (s)-leucineLeucine … (2s)-a-leucine
  • SMP0000251

    Pw000349 View Pathway
    Drug Action

    Roxithromycin Action Pathway

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine
  • SMP0000253

    Pw000351 View Pathway
    Drug Action

    Amikacin Action Pathway

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine
  • SMP0000295

    Pw000363 View Pathway
    Drug Action

    Lymecycline Action Pathway

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine
  • SMP0000258

    Pw000356 View Pathway
    Drug Action

    Spectinomycin Action Pathway

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine
  • SMP0000728

    Pw000705 View Pathway
    Drug Action

    Lincomycin Action Pathway

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine